CLASSIFICATION OF DISEASES AND INJURIES

Reference: CDC website

1. INFECTIOUS AND PARASITIC DISEASES (001-139)
2. NEOPLASMS (140-239)
3. ENDOCRINE, NUTRITIONAL AND METABOLIC DISEASES, AND IMMUNITY DISORDERS (240-279)
4. DISEASES OF THE BLOOD AND BLOOD-FORMING ORGANS (280-289)
5. MENTAL DISORDERS (290-319)
6. DISEASES OF THE NERVOUS SYSTEM AND SENSE ORGANS (320-389)
7. DISEASES OF THE CIRCULATORY SYSTEM (390-459)
8. DISEASES OF THE RESPIRATORY SYSTEM (460-519)
9. DISEASES OF THE DIGESTIVE SYSTEM (520-579)
10. DISEASES OF THE GENITOURINARY SYSTEM (580-629)
11. COMPLICATIONS OF PREGNANCY, CHILDBIRTH, AND THE PUERPERIUM (630-677)
12. DISEASES OF THE SKIN AND SUBCUTANEOUS TISSUE (680-709)
13. DISEASES OF THE MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE (710-739)
14. CONGENITAL ANOMALIES (740-759)
15. CERTAIN CONDITIONS ORIGINATING IN THE PERINATAL PERIOD (760-779)
16. SYMPTOMS, SIGNS, AND ILL-DEFINED CONDITIONS (780-799)
17. INJURY AND POISONING (800-999)

1. INFECTIOUS AND PARASITIC DISEASES (001-139) back to top

Note:    Categories for "late effects" of infectious and parasitic diseases are to be found at 137-139.

Includes:          diseases generally recognized as communicable or transmissible as well as a few diseases of unknown but possibly infectious origin

Excludes:         acute respiratory infections (460-466)

carrier or suspected carrier of infectious organism (V02.0-V02.9)

certain localized infections

influenza (487.0-487.8)

INTESTINAL INFECTIOUS DISEASES (001-009)

Excludes:         helminthiases (120.0-129)

001       Cholera

001.0    Due to Vibrio cholerae

001.1    Due to Vibrio cholerae el tor

001.9    Cholera, unspecified

002       Typhoid and paratyphoid fevers

002.0    Typhoid fever

Typhoid (fever) (infection) [any site]

002.1    Paratyphoid fever A

002.2    Paratyphoid fever B

002.3    Paratyphoid fever C

002.9    Paratyphoid fever, unspecified

003       Other salmonella infections

Includes:           infection or food poisoning by Salmonella [any serotype]

003.0    Salmonella gastroenteritis

Salmonellosis

003.1    Salmonella septicemia

003.2    Localized salmonella infections

003.20  Localized salmonella infection, unspecified

003.21  Salmonella meningitis

003.22  Salmonella pneumonia

003.23  Salmonella arthritis

003.24  Salmonella osteomyelitis

003.29  Other

003.8    Other specified salmonella infections

003.9    Salmonella infection, unspecified

004       Shigellosis

Includes:           bacillary dysentery

004.0    Shigella dysenteriae

Infection by group A Shigella (Schmitz) (Shiga)

004.1    Shigella flexneri

Infection by group B Shigella

004.2    Shigella boydii

Infection by group C Shigella

004.3    Shigella sonnei

Infection by group D Shigella

004.8    Other specified shigella infections

004.9    Shigellosis, unspecified

005       Other food poisoning (bacterial)

Excludes:          salmonella infections (003.0-003.9)

toxic effect of:

food contaminants (989.7)

noxious foodstuffs (988.0-988.9)

005.0    Staphylococcal food poisoning

Staphylococcal toxemia specified as due to food

005.1    Botulism

Food poisoning due to Clostridium botulinum

005.2    Food poisoning due to Clostridium perfringens [C. welchii]

Enteritis necroticans

005.3    Food poisoning due to other Clostridia

005.4    Food poisoning due to Vibrio parahaemolyticus

005.8    Other bacterial food poisoning

Excludes:          salmonella food poisoning (003.0-003.9)

005.81  Food poisoning due to Vibrio vulnificus

005.89  Other bacterial food poisoning

Food poisoning due to Bacillus cereus

005.9    Food poisoning, unspecified

006       Amebiasis

Includes:           infection due to Entamoeba histolytica

Excludes:          amebiasis due to organisms other than Entamoeba histolytica (007.8)

006.0    Acute amebic dysentery without mention of abscess

Acute amebiasis

006.1    Chronic intestinal amebiasis without mention of abscess

Chronic:

amebiasis

amebic dysentery

006.2    Amebic nondysenteric colitis

006.3    Amebic liver abscess

Hepatic amebiasis

006.4    Amebic lung abscess

Amebic abscess of lung (and liver)

006.5    Amebic brain abscess

Amebic abscess of brain (and liver) (and lung)

006.6    Amebic skin ulceration

Cutaneous amebiasis

006.8    Amebic infection of other sites

Amebic:

appendicitis

balanitis

Ameboma

Excludes:          specific infections by free-living amebae (136.2)

006.9    Amebiasis, unspecified

Amebiasis NOS

007       Other protozoal intestinal diseases

Includes:           protozoal:

colitis

diarrhea

dysentery

007.0    Balantidiasis

Infection by Balantidium coli

007.1    Giardiasis

Infection by Giardia lamblia

Lambliasis

007.2    Coccidiosis

Infection by Isospora belli and Isospora hominis

Isosporiasis

007.3    Intestinal trichomoniasis

007.4    Cryptosporidiosis

007.5    Cyclosporiasis

007.8    Other specified protozoal intestinal diseases

Amebiasis due to organisms other than Entamoeba histolytica

007.9    Unspecified protozoal intestinal disease

Flagellate diarrhea

Protozoal dysentery NOS

008       Intestinal infections due to other organisms

Includes:           any condition classifiable to 009.0-009.3 with mention of the responsible organisms

Excludes:          food poisoning by these organisms (005.0-005.9)

008.0    Escherichia coli [E. coli]

008.00  E. coli, unspecified

E. coli enteritis NOS

008.01  Enteropathogenic E. coli

008.02  Enterotoxigenic E. coli

008.03  Enteroinvasive E. coli

008.04  Enterohemorrhagic E. coli

008.09  Other intestinal E. coli infections

008.1    Arizona group of paracolon bacilli

008.2    Aerobacter aerogenes

Enterobacter aerogenes

008.3    Proteus (mirabilis) (morganii)

008.4    Other specified bacteria

008.41  Staphylococcus

Staphylococcal enterocolitis

008.42  Pseudomonas

008.43  Campylobacter

008.44  Yersinia enterocolitica

008.45  Clostridium difficile

Pseudomembranous colitis

008.46  Other anaerobes

Anaerobic enteritis NOS

Bacteroides (fragilis)

Gram-negative anaerobes

008.47  Other gram-negative bacteria

Gram-negative enteritis NOS

Excludes:          gram-negative anaerobes (008.46)

008.49  Other

008.5    Bacterial enteritis, unspecified

008.6    Enteritis due to specified virus

008.61  Rotavirus

008.62  Adenovirus

008.63  Norwalk virus

Norwalk-like agent

008.64  Other small round viruses [SRV's]

Small round virus NOS

008.65  Calcivirus

008.66  Astrovirus

008.67  Enterovirus NEC

Coxsackie virus

Echovirus

Excludes:          poliovirus (045.0-045.9)

008.69  Other viral enteritis

Torovirus

008.8    Other organism, not elsewhere classified

Viral:

enteritis NOS

gastroenteritis

Excludes:          influenza with involvement of gastrointestinal tract (487.8)

009       Ill-defined intestinal infections

Excludes:          diarrheal disease or intestinal infection due to specified organism (001.0-008.8)

diarrhea following gastrointestinal surgery (564.4)

intestinal malabsorption (579.0-579.9)

ischemic enteritis (557.0-557.9)

other noninfectious gastroenteritis and colitis (558.1-558.9)

regional enteritis (555.0-555.9)

ulcerative colitis (556)

009.0    Infectious colitis, enteritis, and gastroenteritis

Colitis (septic)

Dysentery:

NOS

catarrhal

hemorrhagic

Enteritis (septic)

Gastroenteritis (septic)

009.1    Colitis, enteritis, and gastroenteritis of presumed infectious origin

Excludes:          colitis NOS (558.9)

enteritis NOS (558.9)

gastroenteritis NOS (558.9)

009.2    Infectious diarrhea

Diarrhea:

dysenteric

epidemic

Infectious diarrheal disease NOS

009.3    Diarrhea of presumed infectious origin

Excludes:          diarrhea NOS (787.91)

TUBERCULOSIS (010-018)

Includes:          infection by Mycobacterium tuberculosis (human) (bovine)

Excludes:         congenital tuberculosis (771.2)

late effects of tuberculosis (137.0-137.4)

The following fifth-digit subclassification is for use with categories 010-018:

0 unspecified

1 bacteriological or histological examination not done

2 bacteriological or histological examination unknown (at present)

3 tubercle bacilli found (in sputum) by microscopy

4 tubercle bacilli not found (in sputum) by microscopy, but found by bacterial culture

5 tubercle bacilli not found by bacteriological examination, but tuberculosis confirmed histologically

6 tubercle bacilli not found by bacteriological or histological examination, but tuberculosis confirmed by other methods [inoculation of animals]

010       Primary tuberculous infection

Requires fifth digit. See beginning of section 010-018 for codes and definitions.

010.0    Primary tuberculous infection

Excludes:          nonspecific reaction to tuberculin skin test without active tuberculosis (795.5)

positive PPD (795.5)

positive tuberculin skin test without active tuberculosis (795.5)

010.1    Tuberculous pleurisy in primary progressive tuberculosis

010.8    Other primary progressive tuberculosis

Excludes:          tuberculous erythema nodosum (017.1)

010.9    Primary tuberculous infection, unspecified

011       Pulmonary tuberculosis

Requires fifth digit. See beginning of section 010-018 for codes and definitions.

Use additional code to identify any associated silicosis (502)

011.0    Tuberculosis of lung, infiltrative

011.1    Tuberculosis of lung, nodular

011.2    Tuberculosis of lung with cavitation

011.3    Tuberculosis of bronchus

Excludes:          isolated bronchial tuberculosis (012.2)

011.4    Tuberculous fibrosis of lung

011.5    Tuberculous bronchiectasis

011.6    Tuberculous pneumonia [any form]

011.7    Tuberculous pneumothorax

011.8    Other specified pulmonary tuberculosis

011.9    Pulmonary tuberculosis, unspecified

Respiratory tuberculosis NOS

Tuberculosis of lung NOS

012       Other respiratory tuberculosis

Requires fifth digit. See beginning of section 010-018 for codes and definitions.

Excludes:          respiratory tuberculosis, unspecified (011.9)

012.0    Tuberculous pleurisy

Tuberculosis of pleura

Tuberculous empyema

Tuberculous hydrothorax

Excludes:          pleurisy with effusion without mention of cause (511.9)

tuberculous pleurisy in primary progressive tuberculosis (010.1)

012.1    Tuberculosis of intrathoracic lymph nodes

Tuberculosis of lymph nodes:

hilar

mediastinal

tracheobronchial

Tuberculous tracheobronchial adenopathy

Excludes:          that specified as primary (010.0-010.9)

012.2    Isolated tracheal or bronchial tuberculosis

012.3    Tuberculous laryngitis

Tuberculosis of glottis

012.8    Other specified respiratory tuberculosis

Tuberculosis of:

mediastinum

nasopharynx

nose (septum)

sinus [any nasal]

013       Tuberculosis of meninges and central nervous system

Requires fifth digit. See beginning of section 010-018 for codes and definitions.

013.0    Tuberculous meningitis

Tuberculosis of meninges (cerebral) (spinal)

Tuberculous:

leptomeningitis

meningoencephalitis

Excludes:          tuberculoma of meninges (013.1)

013.1    Tuberculoma of meninges

013.2    Tuberculoma of brain

Tuberculosis of brain (current disease)

013.3    Tuberculous abscess of brain

013.4    Tuberculoma of spinal cord

013.5    Tuberculous abscess of spinal cord

013.6    Tuberculous encephalitis or myelitis

013.8    Other specified tuberculosis of central nervous system

013.9    Unspecified tuberculosis of central nervous system

Tuberculosis of central nervous system NOS

014       Tuberculosis of intestines, peritoneum, and mesenteric glands

Requires fifth digit. See beginning of section 010-018 for codes and definitions.

014.0    Tuberculous peritonitis

Tuberculous ascites

014.8    Other

Tuberculosis (of):

anus

intestine (large) (small)

mesenteric glands

rectum

retroperitoneal (lymph nodes)

Tuberculous enteritis

015       Tuberculosis of bones and joints

Requires fifth digit. See beginning of section 010-018 for codes and definitions.

Use additional code to identify manifestation, as:

tuberculous:

arthropathy (711.4)

necrosis of bone (730.8)

osteitis (730.8)

osteomyelitis (730.8)

synovitis (727.01)

tenosynovitis (727.01)

015.0    Vertebral column

Pott's disease

Use additional code to identify manifestation, as:

curvature of spine [Pott's] (737.4)

kyphosis (737.4)

spondylitis (720.81)

015.1    Hip

015.2    Knee

015.5    Limb bones

Tuberculous dactylitis

015.6    Mastoid

Tuberculous mastoiditis

015.7    Other specified bone

015.8    Other specified joint

015.9    Tuberculosis of unspecified bones and joints

016       Tuberculosis of genitourinary system

Requires fifth digit. See beginning of section 010-018 for codes and definitions.

016.0    Kidney

Renal tuberculosis

Use additional code to identify manifestation, as:

tuberculous:

nephropathy (583.81)

pyelitis (590.81)

pyelonephritis (590.81)

016.1    Bladder

016.2    Ureter

016.3    Other urinary organs

016.4    Epididymis

016.5    Other male genital organs

Use additional code to identify manifestation, as:

tuberculosis of:

prostate (601.4)

seminal vesicle (608.81)

testis (608.81)

016.6    Tuberculous oophoritis and salpingitis

016.7    Other female genital organs

Tuberculous:

cervicitis

endometritis

016.9    Genitourinary tuberculosis, unspecified

017       Tuberculosis of other organs

Requires fifth digit. See beginning of section 010-018 for codes and definitions.

017.0    Skin and subcutaneous cellular tissue

Lupus:

exedens

vulgaris

Scrofuloderma

Tuberculosis:

colliquativa

cutis

lichenoides

papulonecrotica

verrucosa cutis

Excludes:          lupus erythematosus (695.4)

disseminated (710.0)

lupus NOS (710.0)

nonspecific reaction to tuberculin skin test without active tuberculosis (795.5)

positive PPD (795.5)

positive tuberculin skin test without active tuberculosis (795.5)

017.1    Erythema nodosum with hypersensitivity reaction in tuberculosis

Bazin's disease

Erythema:

induratum

nodosum, tuberculous

Tuberculosis indurativa

Excludes:          erythema nodosum NOS (695.2)

017.2    Peripheral lymph nodes

Scrofula

Scrofulous abscess

Tuberculous adenitis

Excludes:          tuberculosis of lymph nodes:

bronchial and mediastinal (012.1)

mesenteric and retroperitoneal (014.8)

tuberculous tracheobronchial adenopathy (012.1)

017.3    Eye

Use additional code to identify manifestation, as:

tuberculous:

episcleritis (379.09)

interstitial keratitis (370.59)

iridocyclitis, chronic (364.11)

keratoconjunctivitis (phlyctenular) (370.31)

017.4    Ear

Tuberculosis of ear

Tuberculous otitis media

Excludes:          tuberculous mastoiditis (015.6)

017.5    Thyroid gland

017.6    Adrenal glands

Addison's disease, tuberculous

017.7    Spleen

017.8    Esophagus

017.9    Other specified organs

Use additional code to identify manifestation, as:

tuberculosis of:

endocardium [any valve] (424.91)

myocardium (422.0)

pericardium (420.0)

018       Miliary tuberculosis

Includes:           tuberculosis:

disseminated

generalized

miliary, whether of a single specified site, multiple sites, or unspecified site

polyserositis

018.0    Acute miliary tuberculosis

018.8    Other specified miliary tuberculosis

018.9    Miliary tuberculosis, unspecified

ZOONOTIC BACTERIAL DISEASES (020-027)

020       Plague

Includes:           infection by Yersinia [Pasteurella] pestis

020.0    Bubonic

020.1    Cellulocutaneous

020.2    Septicemic

020.3    Primary pneumonic

020.4    Secondary pneumonic

020.5    Pneumonic, unspecified

020.8    Other specified types of plague

Abortive plague

Ambulatory plague

Pestis minor

020.9    Plague, unspecified

021       Tularemia

Includes:           deerfly fever

infection by Francisella [Pasteurella] tularensis

rabbit fever

021.0    Ulceroglandular tularemia

021.1    Enteric tularemia

Tularemia:

cryptogenic

intestinal

typhoidal

021.2    Pulmonary tularemia

Bronchopneumonic tularemia

021.3    Oculoglandular tularemia

021.8    Other specified tularemia

Tularemia:

generalized or disseminated

glandular

021.9    Unspecified tularemia

022       Anthrax

022.0    Cutaneous anthrax

Malignant pustule

022.1    Pulmonary anthrax

Respiratory anthrax

Wool-sorters' disease

022.2    Gastrointestinal anthrax

022.3    Anthrax septicemia

022.8    Other specified manifestations of anthrax

022.9    Anthrax, unspecified

023       Brucellosis

Includes:           fever:

Malta

Mediterranean

undulant

023.0    Brucella melitensis

023.1    Brucella abortus

023.2    Brucella suis

023.3    Brucella canis

023.8    Other brucellosis

Infection by more than one organism

023.9    Brucellosis, unspecified

024       Glanders

Infection by:

Actinobacillus mallei

Malleomyces mallei

Pseudomonas mallei

Farcy

Malleus

025       Melioidosis

Infection by:

Malleomyces pseudomallei

Pseudomonas pseudomallei

Whitmore's bacillus

Pseudoglanders

026       Rat-bite fever

026.0    Spirillary fever

Rat-bite fever due to Spirillum minor [S. minus]

Sodoku

026.1    Streptobacillary fever

Epidemic arthritic erythema

Haverhill fever

Rat-bite fever due to Streptobacillus moniliformis

026.9    Unspecified rat-bite fever

027       Other zoonotic bacterial diseases

027.0    Listeriosis

Infection by Listeria monocytogenes

Septicemia by Listeria monocytogenes

Use additional code to identify manifestations, as meningitis (320.7)

Excludes:          congenital listeriosis (771.2)

027.1    Erysipelothrix infection

Erysipeloid (of Rosenbach)

Infection by Erysipelothrix insidiosa [E. rhusiopathiae]

Septicemia by Erysipelothrix insidiosa [E. rhusiopathiae]

027.2    Pasteurellosis

Pasteurella pseudotuberculosis infection by Pasteurella multocida [P. septica]

Mesenteric adenitis by Pasteurella multocida [P. septica]

Septic infection (cat bite) (dog bite) by Pasteurella multocida [P. septica]

Excludes:          infection by:

Francisella [Pasteurella] tularensis (021.0-021.9)

Yersinia [Pasteurella] pestis (020.0-020.9)

027.8    Other specified zoonotic bacterial diseases

027.9    Unspecified zoonotic bacterial disease

OTHER BACTERIAL DISEASES (030-041)

Excludes:         bacterial venereal diseases (098.0-099.9)

bartonellosis (088.0)

030       Leprosy

Includes:           Hansen's disease

infection by Mycobacterium leprae

030.0    Lepromatous [type L]

Lepromatous leprosy (macular) (diffuse) (infiltrated) (nodular) (neuritic)

030.1    Tuberculoid [type T]

Tuberculoid leprosy (macular) (maculoanesthetic) (major) (minor) (neuritic)

030.2    Indeterminate [group I]

Indeterminate [uncharacteristic] leprosy (macular) (neuritic)

030.3    Borderline [group B]

Borderline or dimorphous leprosy (infiltrated) (neuritic)

030.8    Other specified leprosy

030.9    Leprosy, unspecified

031       Diseases due to other mycobacteria

031.0    Pulmonary

Infection by Mycobacterium:

avium

intracellulare [Battey bacillus]

kansasii

Battey disease

031.1    Cutaneous

Buruli ulcer

Infection by Mycobacterium:

marinum [M. balnei]

ulcerans

031.2    Disseminated

Disseminated mycobacterium avium-intracellulare complex (DMAC)

Mycobacterium avium-intracellulare complex (MAC) bacteremia

031.8    Other specified mycobacterial diseases

031.9    Unspecified diseases due to mycobacteria

Atypical mycobacterium infection NOS

032       Diphtheria

Includes:           infection by Corynebacterium diphtheriae

032.0    Faucial diphtheria

Membranous angina, diphtheritic

032.1    Nasopharyngeal diphtheria

032.2    Anterior nasal diphtheria

032.3    Laryngeal diphtheria

Laryngotracheitis, diphtheritic

032.8    Other specified diphtheria

032.81  Conjunctival diphtheria

Pseudomembranous diphtheritic conjunctivitis

032.82  Diphtheritic myocarditis

032.83  Diphtheritic peritonitis

032.84  Diphtheritic cystitis

032.85  Cutaneous diphtheria

032.89  Other

032.9    Diphtheria, unspecified

033       Whooping cough

Includes:           pertussis

Use additional code to identify any associated pneumonia (484.3)

033.0    Bordetella pertussis [B. pertussis]

033.1    Bordetella parapertussis [B. parapertussis]

033.8    Whooping cough due to other specified organism

Bordetella bronchiseptica [B. bronchiseptica]

033.9    Whooping cough, unspecified organism

034       Streptococcal sore throat and scarlet fever

034.0    Streptococcal sore throat

Septic:

angina

sore throat

Streptococcal:

angina

laryngitis

pharyngitis

tonsillitis

034.1    Scarlet fever

Scarlatina

Excludes:          parascarlatina (057.8)

035       Erysipelas

Excludes:          postpartum or puerperal erysipelas (670)

036       Meningococcal infection

036.0    Meningococcal meningitis

Cerebrospinal fever (meningococcal)

Meningitis:

cerebrospinal

epidemic

036.1    Meningococcal encephalitis

036.2    Meningococcemia

Meningococcal septicemia

036.3    Waterhouse-Friderichsen syndrome, meningococcal

Meningococcal hemorrhagic adrenalitis

Meningococcic adrenal syndrome

Waterhouse-Friderichsen syndrome NOS

036.4    Meningococcal carditis

036.40  Meningococcal carditis, unspecified

036.41  Meningococcal pericarditis

036.42  Meningococcal endocarditis

036.43  Meningococcal myocarditis

036.8    Other specified meningococcal infections

036.81  Meningococcal optic neuritis

036.82  Meningococcal arthropathy

036.89  Other

036.9    Meningococcal infection, unspecified

Meningococcal infection NOS

037       Tetanus

Excludes:          tetanus:

complicating:

abortion (634-638 with .0, 639.0)

ectopic or molar pregnancy (639.0)

neonatorum (771.3)

puerperal (670)

038       Septicemia

Use additional code for systemic inflammatory response syndrome (SIRS) (995.91-995.92)

Excludes:          bacteremia (790.7)

septicemia (sepsis) of newborn (771.81)

038.0    Streptococcal septicemia

038.1    Staphylococcal septicemia

038.10  Staphylococcal septicemia, unspecified

038.11  Staphylococcus aureus septicemia

038.19  Other staphylococcal septicemia

038.2    Pneumococcal septicemia [Streptococcus pneumoniae septicemia]

038.3    Septicemia due to anaerobes

Septicemia due to bacteroides

Excludes:          gas gangrene (040.0)

that due to anaerobic streptococci (038.0)

038.4    Septicemia due to other gram-negative organisms

038.40  Gram-negative organism, unspecified

Gram-negative septicemia NOS

038.41  Hemophilus influenzae [H. influenzae]

038.42  Escherichia coli [E. coli]

038.43  Pseudomonas

038.44  Serratia

038.49  Other

038.8    Other specified septicemias

Excludes:          septicemia (due to):

anthrax (022.3)

gonococcal (098.89)

herpetic (054.5)

meningococcal (036.2)

septicemic plague (020.2)

038.9    Unspecified septicemia

Septicemia NOS

Excludes:          bacteremia NOS (790.7)

039       Actinomycotic infections

Includes:           actinomycotic mycetoma

infection by Actinomycetales, such as species of Actinomyces, Actinomadura, Nocardia, Streptomyces

maduromycosis (actinomycotic)

schizomycetoma (actinomycotic)

039.0    Cutaneous

Erythrasma

Trichomycosis axillaris

039.1    Pulmonary

Thoracic actinomycosis

039.2    Abdominal

039.3    Cervicofacial

039.4    Madura foot

Excludes:          madura foot due to mycotic infection (117.4)

039.8    Of other specified sites

039.9    Of unspecified site

Actinomycosis NOS

Maduromycosis NOS

Nocardiosis NOS

040       Other bacterial diseases

Excludes:          bacteremia NOS (790.7)

bacterial infection NOS (041.9)

040.0    Gas gangrene

Gas bacillus infection or gangrene

Infection by Clostridium:

histolyticum

oedematiens

perfringens [welchii]

septicum

sordellii

Malignant edema

Myonecrosis, clostridial

Myositis, clostridial

040.1    Rhinoscleroma

040.2    Whipple's disease

Intestinal lipodystrophy

040.3    Necrobacillosis

040.8    Other specified bacterial diseases

040.81  Tropical pyomyositis

040.82  Toxic shock syndrome

Use additional code to identify the organism

040.89  Other

041       Bacterial infection in conditions classified elsewhere and of unspecified site

Note:    This category is provided to be used as an additional code to identify the bacterial agent in diseases classified elsewhere. This category will also be used to classify bacterial infections of unspecified nature or site.

Excludes:          bacteremia NOS (790.7)

septicemia (038.0-038.9)

041.0    Streptococcus

041.00  Streptococcus, unspecified

041.01  Group A

041.02  Group B

041.03  Group C

041.04  Group D [Enterococcus]

041.05  Group G

041.09  Other Streptococcus

041.1    Staphylococcus

041.10  Staphylococcus, unspecified

041.11  Staphylococcus aureus

041.19  Other Staphylococcus

041.2    Pneumococcus

041.3    Friedländer's bacillus

Infection by Klebsiella pneumoniae

041.4    Escherichia coli [E.coli]

041.5    Hemophilus influenzae [H. influenzae]

041.6    Proteus (mirabilis) (morganii)

041.7    Pseudomonas

041.8    Other specified bacterial infections

041.81  Mycoplasma

Eaton's agent

Pleuropneumonia-like organisms [PPLO]

041.82  Bacteroides fragilis

041.83  Clostridium perfringens

041.84  Other anaerobes

Gram-negative anaerobes

Excludes:          Helicobacter pylori (041.86)

041.85  Other gram-negative organisms

Aerobacter aerogenes

Gram-negative bacteria NOS

Mima polymorpha

Serratia

Excludes:          gram-negative anaerobes (041.84)

041.86  Helicobacter pylori (H. pylori)

041.89  Other specified bacteria

041.9    Bacterial infection, unspecified

HUMAN IMMUNODEFICIENCY VIRUS (HIV) INFECTION (042)

042       Human immunodeficiency virus [HIV] disease

Acquired immune deficiency syndrome

Acquired immunodeficiency syndrome

AIDS

AIDS-like syndrome

AIDS-related complex

ARC

HIV infection, symptomatic

Use additional code(s) to identify all manifestations of HIV

Use additional code to identify HIV-2 infection (079.53)

Excludes:          asymptomatic HIV infection status (V08)

exposure to HIV virus (V01.79)

nonspecific serologic evidence of HIV (795.71)

POLIOMYELITIS AND OTHER NON-ARTHROPOD-BORNE VIRAL DISEASES OF CENTRAL NERVOUS SYSTEM (045-049)

045       Acute poliomyelitis

Excludes:          late effects of acute poliomyelitis (138)

The following fifth-digit subclassification is for use with category 045:

0 poliovirus, unspecified type

1 poliovirus type I

2 poliovirus type II

3 poliovirus type III

045.0    Acute paralytic poliomyelitis specified as bulbar

Infantile paralysis (acute) specified as bulbar

Poliomyelitis (acute) (anterior) specified as bulbar

Polioencephalitis (acute) (bulbar)

Polioencephalomyelitis (acute) (anterior) (bulbar)

045.1    Acute poliomyelitis with other paralysis

Paralysis:

acute atrophic, spinal

infantile, paralytic

Poliomyelitis (acute) with paralysis except bulbar

anterior with paralysis except bulbar

epidemic with paralysis except bulbar

045.2    Acute nonparalytic poliomyelitis

Poliomyelitis (acute) specified as nonparalytic

anterior specified as nonparalytic

epidemic specified as nonparalytic

045.9    Acute poliomyelitis, unspecified

Infantile paralysis unspecified whether paralytic or nonparalytic

Poliomyelitis (acute) unspecified whether paralytic or nonparalytic

anterior unspecified whether paralytic or nonparalytic

epidemic unspecified whether paralytic or nonparalytic

046       Slow virus infection of central nervous system

046.0    Kuru

046.1    Jakob-Creutzfeldt disease

Subacute spongiform encephalopathy

046.2    Subacute sclerosing panencephalitis

Dawson's inclusion body encephalitis

Van Bogaert's sclerosing leukoencephalitis

046.3    Progressive multifocal leukoencephalopathy

Multifocal leukoencephalopathy NOS

046.8    Other specified slow virus infection of central nervous system

046.9    Unspecified slow virus infection of central nervous system

047       Meningitis due to enterovirus

Includes:           meningitis:

abacterial

aseptic

viral

Excludes:          meningitis due to:

adenovirus (049.1)

arthropod-borne virus (060.0-066.9)

leptospira (100.81)

virus of:

herpes simplex (054.72)

herpes zoster (053.0)

lymphocytic choriomeningitis (049.0)

mumps (072.1)

poliomyelitis (045.0-045.9)

any other infection specifically classified elsewhere

047.0    Coxsackie virus

047.1    ECHO virus

Meningo-eruptive syndrome

047.8    Other specified viral meningitis

047.9    Unspecified viral meningitis

Viral meningitis NOS

048       Other enterovirus diseases of central nervous system

Boston exanthem

049       Other non-arthropod-borne viral diseases of central nervous system

Excludes:          late effects of viral encephalitis (139.0)

049.0    Lymphocytic choriomeningitis

Lymphocytic:

meningitis (serous) (benign)

meningoencephalitis (serous) (benign)

049.1    Meningitis due to adenovirus

049.8    Other specified non-arthropod-borne viral diseases of central nervous system

Encephalitis:

acute:

inclusion body

necrotizing

epidemic

lethargica

Rio Bravo

von Economo's disease

049.9    Unspecified non-arthropod-borne viral diseases of central nervous system

Viral encephalitis NOS

VIRAL DISEASES ACCOMPANIED BY EXANTHEM (050-057)

Excludes:         arthropod-borne viral diseases (060.0-066.9)

Boston exanthem (048)

050       Smallpox

050.0    Variola major

Hemorrhagic (pustular) smallpox

Malignant smallpox

Purpura variolosa

050.1    Alastrim

Variola minor

050.2    Modified smallpox

Varioloid

050.9    Smallpox, unspecified

051       Cowpox and paravaccinia

051.0    Cowpox

Vaccinia not from vaccination

Excludes:          vaccinia (generalized) (from vaccination) (999.0)

051.1    Pseudocowpox

Milkers' node

051.2    Contagious pustular dermatitis

Ecthyma contagiosum

Orf

051.9    Paravaccinia, unspecified

052       Chickenpox

052.0    Postvaricella encephalitis

Postchickenpox encephalitis

052.1    Varicella (hemorrhagic) pneumonitis

052.7    With other specified complications

052.8    With unspecified complication

052.9    Varicella without mention of complication

Chickenpox NOS

Varicella NOS

053       Herpes zoster

Includes:           shingles

zona

053.0    With meningitis

053.1    With other nervous system complications

053.10  With unspecified nervous system complication

053.11  Geniculate herpes zoster

Herpetic geniculate ganglionitis

053.12  Postherpetic trigeminal neuralgia

053.13  Postherpetic polyneuropathy

053.19  Other

053.2    With ophthalmic complications

053.20  Herpes zoster dermatitis of eyelid

Herpes zoster ophthalmicus

053.21  Herpes zoster keratoconjunctivitis

053.22  Herpes zoster iridocyclitis

053.29  Other

053.7    With other specified complications

053.71  Otitis externa due to herpes zoster

053.79  Other

053.8    With unspecified complication

053.9    Herpes zoster without mention of complication

Herpes zoster NOS

054       Herpes simplex

Excludes:          congenital herpes simplex (771.2)

054.0    Eczema herpeticum

Kaposi's varicelliform eruption

054.1    Genital herpes

054.10  Genital herpes, unspecified

Herpes progenitalis

054.11  Herpetic vulvovaginitis

054.12  Herpetic ulceration of vulva

054.13  Herpetic infection of penis

054.19  Other

054.2    Herpetic gingivostomatitis

054.3    Herpetic meningoencephalitis

Herpes encephalitis

Simian B disease

054.4    With ophthalmic complications

054.40  With unspecified ophthalmic complication

054.41  Herpes simplex dermatitis of eyelid

054.42  Dendritic keratitis

054.43  Herpes simplex disciform keratitis

054.44  Herpes simplex iridocyclitis

054.49  Other

054.5    Herpetic septicemia

054.6    Herpetic whitlow

Herpetic felon

054.7    With other specified complications

054.71  Visceral herpes simplex

054.72  Herpes simplex meningitis

054.73  Herpes simplex otitis externa

054.79  Other

054.8    With unspecified complication

054.9    Herpes simplex without mention of complication

055       Measles

Includes:           morbilli

rubeola

055.0    Postmeasles encephalitis

055.1    Postmeasles pneumonia

055.2    Postmeasles otitis media

055.7    With other specified complications

055.71  Measles keratoconjunctivitis

Measles keratitis

055.79  Other

055.8    With unspecified complication

055.9    Measles without mention of complication

056       Rubella

Includes:           German measles

Excludes:          congenital rubella (771.0)

056.0    With neurological complications

056.00  With unspecified neurological complication

056.01  Encephalomyelitis due to rubella

Encephalitis due to rubella

Meningoencephalitis due to rubella

056.09  Other

056.7    With other specified complications

056.71  Arthritis due to rubella

056.79  Other

056.8    With unspecified complications

056.9    Rubella without mention of complication

057       Other viral exanthemata

057.0    Erythema infectiosum [fifth disease]

057.8    Other specified viral exanthemata

Dukes (-Filatow) disease

Exanthema subitum [sixth disease]

Fourth disease

Parascarlatina

Pseudoscarlatina

Roseola infantum

057.9    Viral exanthem, unspecified

ARTHROPOD-BORNE VIRAL DISEASES (060-066)

Use additional code to identify any associated meningitis (321.2)

Excludes:         late effects of viral encephalitis (139.0)

060       Yellow fever

060.0    Sylvatic

Yellow fever:

jungle

sylvan

060.1    Urban

060.9    Yellow fever, unspecified

061       Dengue

Breakbone fever

Excludes:          hemorrhagic fever caused by dengue virus (065.4)

062       Mosquito-borne viral encephalitis

062.0    Japanese encephalitis

Japanese B encephalitis

062.1    Western equine encephalitis

062.2    Eastern equine encephalitis

Excludes:          Venezuelan equine encephalitis (066.2)

062.3    St. Louis encephalitis

062.4    Australian encephalitis

Australian arboencephalitis

Australian X disease

Murray Valley encephalitis

062.5    California virus encephalitis

Encephalitis:

California

La Crosse

Tahyna fever

062.8    Other specified mosquito-borne viral encephalitis

Encephalitis by Ilheus virus

Excludes: West Nile virus (066.40-066.49)

062.9    Mosquito-borne viral encephalitis, unspecified

063       Tick-borne viral encephalitis

Includes:           diphasic meningoencephalitis

063.0    Russian spring-summer [taiga] encephalitis

063.1    Louping ill

063.2    Central European encephalitis

063.8    Other specified tick-borne viral encephalitis

Langat encephalitis

Powassan encephalitis

063.9    Tick-borne viral encephalitis, unspecified

064       Viral encephalitis transmitted by other and unspecified arthropods

Arthropod-borne viral encephalitis, vector unknown

Negishi virus encephalitis

Excludes:          viral encephalitis NOS (049.9)

065       Arthropod-borne hemorrhagic fever

065.0    Crimean hemorrhagic fever [CHF Congo virus]

Central Asian hemorrhagic fever

065.1    Omsk hemorrhagic fever

065.2    Kyasanur Forest disease

065.3    Other tick-borne hemorrhagic fever

065.4    Mosquito-borne hemorrhagic fever

Chikungunya hemorrhagic fever

Dengue hemorrhagic fever

Excludes:          Chikungunya fever (066.3)

dengue (061)

yellow fever (060.0-060.9)

065.8    Other specified arthropod-borne hemorrhagic fever

Mite-borne hemorrhagic fever

065.9    Arthropod-borne hemorrhagic fever, unspecified

Arbovirus hemorrhagic fever NOS

066       Other arthropod-borne viral diseases

066.0    Phlebotomus fever

Changuinola fever

Sandfly fever

066.1    Tick-borne fever

Nairobi sheep disease

Tick fever:

American mountain

Colorado

Kemerovo

Quaranfil

066.2    Venezuelan equine fever

Venezuelan equine encephalitis

066.3    Other mosquito-borne fever

Fever (viral):

Bunyamwera

Bwamba

Chikungunya

Guama

Mayaro

Mucambo

O'Nyong-Nyong

Oropouche

Pixuna

Rift valley

Ross river

Wesselsbron

Zika

Excludes:          dengue (061)

yellow fever (060.0-060.9)

066.4    West Nile fever

066.40 West Nile fever, unspecified

West Nile fever NOS

West Nile fever without complications

West Nile virus NOS

066.41  West Nile fever with encephalitis

West Nile encephalitis

West Nile encephalomyelitis

066.42  West Nile fever with other neurologic manifestation

Use additional code to specify the neurologic manifestation

066.49  West Nile fever with other complications

Use additional code to specify the other conditions

066.8    Other specified arthropod-borne viral diseases

Chandipura fever

Piry fever

066.9    Arthropod-borne viral disease, unspecified

Arbovirus infection NOS

OTHER DISEASES DUE TO VIRUSES AND CHLAMYDIAE (070-079)

070       Viral hepatitis

Includes:           viral hepatitis (acute) (chronic)

Excludes:          cytomegalic inclusion virus hepatitis (078.5)

The following fifth-digit subclassification is for use with categories 070.2 and 070.3:

0 acute or unspecified, without mention of hepatitis delta

1 acute or unspecified, with hepatitis delta

2 chronic, without mention of hepatitis delta

3 chronic, with hepatitis delta

070.0    Viral hepatitis A with hepatic coma

070.1    Viral hepatitis A without mention of hepatic coma

Infectious hepatitis

070.2    Viral hepatitis B with hepatic coma

070.3    Viral hepatitis B without mention of hepatic coma

Serum hepatitis

070.4    Other specified viral hepatitis with hepatic coma

070.41  Acute hepatitis C with hepatic coma

070.42  Hepatitis delta without mention of active hepatitis B disease with hepatic coma

Hepatitis delta with hepatitis B carrier state

070.43  Hepatitis E with hepatic coma

070.44  Chronic hepatitis C with hepatic coma

070.49  Other specified viral hepatitis with hepatic coma

070.5    Other specified viral hepatitis without mention of hepatic coma

070.51  Acute hepatitis C without mention of hepatic coma

070.52  Hepatitis delta without mention of active hepatitis B disease or hepatic coma

070.53  Hepatitis E without mention of hepatic coma

070.54  Chronic hepatitis C without mention of hepatic coma

070.59  Other specified viral hepatitis without mention of hepatic coma

070.6    Unspecified viral hepatitis with hepatic coma

Excludes:          unspecified viral hepatitis C with hepatic coma (070.71)

070.7    Unspecified viral hepatitis C

070.70  Unspecified viral hepatitis C without hepatic coma

Unspecified viral hepatitis C NOS

070.71  Unspecified viral hepatitis C with hepatic coma

070.9    Unspecified viral hepatitis without mention of hepatic coma

Viral hepatitis NOS

Excludes:          unspecified viral hepatitis C without hepatic coma (070.70)

071       Rabies

Hydrophobia

Lyssa

072       Mumps

072.0    Mumps orchitis

072.1    Mumps meningitis

072.2    Mumps encephalitis

Mumps meningoencephalitis

072.3    Mumps pancreatitis

072.7    Mumps with other specified complications

072.71  Mumps hepatitis

072.72  Mumps polyneuropathy

072.79  Other

072.8    Mumps with unspecified complication

072.9    Mumps without mention of complication

Epidemic parotitis

Infectious parotitis

073       Ornithosis

Includes:           parrot fever

psittacosis

073.0    With pneumonia

Lobular pneumonitis due to ornithosis

073.7    With other specified complications

073.8    With unspecified complication

073.9    Ornithosis, unspecified

074       Specific diseases due to Coxsackie virus

Excludes:          Coxsackie virus:

infection NOS (079.2)

meningitis (047.0)

074.0    Herpangina

Vesicular pharyngitis

074.1    Epidemic pleurodynia

Bornholm disease

Devil's grip

Epidemic:

myalgia

myositis

074.2    Coxsackie carditis

074.20  Coxsackie carditis, unspecified

074.21  Coxsackie pericarditis

074.22  Coxsackie endocarditis

074.23  Coxsackie myocarditis

   Aseptic myocarditis of newborn

074.3    Hand, foot, and mouth disease

Vesicular stomatitis and exanthem

074.8    Other specified diseases due to Coxsackie virus

Acute lymphonodular pharyngitis

075       Infectious mononucleosis

Glandular fever

Monocytic angina

Pfeiffer's disease

076       Trachoma

Excludes:          late effect of trachoma (139.1)

076.0    Initial stage

Trachoma dubium

076.1    Active stage

Granular conjunctivitis (trachomatous)

Trachomatous:

follicular conjunctivitis

pannus

076.9    Trachoma, unspecified

Trachoma NOS

077       Other diseases of conjunctiva due to viruses and Chlamydiae

Excludes:          ophthalmic complications of viral diseases classified elsewhere

077.0    Inclusion conjunctivitis

Paratrachoma

Swimming pool conjunctivitis

Excludes:          inclusion blennorrhea (neonatal) (771.6)

077.1    Epidemic keratoconjunctivitis

Shipyard eye

077.2    Pharyngoconjunctival fever

Viral pharyngoconjunctivitis

077.3    Other adenoviral conjunctivitis

Acute adenoviral follicular conjunctivitis

077.4    Epidemic hemorrhagic conjunctivitis

Apollo:

conjunctivitis

disease

Conjunctivitis due to enterovirus type 70

Hemorrhagic conjunctivitis (acute) (epidemic)

077.8    Other viral conjunctivitis

Newcastle conjunctivitis

077.9    Unspecified diseases of conjunctiva due to viruses and Chlamydiae

077.98  Due to Chlamydiae

077.99  Due to viruses

Viral conjunctivitis NOS

078       Other diseases due to viruses and Chlamydiae

Excludes:          viral infection NOS (079.0-079.9)

viremia NOS (790.8)

078.0    Molluscum contagiosum

078.1    Viral warts

Viral warts due to human papillomavirus

078.10  Viral warts, unspecified

Condyloma NOS

Verruca NOS:

NOS

Vulgaris

Warts (infectious)

078.11  Condyloma acuminatum

078.19  Other specified viral warts

Genital warts NOS

Verruca

plana

plantaris

078.2    Sweating fever

Miliary fever

Sweating disease

078.3    Cat-scratch disease

Benign lymphoreticulosis (of inoculation)

Cat-scratch fever

078.4    Foot and mouth disease

Aphthous fever

Epizootic:

aphthae

stomatitis

078.5    Cytomegaloviral disease

Cytomegalic inclusion disease

Salivary gland virus disease

Use additional code to identify manifestation, as:

cytomegalic inclusion virus:

hepatitis (573.1)

pneumonia (484.1)

Excludes:          congenital cytomegalovirus infection (771.1)

078.6    Hemorrhagic nephrosonephritis

Hemorrhagic fever:

epidemic

Korean

Russian with renal syndrome

078.7    Arenaviral hemorrhagic fever

Hemorrhagic fever:

Argentine

Bolivian

Junin virus

Machupo virus

078.8    Other specified diseases due to viruses and Chlamydiae

Excludes:          epidemic diarrhea (009.2)

lymphogranuloma venereum (099.1)

078.81  Epidemic vertigo

078.82  Epidemic vomiting syndrome

Winter vomiting disease

078.88  Other specified diseases due to Chlamydiae

078.89  Other specified diseases due to viruses

Epidemic cervical myalgia

Marburg disease

Tanapox

079       Viral and chlamydial infection in conditions classified elsewhere and of unspecified site

Note:    This category is provided to be used as an additional code to identify the viral agent in diseases classifiable elsewhere. This category will also be used to classify virus infection of unspecified nature or site.

079.0    Adenovirus

079.1    ECHO virus

079.2    Coxsackie virus

079.3    Rhinovirus

079.4    Human papillomavirus

079.5    Retrovirus

Excludes:          human immunodeficiency virus, type 1 [HIV-1] (042)

human T-cell lymphotrophic virus, type III [HTLV-III] (042)

lymphadenopathy-associated virus [LAV] (042)

079.50  Retrovirus, unspecified

079.51  Human T-cell lymphotrophic virus, type I [HTLV-I]

079.52  Human T-cell lymphotrophic virus, type II [HTLV-II]

079.53  Human immunodeficiency virus, type 2 [HIV-2]

079.59  Other specified retrovirus

079.6    Respiratory syncytial virus (RSV)

079.8    Other specified viral and chlamydial infections

079.81  Hantavirus

079.82  SARS-associated coronavirus

079.88  Other specified chlamydial infection

079.89  Other specified viral infection

079.9    Unspecified viral and chlamydial infections

Excludes:          viremia NOS (790.8)

079.98  Unspecified chlamydial infection

Chlamydial infection NOS

079.99  Unspecified viral infection

Viral infection NOS

RICKETTSIOSES AND OTHER ARTHROPOD-BORNE DISEASES (080-088)

Excludes:         arthropod-borne viral diseases (060.0-066.9)

080       Louse-borne [epidemic] typhus

Typhus (fever):

classical

epidemic

exanthematic NOS

louse-borne

081       Other typhus

081.0    Murine [endemic] typhus

Typhus (fever):

endemic

flea-borne

081.1    Brill's disease

Brill-Zinsser disease

Recrudescent typhus (fever)

081.2    Scrub typhus

Japanese river fever

Kedani fever

Mite-borne typhus

Tsutsugamushi

081.9    Typhus, unspecified

Typhus (fever) NOS

082       Tick-borne rickettsioses

082.0    Spotted fevers

Rocky mountain spotted fever

Sao Paulo fever

082.1    Boutonneuse fever

African tick typhus

India tick typhus

Kenya tick typhus

Marseilles fever

Mediterranean tick fever

082.2    North Asian tick fever

Siberian tick typhus

082.3    Queensland tick typhus

082.4    Ehrlichiosis

082.40  Ehrlichiosis, unspecified

082.41  Ehrlichiosis chaffeensis [E. chaffeensis]

082.49  Other ehrlichiosis

082.8    Other specified tick-borne rickettsioses

Lone star fever

082.9    Tick-borne rickettsiosis, unspecified

Tick-borne typhus NOS

083       Other rickettsioses

083.0    Q fever

083.1    Trench fever

Quintan fever

Wolhynian fever

083.2    Rickettsialpox

Vesicular rickettsiosis

083.8    Other specified rickettsioses

083.9    Rickettsiosis, unspecified

084       Malaria

Note:    Subcategories 084.0-084.6 exclude the listed conditions with mention of pernicious complications (084.8-084.9).

Excludes:          congenital malaria (771.2)

084.0    Falciparum malaria [malignant tertian]

Malaria (fever):

by Plasmodium falciparum

subtertian

084.1    Vivax malaria [benign tertian]

Malaria (fever) by Plasmodium vivax

084.2    Quartan malaria

Malaria (fever) by Plasmodium malariae

Malariae malaria

084.3    Ovale malaria

Malaria (fever) by Plasmodium ovale

084.4    Other malaria

Monkey malaria

084.5    Mixed malaria

Malaria (fever) by more than one parasite

084.6    Malaria, unspecified

Malaria (fever) NOS

084.7    Induced malaria

Therapeutically induced malaria

Excludes:          accidental infection from syringe, blood transfusion, etc. (084.0-084.6, above, according to parasite species)

transmission from mother to child during delivery (771.2)

084.8    Blackwater fever

Hemoglobinuric:

fever (bilious)

malaria

Malarial hemoglobinuria

084.9    Other pernicious complications of malaria

Algid malaria

Cerebral malaria

Use additional code to identify complication, as:

malarial:

hepatitis (573.2)

nephrosis (581.81)

085       Leishmaniasis

085.0    Visceral [kala-azar]

Dumdum fever

Infection by Leishmania:

donovani

infantum

Leishmaniasis:

dermal, post-kala-azar

Mediterranean

visceral (Indian)

085.1    Cutaneous, urban

Aleppo boil

Baghdad boil

Delhi boil

Infection by Leishmania tropica (minor)

Leishmaniasis, cutaneous:

dry form

late

recurrent

ulcerating

Oriental sore

085.2    Cutaneous, Asian desert

Infection by Leishmania tropica major

Leishmaniasis, cutaneous:

acute necrotizing

rural

wet form

zoonotic form

085.3    Cutaneous, Ethiopian

Infection by Leishmania ethiopica

Leishmaniasis, cutaneous:

diffuse

lepromatous

085.4    Cutaneous, American

Chiclero ulcer

Infection by Leishmania mexicana

Leishmaniasis tegumentaria diffusa

085.5    Mucocutaneous (American)

Espundia

Infection by Leishmania braziliensis

Uta

085.9    Leishmaniasis, unspecified

086       Trypanosomiasis

Use additional code to identify manifestations, as:

trypanosomiasis:

encephalitis (323.2)

meningitis (321.3)

086.0    Chagas' disease with heart involvement

American trypanosomiasis with heart involvement

Infection by Trypanosoma cruzi with heart involvement

Any condition classifiable to 086.2 with heart involvement

086.1    Chagas' disease with other organ involvement

American trypanosomiasis with involvement of organ other than heart

Infection by Trypanosoma cruzi with involvement of organ other than heart

Any condition classifiable to 086.2 with involvement of organ other than heart

086.2    Chagas' disease without mention of organ involvement

American trypanosomiasis

Infection by Trypanosoma cruzi

086.3    Gambian trypanosomiasis

Gambian sleeping sickness

Infection by Trypanosoma gambiense

086.4    Rhodesian trypanosomiasis

Infection by Trypanosoma rhodesiense

Rhodesian sleeping sickness

086.5    African trypanosomiasis, unspecified

Sleeping sickness NOS

086.9    Trypanosomiasis, unspecified

087       Relapsing fever

Includes:           recurrent fever

087.0    Louse-borne

087.1    Tick-borne

087.9    Relapsing fever, unspecified

088       Other arthropod-borne diseases

088.0    Bartonellosis

Carrión's disease

Oroya fever

Verruga peruana

088.8    Other specified arthropod-borne diseases

088.81  Lyme disease

Erythema chronicum migrans

088.82  Babesiosis

Babesiasis

088.89  Other

088.9    Arthropod-borne disease, unspecified

SYPHILIS AND OTHER VENEREAL DISEASES (090-099)

Excludes:         nonvenereal endemic syphilis (104.0)

urogenital trichomoniasis (131.0)

090       Congenital syphilis

090.0    Early congenital syphilis, symptomatic

Congenital syphilitic:

choroiditis

coryza (chronic)

hepatomegaly

mucous patches

periostitis

splenomegaly

Syphilitic (congenital):

epiphysitis

osteochondritis

pemphigus

Any congenital syphilitic condition specified as early or manifest less than two years after birth

090.1    Early congenital syphilis, latent

Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after birth

090.2    Early congenital syphilis, unspecified

Congenital syphilis NOS, less than two years after birth

090.3    Syphilitic interstitial keratitis

Syphilitic keratitis:

parenchymatous

punctata profunda

Excludes:          interstitial keratitis NOS (370.50)

090.4    Juvenile neurosyphilis

Use additional code to identify any associated mental disorder

090.40  Juvenile neurosyphilis, unspecified

Congenital neurosyphilis

Dementia paralytica juvenilis

Juvenile:

general paresis

tabes

taboparesis

090.41  Congenital syphilitic encephalitis

090.42  Congenital syphilitic meningitis

090.49  Other

090.5    Other late congenital syphilis, symptomatic

Gumma due to congenital syphilis

Hutchinson's teeth

Syphilitic saddle nose

Any congenital syphilitic condition specified as late or manifest two years or more after birth

090.6    Late congenital syphilis, latent

Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after birth

090.7    Late congenital syphilis, unspecified

Congenital syphilis NOS, two years or more after birth

090.9    Congenital syphilis, unspecified

091       Early syphilis, symptomatic

Excludes:          early cardiovascular syphilis (093.0-093.9)

early neurosyphilis (094.0-094.9)

091.0    Genital syphilis (primary)

Genital chancre

091.1    Primary anal syphilis

091.2    Other primary syphilis

Primary syphilis of:

breast

fingers

lip

tonsils

091.3    Secondary syphilis of skin or mucous membranes

Condyloma latum

Secondary syphilis of:

anus

mouth

pharynx

skin

tonsils

vulva

091.4    Adenopathy due to secondary syphilis

Syphilitic adenopathy (secondary)

Syphilitic lymphadenitis (secondary)

091.5    Uveitis due to secondary syphilis

091.50  Syphilitic uveitis, unspecified

091.51  Syphilitic chorioretinitis (secondary)

091.52  Syphilitic iridocyclitis (secondary)

091.6    Secondary syphilis of viscera and bone

091.61  Secondary syphilitic periostitis

091.62  Secondary syphilitic hepatitis

Secondary syphilis of liver

091.69  Other viscera

091.7    Secondary syphilis, relapse

Secondary syphilis, relapse (treated) (untreated)

091.8    Other forms of secondary syphilis

091.81  Acute syphilitic meningitis (secondary)

091.82  Syphilitic alopecia

091.89  Other

091.9    Unspecified secondary syphilis

092       Early syphilis, latent

Includes:           syphilis (acquired) without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after infection

092.0    Early syphilis, latent, serological relapse after treatment

092.9    Early syphilis, latent, unspecified

093       Cardiovascular syphilis

093.0    Aneurysm of aorta, specified as syphilitic

Dilatation of aorta, specified as syphilitic

093.1    Syphilitic aortitis

093.2    Syphilitic endocarditis

093.20  Valve, unspecified

Syphilitic ostial coronary disease

093.21  Mitral valve

093.22  Aortic valve

Syphilitic aortic incompetence or stenosis

093.23  Tricuspid valve

093.24  Pulmonary valve

093.8    Other specified cardiovascular syphilis

093.81  Syphilitic pericarditis

093.82  Syphilitic myocarditis

093.89  Other

093.9    Cardiovascular syphilis, unspecified

094       Neurosyphilis

Use additional code to identify any associated mental disorder

094.0    Tabes dorsalis

Locomotor ataxia (progressive)

Posterior spinal sclerosis (syphilitic)

Tabetic neurosyphilis

Use additional code to identify manifestation, as:

neurogenic arthropathy [Charcot's joint disease] (713.5)

094.1    General paresis

Dementia paralytica

General paralysis (of the insane) (progressive)

Paretic neurosyphilis

Taboparesis

094.2    Syphilitic meningitis

Meningovascular syphilis

Excludes:          acute syphilitic meningitis (secondary) (091.81)

094.3    Asymptomatic neurosyphilis

094.8    Other specified neurosyphilis

094.81  Syphilitic encephalitis

094.82  Syphilitic Parkinsonism

094.83  Syphilitic disseminated retinochoroiditis

094.84  Syphilitic optic atrophy

094.85  Syphilitic retrobulbar neuritis

094.86  Syphilitic acoustic neuritis

094.87  Syphilitic ruptured cerebral aneurysm

094.89  Other

094.9    Neurosyphilis, unspecified

Gumma (syphilitic) of central nervous system NOS

Syphilis (early) (late) of central nervous system NOS

Syphiloma of central nervous system NOS

095       Other forms of late syphilis, with symptoms

Includes:           gumma (syphilitic)

tertiary, or unspecified stage

095.0    Syphilitic episcleritis

095.1    Syphilis of lung

095.2    Syphilitic peritonitis

095.3    Syphilis of liver

095.4    Syphilis of kidney

095.5    Syphilis of bone

095.6    Syphilis of muscle

Syphilitic myositis

095.7    Syphilis of synovium, tendon, and bursa

Syphilitic:

bursitis

synovitis

095.8    Other specified forms of late symptomatic syphilis

Excludes:          cardiovascular syphilis (093.0-093.9)

neurosyphilis (094.0-094.9)

095.9    Late symptomatic syphilis, unspecified

096       Late syphilis, latent

Syphilis (acquired) without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after infection

097       Other and unspecified syphilis

097.0    Late syphilis, unspecified

097.1    Latent syphilis, unspecified

Positive serological reaction for syphilis

097.9    Syphilis, unspecified

Syphilis (acquired) NOS

Excludes:          syphilis NOS causing death under two years of age (090.9)

098       Gonococcal infections

098.0    Acute, of lower genitourinary tract

Gonococcal:

Bartholinitis (acute)

urethritis (acute)

vulvovaginitis (acute)

Gonorrhea (acute):

NOS

genitourinary (tract) NOS

098.1    Acute, of upper genitourinary tract

098.10  Gonococcal infection (acute) of upper genitourinary tract, site unspecified

098.11  Gonococcal cystitis (acute)

Gonorrhea (acute) of bladder

098.12  Gonococcal prostatitis (acute)

098.13  Gonococcal epididymo-orchitis (acute)

Gonococcal orchitis (acute)

098.14  Gonococcal seminal vesiculitis (acute)

Gonorrhea (acute) of seminal vesicle

098.15  Gonococcal cervicitis (acute)

Gonorrhea (acute) of cervix

098.16  Gonococcal endometritis (acute)

Gonorrhea (acute) of uterus

098.17  Gonococcal salpingitis, specified as acute

098.19  Other

098.2    Chronic, of lower genitourinary tract

Gonococcal specified as chronic or with duration of two months or more:

Bartholinitis specified as chronic or with duration of two months or more

urethritis specified as chronic or with duration of two months or more

vulvovaginitis specified as chronic or with duration of two months or more

Gonorrhea specified as chronic or with duration of two months or more:

NOS specified as chronic or with duration of two months or more

genitourinary (tract) specified as chronic or with duration of two months or more

Any condition classifiable to 098.0 specified as chronic or with duration of two months or more

098.3    Chronic, of upper genitourinary tract

Any condition classifiable to 098.1 stated as chronic or with a duration of two months or more

098.30  Chronic gonococcal infection of upper genitourinary tract, site unspecified

098.31  Gonococcal cystitis, chronic

Any condition classifiable to 098.11, specified as chronic

Gonorrhea of bladder, chronic

098.32  Gonococcal prostatitis, chronic

Any condition classifiable to 098.12, specified as chronic

098.33  Gonococcal epididymo-orchitis, chronic

Any condition classifiable to 098.13, specified as chronic

Chronic gonococcal orchitis

098.34  Gonococcal seminal vesiculitis, chronic

Any condition classifiable to 098.14, specified as chronic

Gonorrhea of seminal vesicle, chronic

098.35  Gonococcal cervicitis, chronic

Any condition classifiable to 098.15, specified as chronic

Gonorrhea of cervix, chronic

098.36  Gonococcal endometritis, chronic

Any condition classifiable to 098.16, specified as chronic

098.37  Gonococcal salpingitis (chronic)

098.39  Other

098.4    Gonococcal infection of eye

098.40  Gonococcal conjunctivitis (neonatorum)

Gonococcal ophthalmia (neonatorum)

098.41  Gonococcal iridocyclitis

098.42  Gonococcal endophthalmia

098.43  Gonococcal keratitis

098.49  Other

098.5    Gonococcal infection of joint

098.50  Gonococcal arthritis

Gonococcal infection of joint NOS

098.51  Gonococcal synovitis and tenosynovitis

098.52  Gonococcal bursitis

098.53  Gonococcal spondylitis

098.59  Other

Gonococcal rheumatism

098.6    Gonococcal infection of pharynx

098.7    Gonococcal infection of anus and rectum

Gonococcal proctitis

098.8    Gonococcal infection of other specified sites

098.81  Gonococcal keratosis (blennorrhagica)

098.82  Gonococcal meningitis

098.83  Gonococcal pericarditis

098.84  Gonococcal endocarditis

098.85  Other gonococcal heart disease

098.86  Gonococcal peritonitis

098.89  Other

Gonococcemia

099       Other venereal diseases

099.0    Chancroid

Bubo (inguinal):

chancroidal

due to Hemophilus ducreyi

Chancre:

Ducrey's simple soft

Ulcus molle (cutis) (skin)

099.1    Lymphogranuloma venereum

Climatic or tropical bubo

(Durand-) Nicolas-Favre disease

Esthiomene

Lymphogranuloma inguinale

099.2    Granuloma inguinale

Donovanosis

Granuloma pudendi (ulcerating)

Granuloma venereum

Pudendal ulcer

099.3    Reiter's disease

Reiter's syndrome

Use additional code for associated:

arthropathy (711.1)

conjunctivitis (372.33)

099.4    Other nongonococcal urethritis [NGU]

099.40  Unspecified

Nonspecific urethritis

099.41  Chlamydia trachomatis

099.49  Other specified organism

099.5    Other venereal diseases due to Chlamydia trachomatis

Excludes:          Chlamydia trachomatis infection of conjunctiva (076.0-076.9, 077.0, 077.9)

Lymphogranuloma venereum (099.1)

099.50  Unspecified site

099.51  Pharynx

099.52  Anus and rectum

099.53  Lower genitourinary sites

Excludes:          urethra (099.41)

Use additional code to specify site of infection, such as:

bladder (595.4)

cervix (616.0)

vagina and vulva (616.11)

099.54  Other genitourinary sites

Use additional code to specify site of infection, such as:

pelvic inflammatory disease NOS (614.9)

testis and epididymis (604.91)

099.55  Unspecified genitourinary site

099.56  Peritoneum

Perihepatitis

099.59  Other specified site

099.8    Other specified venereal diseases

099.9    Venereal disease, unspecified

OTHER SPIROCHETAL DISEASES (100-104)

100       Leptospirosis

100.0    Leptospirosis icterohemorrhagica

Leptospiral or spirochetal jaundice (hemorrhagic)

Weil's disease

100.8    Other specified leptospiral infections

100.81  Leptospiral meningitis (aseptic)

100.89  Other

Fever:

Fort Bragg

pretibial

swamp

Infection by Leptospira:

australis

bataviae

pyrogenes

100.9    Leptospirosis, unspecified

101       Vincent's angina

Acute necrotizing ulcerative:

gingivitis

stomatitis

Fusospirochetal pharyngitis

Spirochetal stomatitis

Trench mouth

Vincent's:

gingivitis

infection [any site]

102       Yaws

Includes:           frambesia

pian

102.0    Initial lesions

Chancre of yaws

Frambesia, initial or primary

Initial frambesial ulcer

Mother yaw

102.1    Multiple papillomata and wet crab yaws

Butter yaws

Frambesioma

Pianoma

Plantar or palmar papilloma of yaws

102.2    Other early skin lesions

Early yaws (cutaneous) (macular) (papular) (maculopapular) (micropapular)

Frambeside of early yaws

Cutaneous yaws, less than five years after infection

102.3    Hyperkeratosis

Ghoul hand

Hyperkeratosis, palmar or plantar (early) (late) due to yaws

Worm-eaten soles

102.4    Gummata and ulcers

Nodular late yaws (ulcerated)

Gummatous frambeside

102.5    Gangosa

Rhinopharyngitis mutilans

102.6    Bone and joint lesions

Goundou of yaws (late)

Gumma, bone of yaws (late)

Gummatous osteitis or periostitis of yaws (late)

Hydrarthrosis of yaws (early) (late)

Osteitis of yaws (early) (late)

Periostitis (hypertrophic) of yaws (early) (late)

102.7    Other manifestations

Juxta-articular nodules of yaws

Mucosal yaws

102.8    Latent yaws

Yaws without clinical manifestations, with positive serology

102.9    Yaws, unspecified

103       Pinta

103.0    Primary lesions

Chancre (primary) of pinta [carate]

Papule (primary) of pinta [carate]

Pintid of pinta [carate]

103.1    Intermediate lesions

Erythematous plaques of pinta [carate]

Hyperchromic lesions of pinta [carate]

Hyperkeratosis of pinta [carate]

103.2    Late lesions

Cardiovascular lesions of pinta [carate]

Skin lesions of pinta [carate]:

achromic of pinta [carate]

cicatricial of pinta [carate]

dyschromic of pinta [carate]

Vitiligo of pinta [carate]

103.3    Mixed lesions

Achromic and hyperchromic skin lesions of pinta [carate]

103.9    Pinta, unspecified

104       Other spirochetal infection

104.0    Nonvenereal endemic syphilis

Bejel

Njovera

104.8    Other specified spirochetal infections

Excludes:          relapsing fever (087.0-087.9)

syphilis (090.0-097.9)

104.9    Spirochetal infection, unspecified

MYCOSES (110-118)

Use additional code to identify manifestation, as:

arthropathy (711.6)

meningitis (321.0-321.1)

otitis externa (380.15)

Excludes:         infection by Actinomycetales, such as species of Actinomyces, Actinomadura, Nocardia, Streptomyces (039.0-039.9)

110       Dermatophytosis

Includes:           infection by species of Epidermophyton, Microsporum, and Trichophyton

tinea, any type except those in 111

110.0    Of scalp and beard

Kerion

Sycosis, mycotic

Trichophytic tinea [black dot tinea], scalp

110.1    Of nail

Dermatophytic onychia

Onychomycosis

Tinea unguium

110.2    Of hand

Tinea manuum

110.3    Of groin and perianal area

Dhobie itch

Eczema marginatum

Tinea cruris

110.4    Of foot

Athlete's foot

Tinea pedis

110.5    Of the body

Herpes circinatus

Tinea imbricata [Tokelau]

110.6    Deep seated dermatophytosis

Granuloma trichophyticum

Majocchi's granuloma

110.8    Of other specified sites

110.9    Of unspecified site

Favus NOS

Microsporic tinea NOS

Ringworm NOS

111       Dermatomycosis, other and unspecified

111.0    Pityriasis versicolor

Infection by Malassezia [Pityrosporum] furfur

Tinea flava

Tinea versicolor

111.1    Tinea nigra

Infection by Cladosporium species

Keratomycosis nigricans

Microsporosis nigra

Pityriasis nigra

Tinea palmaris nigra

111.2    Tinea blanca

Infection by Trichosporon (beigelii) cutaneum

White piedra

111.3    Black piedra

Infection by Piedraia hortai

111.8    Other specified dermatomycoses

111.9    Dermatomycosis, unspecified

112       Candidiasis

Includes:           infection by Candida species

moniliasis

Excludes:          neonatal monilial infection (771.7)

112.0    Of mouth

Thrush (oral)

112.1    Of vulva and vagina

Candidal vulvovaginitis

Monilial vulvovaginitis

112.2    Of other urogenital sites

Candidal balanitis

112.3    Of skin and nails

Candidal intertrigo

Candidal onychia

Candidal perionyxis [paronychia]

112.4    Of lung

Candidal pneumonia

112.5    Disseminated

Systemic candidiasis

112.8    Of other specified sites

112.81  Candidal endocarditis

112.82  Candidal otitis externa

Otomycosis in moniliasis

112.83  Candidal meningitis

112.84  Candidal esophagitis

112.85  Candidal enteritis

112.89  Other

112.9    Of unspecified site

114       Coccidioidomycosis

Includes:           infection by Coccidioides (immitis)

Posada-Wernicke disease

114.0    Primary coccidioidomycosis (pulmonary)

Acute pulmonary coccidioidomycosis

Coccidioidomycotic pneumonitis

Desert rheumatism

Pulmonary coccidioidomycosis

San Joaquin Valley fever

114.1    Primary extrapulmonary coccidioidomycosis

Chancriform syndrome

Primary cutaneous coccidioidomycosis

114.2    Coccidioidal meningitis

114.3    Other forms of progressive coccidioidomycosis

Coccidioidal granuloma

Disseminated coccidioidomycosis

114.4    Chronic pulmonary coccidioidomycosis

114.5    Pulmonary coccidioidomycosis, unspecified

114.9    Coccidioidomycosis, unspecified

115       Histoplasmosis

The following fifth-digit subclassification is for use with category 115:

0 without mention of manifestation

1 meningitis

2 retinitis

3 pericarditis

4 endocarditis

5 pneumonia

9 other

115.0    Infection by Histoplasma capsulatum

American histoplasmosis

Darling's disease

Reticuloendothelial cytomycosis

Small form histoplasmosis

115.1    Infection by Histoplasma duboisii

African histoplasmosis

Large form histoplasmosis

115.9    Histoplasmosis, unspecified

Histoplasmosis NOS

116       Blastomycotic infection

116.0    Blastomycosis

Blastomycotic dermatitis

Chicago disease

Cutaneous blastomycosis

Disseminated blastomycosis

Gilchrist's disease

Infection by Blastomyces [Ajellomyces] dermatitidis

North American blastomycosis

Primary pulmonary blastomycosis

116.1    Paracoccidioidomycosis

Brazilian blastomycosis

Infection by Paracoccidioides [Blastomyces] brasiliensis

Lutz-Splendore-Almeida disease

Mucocutaneous-lymphangitic paracoccidioidomycosis

Pulmonary paracoccidioidomycosis

South American blastomycosis

Visceral paracoccidioidomycosis

116.2    Lobomycosis

Infections by Loboa [Blastomyces] loboi

Keloidal blastomycosis

Lobo's disease

117       Other mycoses

117.0    Rhinosporidiosis

Infection by Rhinosporidium seeberi

117.1    Sporotrichosis

Cutaneous sporotrichosis

Disseminated sporotrichosis

Infection by Sporothrix [Sporotrichum] schenckii

Lymphocutaneous sporotrichosis

Pulmonary sporotrichosis

Sporotrichosis of the bones

117.2    Chromoblastomycosis

Chromomycosis

Infection by Cladosporidium carrionii, Fonsecaea compactum, Fonsecaea pedrosoi, Phialophora verrucosa

117.3    Aspergillosis

Infection by Aspergillus species, mainly A. fumigatus, A. flavus group, A. terreus group

117.4    Mycotic mycetomas

Infection by various genera and species of Ascomycetes and Deuteromycetes, such as Acremonium [Cephalosporium] falciforme, Neotestudina rosatii, Madurella grisea, Madurella mycetomii, Pyrenochaeta romeroi, Zopfia [Leptosphaeria] senegalensis

Madura foot, mycotic

Maduromycosis, mycotic

Excludes:          actinomycotic mycetomas (039.0-039.9)

117.5    Cryptococcosis

Busse-Buschke's disease

European cryptococcosis

Infection by Cryptococcus neoformans

Pulmonary cryptococcosis

Systemic cryptococcosis

Torula

117.6    Allescheriosis [Petriellidosis]

Infections by Allescheria [Petriellidium] boydii [Monosporium apiospermum]

Excludes:          mycotic mycetoma (117.4)

117.7    Zygomycosis [Phycomycosis or Mucormycosis]

Infection by species of Absidia, Basidiobolus, Conidiobolus, Cunninghamella, Entomophthora, Mucor, Rhizopus, Saksenaea

117.8    Infection by dematiacious fungi [Phaehyphomycosis]

Infection by dematiacious fungi, such as Cladosporium trichoides [bantianum], Dreschlera hawaiiensis, Phialophora gougerotii, Phialophora jeanselmi

117.9    Other and unspecified mycoses

118       Opportunistic mycoses

Infection of skin, subcutaneous tissues, and/or organs by a wide variety of fungi generally considered to be pathogenic to compromised hosts only (e.g., infection by species of Alternaria, Dreschlera, Fusarium)

HELMINTHIASES (120-129)

120       Schistosomiasis [bilharziasis]

120.0    Schistosoma haematobium

Vesical schistosomiasis NOS

120.1    Schistosoma mansoni

Intestinal schistosomiasis NOS

120.2    Schistosoma japonicum

Asiatic schistosomiasis NOS

Katayama disease or fever

120.3    Cutaneous

Cercarial dermatitis

Infection by cercariae of Schistosoma

Schistosome dermatitis

Swimmers' itch

120.8    Other specified schistosomiasis

Infection by Schistosoma:

bovis

intercalatum

mattheii

Infection by Schistosoma spindale

Schistosomiasis chestermani

120.9    Schistosomiasis, unspecified

Blood flukes NOS

Hemic distomiasis

121       Other trematode infections

121.0    Opisthorchiasis

Infection by:

cat liver fluke

Opisthorchis (felineus) (tenuicollis) (viverrini)

121.1    Clonorchiasis

Biliary cirrhosis due to clonorchiasis

Chinese liver fluke disease

Hepatic distomiasis due to Clonorchis sinensis

Oriental liver fluke disease

121.2    Paragonimiasis

Infection by Paragonimus

Lung fluke disease (oriental)

Pulmonary distomiasis

121.3    Fascioliasis

Infection by Fasciola:

gigantica

hepatica

Liver flukes NOS

Sheep liver fluke infection

121.4    Fasciolopsiasis

Infection by Fasciolopsis (buski)

Intestinal distomiasis

121.5    Metagonimiasis

Infection by Metagonimus yokogawai

121.6    Heterophyiasis

Infection by:

Heterophyes heterophyes

Stellantchasmus falcatus

121.8    Other specified trematode infections

Infection by:

Dicrocoelium dendriticum

Echinostoma ilocanum

Gastrodiscoides hominis

121.9    Trematode infection, unspecified

Distomiasis NOS

Fluke disease NOS

122       Echinococcosis

Includes:           echinococciasis

hydatid disease

hydatidosis

122.0    Echinococcus granulosus infection of liver

122.1    Echinococcus granulosus infection of lung

122.2    Echinococcus granulosus infection of thyroid

122.3    Echinococcus granulosus infection, other

122.4    Echinococcus granulosus infection, unspecified

122.5    Echinococcus multilocularis infection of liver

122.6    Echinococcus multilocularis infection, other

122.7    Echinococcus multilocularis infection, unspecified

122.8    Echinococcosis, unspecified, of liver

122.9    Echinococcosis, other and unspecified

123       Other cestode infection

123.0    Taenia solium infection, intestinal form

Pork tapeworm (adult) (infection)

123.1    Cysticercosis

Cysticerciasis

Infection by Cysticercus cellulosae [larval form of Taenia solium]

123.2    Taenia saginata infection

Beef tapeworm (infection)

Infection by Taeniarhynchus saginatus

123.3    Taeniasis, unspecified

123.4    Diphyllobothriasis, intestinal

Diphyllobothrium (adult) (latum) (pacificum) infection

Fish tapeworm (infection)

123.5    Sparganosis [larval diphyllobothriasis]

Infection by:

Diphyllobothrium larvae

Sparganum (mansoni) (proliferum)

Spirometra larvae

123.6    Hymenolepiasis

Dwarf tapeworm (infection)

Hymenolepis (diminuta) (nana) infection

Rat tapeworm (infection)

123.8    Other specified cestode infection

Diplogonoporus (grandis) infection

Dipylidium (caninum) infection

Dog tapeworm (infection)

123.9    Cestode infection, unspecified

Tapeworm (infection) NOS

124       Trichinosis

Trichinella spiralis infection

Trichinellosis

Trichiniasis

125       Filarial infection and dracontiasis

125.0    Bancroftian filariasis

Chyluria due to Wuchereria bancrofti

Elephantiasis due to Wuchereria bancrofti

Infection due to Wuchereria bancrofti

Lymphadenitis due to Wuchereria bancrofti

Lymphangitis due to Wuchereria bancrofti

Wuchereriasis

125.1    Malayan filariasis

Brugia filariasis due to Brugia [Wuchereria] malayi

Chyluria due to Brugia [Wuchereria] malayi

Elephantiasis due to Brugia [Wuchereria] malayi

Infection due to Brugia [Wuchereria] malayi

Lymphadenitis due to Brugia [Wuchereria] malayi

Lymphangitis due to Brugia [Wuchereria] malayi

125.2    Loiasis

Eyeworm disease of Africa

Loa loa infection

125.3    Onchocerciasis

Onchocerca volvulus infection

Onchocercosis

125.4    Dipetalonemiasis

Infection by:

Acanthocheilonema perstans

Dipetalonema perstans

125.5    Mansonella ozzardi infection

Filariasis ozzardi

125.6    Other specified filariasis

Dirofilaria infection

Infection by:

Acanthocheilonema streptocerca

Dipetalonema streptocerca

125.7    Dracontiasis

Guinea-worm infection

Infection by Dracunculus medinensis

125.9    Unspecified filariasis

126       Ancylostomiasis and necatoriasis

Includes:           cutaneous larva migrans due to Ancylostoma

hookworm (disease) (infection)

uncinariasis

126.0    Ancylostoma duodenale

126.1    Necator americanus

126.2    Ancylostoma braziliense

126.3    Ancylostoma ceylanicum

126.8    Other specified Ancylostoma

126.9    Ancylostomiasis and necatoriasis, unspecified

Creeping eruption NOS

Cutaneous larva migrans NOS

127       Other intestinal helminthiases

127.0    Ascariasis

Ascaridiasis

Infection by Ascaris lumbricoides

Roundworm infection

127.1    Anisakiasis

Infection by Anisakis larva

127.2    Strongyloidiasis

Infection by Strongyloides stercoralis

Excludes:          trichostrongyliasis (127.6)

127.3    Trichuriasis

Infection by Trichuris trichiuria

Trichocephaliasis

Whipworm (disease) (infection)

127.4    Enterobiasis

Infection by Enterobius vermicularis

Oxyuriasis

Oxyuris vermicularis infection

Pinworm (disease) (infection)

Threadworm infection

127.5    Capillariasis

Infection by Capillaria philippinensis

Excludes:          infection by Capillaria hepatica (128.8)

127.6    Trichostrongyliasis

Infection by Trichostrongylus species

127.7    Other specified intestinal helminthiasis

Infection by:

Oesophagostomum apiostomum and related species

Ternidens diminutus

other specified intestinal helminth

Physalopteriasis

127.8    Mixed intestinal helminthiasis

Infection by intestinal helminths classified to more than one of the categories 120.0-127.7

Mixed helminthiasis NOS

127.9    Intestinal helminthiasis, unspecified

128       Other and unspecified helminthiases

128.0    Toxocariasis

Larva migrans visceralis

Toxocara (canis) (cati) infection

Visceral larva migrans syndrome

128.1    Gnathostomiasis

Infection by Gnathostoma spinigerum and related species

128.8    Other specified helminthiasis

Infection by:

Angiostrongylus cantonensis

Capillaria hepatica

other specified helminth

128.9    Helminth infection, unspecified

Helminthiasis NOS

Worms NOS

129       Intestinal parasitism, unspecified

OTHER INFECTIOUS AND PARASITIC DISEASES (130-136)

130       Toxoplasmosis

Includes:           infection by toxoplasma gondii

toxoplasmosis (acquired)

Excludes:          congenital toxoplasmosis (771.2)

130.0    Meningoencephalitis due to toxoplasmosis

Encephalitis due to acquired toxoplasmosis

130.1    Conjunctivitis due to toxoplasmosis

130.2    Chorioretinitis due to toxoplasmosis

Focal retinochoroiditis due to acquired toxoplasmosis

130.3    Myocarditis due to toxoplasmosis

130.4    Pneumonitis due to toxoplasmosis

130.5    Hepatitis due to toxoplasmosis

130.7    Toxoplasmosis of other specified sites

130.8    Multisystemic disseminated toxoplasmosis

Toxoplasmosis of multiple sites

130.9    Toxoplasmosis, unspecified

131       Trichomoniasis

Includes:           infection due to Trichomonas (vaginalis)

131.0    Urogenital trichomoniasis

131.00  Urogenital trichomoniasis, unspecified

Fluor (vaginalis) trichomonal or due to Trichomonas (vaginalis)

Leukorrhea (vaginalis) trichomonal or due to Trichomonas (vaginalis)

131.01  Trichomonal vulvovaginitis

Vaginitis, trichomonal or due to Trichomonas (vaginalis)

131.02  Trichomonal urethritis

131.03  Trichomonal prostatitis

131.09  Other

131.8    Other specified sites

Excludes:          intestinal (007.3)

131.9    Trichomoniasis, unspecified

132       Pediculosis and phthirus infestation

132.0    Pediculus capitis [head louse]

132.1    Pediculus corporis [body louse]

132.2    Phthirus pubis [pubic louse]

Pediculus pubis

132.3    Mixed infestation

Infestation classifiable to more than one of the categories 132.0-132.2

132.9    Pediculosis, unspecified

133       Acariasis

133.0    Scabies

Infestation by Sarcoptes scabiei

Norwegian scabies

Sarcoptic itch

133.8    Other acariasis

Chiggers

Infestation by:

Demodex folliculorum

Trombicula

133.9    Acariasis, unspecified

Infestation by mites NOS

134       Other infestation

134.0    Myiasis

Infestation by:

Dermatobia (hominis)

fly larvae

Gasterophilus (intestinalis)

maggots

Oestrus ovis

134.1    Other arthropod infestation

Infestation by:

chigoe

sand flea

Tunga penetrans

Jigger disease

Scarabiasis

Tungiasis

134.2    Hirudiniasis

Hirudiniasis (external) (internal)

Leeches (aquatic) (land)

134.8    Other specified infestations

134.9    Infestation, unspecified

Infestation (skin) NOS

Skin parasites NOS

135       Sarcoidosis

Besnier-Boeck-Schaumann disease

Lupoid (miliary) of Boeck

Lupus pernio (Besnier)

Lymphogranulomatosis, benign (Schaumann's)

Sarcoid (any site):

NOS

Boeck

Darier-Roussy

Uveoparotid fever

136       Other and unspecified infectious and parasitic diseases

136.0    Ainhum

Dactylolysis spontanea

136.1    Behçet's syndrome

136.2    Specific infections by free-living amebae

Meningoencephalitis due to Naegleria

136.3    Pneumocystosis

Pneumonia due to Pneumocystis carinii

136.4    Psorospermiasis

136.5    Sarcosporidiosis

Infection by Sarcocystis lindemanni

136.8    Other specified infectious and parasitic diseases

Candiru infestation

136.9    Unspecified infectious and parasitic diseases

Infectious disease NOS

Parasitic disease NOS

LATE EFFECTS OF INFECTIOUS AND PARASITIC DISEASES (137-139)

137       Late effects of tuberculosis

Note:    This category is to be used to indicate conditions classifiable to 010-018 as the cause of late effects, which are themselves classified elsewhere. The "late effects" include those specified as such, as sequelae, or as due to old or inactive tuberculosis, without evidence of active disease.

137.0    Late effects of respiratory or unspecified tuberculosis

137.1    Late effects of central nervous system tuberculosis

137.2    Late effects of genitourinary tuberculosis

137.3    Late effects of tuberculosis of bones and joints

137.4    Late effects of tuberculosis of other specified organs

138       Late effects of acute poliomyelitis

Note:    This category is to be used to indicate conditions classifiable to 045 as the cause of late effects, which are themselves classified elsewhere.  The "late effects" include conditions specified as such, or as sequelae, or as due to old or inactive poliomyelitis, without evidence of active disease.

139       Late effects of other infectious and parasitic diseases

Note:    This category is to be used to indicate conditions classifiable to categories 001-009, 020-041, 046-136 as the cause of late effects, which are themselves classified elsewhere.  The "late effects" include conditions specified as such; they also include sequela of diseases classifiable to the above categories if there is evidence that the disease itself is no longer present.

139.0    Late effects of viral encephalitis

Late effects of conditions classifiable to 049.8-049.9, 062-064

139.1    Late effects of trachoma

Late effects of conditions classifiable to 076

139.8    Late effects of other and unspecified infectious and parasitic diseases

2. NEOPLASMS (140-239) back to top

1.             Content:

This chapter contains the following broad groups:

140-195       Malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphatic and hematopoietic tissue

196-198       Malignant neoplasms, stated or presumed to be secondary, of specified sites

199             Malignant neoplasms, without specification of site

200-208       Malignant neoplasms, stated or presumed to be primary, of lymphatic and hematopoietic tissue

210-229       Benign neoplasms

230-234       Carcinoma in situ

235-238       Neoplasms of uncertain behavior [see Note, at beginning of section 235-238]

239             Neoplasms of unspecified nature

2.             Functional activity

All neoplasms are classified in this chapter, whether or not functionally active. An additional code from Chapter 3 may be used to identify such functional activity associated with any neoplasm, e.g.:

catecholamine-producing malignant pheochromocytoma of adrenal:

            code 194.0, additional code 255.6

basophil adenoma of pituitary with Cushing's syndrome:

            code 227.3, additional code 255.0

3.             Morphology [Histology]

For those wishing to identify the histological type of neoplasms, a comprehensive coded nomenclature, which comprises the morphology rubrics of the ICD-Oncology, is given after the E-code chapter.

4.             Malignant neoplasms overlapping site boundaries

Categories 140-195 are for the classification of primary malignant neoplasms according to their point of origin.  A malignant neoplasm that overlaps two or more subcategories within a three-digit rubric and whose point of origin cannot be determined should be classified to the subcategory .8 "Other."  For example, "carcinoma involving tip and ventral surface of tongue" should be assigned to 141.8. On the other hand, "carcinoma of tip of tongue, extending to involve the ventral surface" should be coded to 141.2, as the point of origin, the tip, is known.  Three subcategories (149.8, 159.8, 165.8) have been provided for malignant neoplasms that overlap the boundaries of three-digit rubrics within certain systems.  Overlapping malignant neoplasms that cannot be classified as indicated above should be assigned to the appropriate subdivision of category 195 (Malignant neoplasm of other and ill-defined sites).

MALIGNANT NEOPLASM OF LIP, ORAL CAVITY, AND PHARYNX (140-149)

Excludes:         carcinoma in situ (230.0)

140       Malignant neoplasm of lip

Excludes:          skin of lip (173.0)

140.0    Upper lip, vermilion border

Upper lip:

NOS

external

lipstick area

140.1    Lower lip, vermilion border

Lower lip:

NOS

external

lipstick area

140.3    Upper lip, inner aspect

Upper lip:

buccal aspect

frenulum

mucosa

oral aspect

140.4    Lower lip, inner aspect

Lower lip:

buccal aspect

frenulum

mucosa

oral aspect

140.5    Lip, unspecified, inner aspect

Lip, not specified whether upper or lower:

buccal aspect

frenulum

mucosa

oral aspect

140.6    Commissure of lip

Labial commissure

140.8    Other sites of lip

Malignant neoplasm of contiguous or overlapping sites of lip whose point of origin cannot be determined

140.9    Lip, unspecified, vermilion border

Lip, not specified as upper or lower:

NOS

external

lipstick area

141       Malignant neoplasm of tongue

141.0    Base of tongue

Dorsal surface of base of tongue

Fixed part of tongue NOS

141.1    Dorsal surface of tongue

Anterior two-thirds of tongue, dorsal surface

Dorsal tongue NOS

Midline of tongue

Excludes:          dorsal surface of base of tongue (141.0)

141.2    Tip and lateral border of tongue

141.3    Ventral surface of tongue

Anterior two-thirds of tongue, ventral surface

Frenulum linguae

141.4    Anterior two-thirds of tongue, part unspecified

Mobile part of tongue NOS

141.5    Junctional zone

Border of tongue at junction of fixed and mobile parts at insertion of anterior tonsillar pillar

141.6    Lingual tonsil

141.8    Other sites of tongue

Malignant neoplasm of contiguous or overlapping sites of tongue whose point of origin cannot be determined

141.9    Tongue, unspecified

Tongue NOS

142       Malignant neoplasm of major salivary glands

Includes:           salivary ducts

Excludes:          malignant neoplasm of minor salivary glands:

NOS (145.9)

buccal mucosa (145.0)

soft palate (145.3)

tongue (141.0-141.9)

tonsil, palatine (146.0)

142.0    Parotid gland

142.1    Submandibular gland

Submaxillary gland

142.2    Sublingual gland

142.8    Other major salivary glands

Malignant neoplasm of contiguous or overlapping sites of salivary glands and ducts whose point of origin cannot be determined

142.9    Salivary gland, unspecified

Salivary gland (major) NOS

143       Malignant neoplasm of gum

Includes:           alveolar (ridge) mucosa

gingiva (alveolar) (marginal)

interdental papillae

Excludes:          malignant odontogenic neoplasms (170.0-170.1)

143.0    Upper gum

143.1    Lower gum

143.8    Other sites of gum

Malignant neoplasm of contiguous or overlapping sites of gum whose point of origin cannot be determined

143.9    Gum, unspecified

144       Malignant neoplasm of floor of mouth

144.0    Anterior portion

Anterior to the premolar-canine junction

144.1    Lateral portion

144.8    Other sites of floor of mouth

Malignant neoplasm of contiguous or overlapping sites of floor of mouth whose point of origin cannot be determined

144.9    Floor of mouth, part unspecified

145       Malignant neoplasm of other and unspecified parts of mouth

Excludes:          mucosa of lips (140.0-140.9)

145.0    Cheek mucosa

Buccal mucosa

Cheek, inner aspect

145.1    Vestibule of mouth

Buccal sulcus (upper) (lower)

Labial sulcus (upper) (lower)

145.2    Hard palate

145.3    Soft palate

Excludes:          nasopharyngeal [posterior] [superior] surface of soft palate (147.3)

145.4    Uvula

145.5    Palate, unspecified

Junction of hard and soft palate

Roof of mouth

145.6    Retromolar area

145.8    Other specified parts of mouth

Malignant neoplasm of contiguous or overlapping sites of mouth whose point of origin cannot be determined

145.9    Mouth, unspecified

Buccal cavity NOS

Minor salivary gland, unspecified site

Oral cavity NOS

146       Malignant neoplasm of oropharynx

146.0    Tonsil

Tonsil:

NOS

faucial

palatine

Excludes:          lingual tonsil (141.6)

pharyngeal tonsil (147.1)

146.1    Tonsillar fossa

146.2    Tonsillar pillars (anterior) (posterior)

Faucial pillar

Glossopalatine fold

Palatoglossal arch

Palatopharyngeal arch

146.3    Vallecula

Anterior and medial surface of the pharyngoepiglottic fold

146.4    Anterior aspect of epiglottis

Epiglottis, free border [margin]

Glossoepiglottic fold(s)

Excludes:          epiglottis:

NOS (161.1)

suprahyoid portion (161.1)

146.5    Junctional region

Junction of the free margin of the epiglottis, the aryepiglottic fold, and the pharyngoepiglottic fold

146.6    Lateral wall of oropharynx

146.7    Posterior wall of oropharynx

146.8    Other specified sites of oropharynx

Branchial cleft

Malignant neoplasm of contiguous or overlapping sites of oropharynx whose point of origin cannot be determined

146.9    Oropharynx, unspecified

147       Malignant neoplasm of nasopharynx

147.0    Superior wall

Roof of nasopharynx

147.1    Posterior wall

Adenoid

Pharyngeal tonsil

147.2    Lateral wall

Fossa of Rosenmüller

Opening of auditory tube

Pharyngeal recess

147.3    Anterior wall

Floor of nasopharynx

Nasopharyngeal [posterior] [superior] surface of soft palate

Posterior margin of nasal septum and choanae

147.8    Other specified sites of nasopharynx

Malignant neoplasm of contiguous or overlapping sites of nasopharynx whose point of origin cannot be determined

147.9    Nasopharynx, unspecified

Nasopharyngeal wall NOS

148       Malignant neoplasm of hypopharynx

148.0    Postcricoid region

148.1    Pyriform sinus

Pyriform fossa

148.2    Aryepiglottic fold, hypopharyngeal aspect

Aryepiglottic fold or interarytenoid fold:

NOS

marginal zone

Excludes:          aryepiglottic fold or interarytenoid fold, laryngeal aspect (161.1)

148.3    Posterior hypopharyngeal wall

148.8    Other specified sites of hypopharynx

Malignant neoplasm of contiguous or overlapping sites of hypopharynx whose point of origin cannot be determined

148.9    Hypopharynx, unspecified

Hypopharyngeal wall NOS

Hypopharynx NOS

149       Malignant neoplasm of other and ill-defined sites within the lip, oral cavity, and pharynx

149.0    Pharynx, unspecified

149.1    Waldeyer's ring

149.8    Other

Malignant neoplasms of lip, oral cavity, and pharynx whose point of origin cannot be assigned to any one of the categories 140-148

Excludes:          "book leaf" neoplasm [ventral surface of tongue and floor of mouth] (145.8)

149.9    Ill-defined

MALIGNANT NEOPLASM OF DIGESTIVE ORGANS AND PERITONEUM (150-159)

Excludes:         carcinoma in situ (230.1-230.9)

150       Malignant neoplasm of esophagus

150.0    Cervical esophagus

150.1    Thoracic esophagus

150.2    Abdominal esophagus

Excludes:          adenocarcinoma (151.0)

cardio-esophageal junction (151.0)

150.3    Upper third of esophagus

Proximal third of esophagus

150.4    Middle third of esophagus

150.5    Lower third of esophagus

Distal third of esophagus

Excludes:          adenocarcinoma (151.0)

cardio-esophageal junction (151.0)

150.8    Other specified part

Malignant neoplasm of contiguous or overlapping sites of esophagus whose point of origin cannot be determined

150.9    Esophagus, unspecified

151       Malignant neoplasm of stomach

151.0    Cardia

Cardiac orifice

Cardio-esophageal junction

Excludes:          squamous cell carcinoma (150.2, 150.5)

151.1    Pylorus

Prepylorus

Pyloric canal

151.2    Pyloric antrum

Antrum of stomach NOS

151.3    Fundus of stomach

151.4    Body of stomach

151.5    Lesser curvature, unspecified

Lesser curvature, not classifiable to 151.1-151.4

151.6    Greater curvature, unspecified

Greater curvature, not classifiable to 151.0-151.4

151.8    Other specified sites of stomach

Anterior wall, not classifiable to 151.0-151.4

Posterior wall, not classifiable to 151.0-151.4

Malignant neoplasm of contiguous or overlapping sites of stomach whose point of origin cannot be determined

151.9    Stomach, unspecified

Carcinoma ventriculi

Gastric cancer

152       Malignant neoplasm of small intestine, including duodenum

152.0    Duodenum

152.1    Jejunum

152.2    Ileum

Excludes:          ileocecal valve (153.4)

152.3    Meckel's diverticulum

152.8    Other specified sites of small intestine

Duodenojejunal junction

Malignant neoplasm of contiguous or overlapping sites of small intestine whose point of origin cannot be determined

152.9    Small intestine, unspecified

153       Malignant neoplasm of colon

153.0    Hepatic flexure

153.1    Transverse colon

153.2    Descending colon

Left colon

153.3    Sigmoid colon

Sigmoid (flexure)

Excludes:          rectosigmoid junction (154.0)

153.4    Cecum

Ileocecal valve

153.5    Appendix

153.6    Ascending colon

Right colon

153.7    Splenic flexure

153.8    Other specified sites of large intestine

Malignant neoplasm of contiguous or overlapping sites of colon whose point of origin cannot be determined

Excludes:          ileocecal valve (153.4)

rectosigmoid junction (154.0)

153.9    Colon, unspecified

Large intestine NOS

154       Malignant neoplasm of rectum, rectosigmoid junction, and anus

154.0    Rectosigmoid junction

Colon with rectum

Rectosigmoid (colon)

154.1    Rectum

Rectal ampulla

154.2    Anal canal

Anal sphincter

Excludes:          skin of anus (172.5, 173.5)

154.3    Anus, unspecified

Excludes:          anus:

margin (172.5, 173.5)

skin (172.5, 173.5)

perianal skin (172.5, 173.5)

154.8    Other

Anorectum

Cloacogenic zone

Malignant neoplasm of contiguous or overlapping sites of rectum, rectosigmoid junction, and anus whose point of origin cannot be determined

155       Malignant neoplasm of liver and intrahepatic bile ducts

155.0    Liver, primary

Carcinoma:

liver, specified as primary

hepatocellular

liver cell

Hepatoblastoma

155.1    Intrahepatic bile ducts

Canaliculi biliferi

Interlobular:

bile ducts

biliary canals

Intrahepatic:

biliary passages

canaliculi

gall duct

Excludes:          hepatic duct (156.1)

155.2    Liver, not specified as primary or secondary

156       Malignant neoplasm of gallbladder and extrahepatic bile ducts

156.0    Gallbladder

156.1    Extrahepatic bile ducts

Biliary duct or passage

NOS

Common bile duct

Cystic duct

Hepatic duct

Sphincter of Oddi

156.2    Ampulla of Vater

156.8    Other specified sites of gallbladder and extrahepatic bile ducts

Malignant neoplasm of contiguous or overlapping sites of gallbladder and extrahepatic bile ducts whose point of origin cannot be determined

156.9    Biliary tract, part unspecified

Malignant neoplasm involving both intrahepatic and extrahepatic bile ducts

157       Malignant neoplasm of pancreas

157.0    Head of pancreas

157.1    Body of pancreas

157.2    Tail of pancreas

157.3    Pancreatic duct

Duct of:

Santorini

Wirsung

157.4    Islets of Langerhans

Islets of Langerhans, any part of pancreas

Use additional code to identify any functional activity

157.8    Other specified sites of pancreas

Ectopic pancreatic tissue

Malignant neoplasm of contiguous or overlapping sites of pancreas whose point of origin cannot be determined

157.9    Pancreas, part unspecified

158       Malignant neoplasm of retroperitoneum and peritoneum

158.0    Retroperitoneum

Periadrenal tissue

Perinephric tissue

Perirenal tissue

Retrocecal tissue

158.8    Specified parts of peritoneum

Cul-de-sac (of Douglas)

Mesentery

Mesocolon

Omentum

Peritoneum:

parietal

pelvic

Rectouterine pouch

Malignant neoplasm of contiguous or overlapping sites of retroperitoneum and peritoneum whose point of origin cannot be determined

158.9    Peritoneum, unspecified

159       Malignant neoplasm of other and ill-defined sites within the digestive organs and peritoneum

159.0    Intestinal tract, part unspecified

Intestine NOS

159.1    Spleen, not elsewhere classified

Angiosarcoma of spleen

Fibrosarcoma of spleen

Excludes:          Hodgkin's disease (201.0-201.9)

lymphosarcoma (200.1)

reticulosarcoma (200.0)

159.8    Other sites of digestive system and intra-abdominal organs

Malignant neoplasm of digestive organs and peritoneum whose point of origin cannot be assigned to any one of the categories 150-158

Excludes:          anus and rectum (154.8)

cardio-esophageal junction (151.0)

colon and rectum (154.0)

159.9    Ill-defined

Alimentary canal or tract NOS

Gastrointestinal tract NOS

Excludes:          abdominal NOS (195.2)

intra-abdominal NOS (195.2)

MALIGNANT NEOPLASM OF RESPIRATORY AND INTRATHORACIC ORGANS (160-165)

Excludes:         carcinoma in situ (231.0-231.9)

160       Malignant neoplasm of nasal cavities, middle ear, and accessory sinuses

160.0    Nasal cavities

Cartilage of nose

Conchae, nasal

Internal nose

Septum of nose

Vestibule of nose

Excludes:          nasal bone (170.0)

nose NOS (195.0)

olfactory bulb (192.0)

posterior margin of septum and choanae (147.3)

skin of nose (172.3, 173.3)

turbinates (170.0)

160.1    Auditory tube, middle ear, and mastoid air cells

Antrum tympanicum

Eustachian tube

Tympanic cavity

Excludes:          auditory canal (external) (172.2, 173.2)

bone of ear (meatus) (170.0)

cartilage of ear (171.0)

ear (external) (skin) (172.2, 173.2)

160.2    Maxillary sinus

Antrum (Highmore) (maxillary)

160.3    Ethmoidal sinus

160.4    Frontal sinus

160.5    Sphenoidal sinus

160.8    Other

Malignant neoplasm of contiguous or overlapping sites of nasal cavities, middle ear, and accessory sinuses whose point of origin cannot be determined

160.9    Accessory sinus, unspecified

161       Malignant neoplasm of larynx

161.0    Glottis

Intrinsic larynx

Laryngeal commissure (anterior) (posterior)

True vocal cord

Vocal cord NOS

161.1    Supraglottis

Aryepiglottic fold or interarytenoid fold, laryngeal aspect

Epiglottis (suprahyoid portion) NOS

Extrinsic larynx

False vocal cords

Posterior (laryngeal) surface of epiglottis

Ventricular bands

Excludes:          anterior aspect of epiglottis (146.4)

aryepiglottic fold or interarytenoid fold:

NOS (148.2)

hypopharyngeal aspect (148.2)

marginal zone (148.2)

161.2    Subglottis

161.3    Laryngeal cartilages

Cartilage:

arytenoid

cricoid

cuneiform

thyroid

161.8    Other specified sites of larynx

Malignant neoplasm of contiguous or overlapping sites of larynx whose point of origin cannot be determined

161.9    Larynx, unspecified

162       Malignant neoplasm of trachea, bronchus, and lung

162.0    Trachea

Cartilage of trachea

Mucosa of trachea

162.2    Main bronchus

Carina

Hilus of lung

162.3    Upper lobe, bronchus or lung

162.4    Middle lobe, bronchus or lung

162.5    Lower lobe, bronchus or lung

162.8    Other parts of bronchus or lung

Malignant neoplasm of contiguous or overlapping sites of bronchus or lung whose point of origin cannot be determined

162.9    Bronchus and lung, unspecified

163       Malignant neoplasm of pleura

163.0    Parietal pleura

163.1    Visceral pleura

163.8    Other specified sites of pleura

Malignant neoplasm of contiguous or overlapping sites of pleura whose point of origin cannot be determined

163.9    Pleura, unspecified

164       Malignant neoplasm of thymus, heart, and mediastinum

164.0    Thymus

164.1    Heart

Endocardium

Epicardium

Myocardium

Pericardium

Excludes:          great vessels (171.4)

164.2    Anterior mediastinum

164.3    Posterior mediastinum

164.8    Other

Malignant neoplasm of contiguous or overlapping sites of thymus, heart, and mediastinum whose point of origin cannot be determined

164.9    Mediastinum, part unspecified

165       Malignant neoplasm of other and ill-defined sites within the respiratory system and intrathoracic organs

165.0    Upper respiratory tract, part unspecified

165.8    Other

Malignant neoplasm of respiratory and intrathoracic organs whose point of origin cannot be assigned to any one of the categories 160-164

165.9    Ill-defined sites within the respiratory system

Respiratory tract NOS

Excludes:          intrathoracic NOS (195.1)

thoracic NOS (195.1)

MALIGNANT NEOPLASM OF BONE, CONNECTIVE TISSUE, SKIN, AND BREAST (170-176)

Excludes:         carcinoma in situ:

breast (233.0)

skin (232.0-232.9)

170       Malignant neoplasm of bone and articular cartilage

Includes:           cartilage (articular) (joint)

periosteum

Excludes:          bone marrow NOS (202.9)

cartilage:

ear (171.0)

eyelid (171.0)

larynx (161.3)

nose (160.0)

synovia (171.0-171.9)

170.0    Bones of skull and face, except mandible

Bone:

ethmoid

frontal

malar

nasal

occipital

orbital

parietal

sphenoid

temporal

zygomatic

Maxilla (superior)

Turbinate

Upper jaw bone

Vomer

Excludes:          carcinoma, any type except intraosseous or odontogenic:

maxilla, maxillary (sinus) (160.2)

upper jaw bone (143.0)

jaw bone (lower) (170.1)

170.1    Mandible

Inferior maxilla

Jaw bone NOS

Lower jaw bone

Excludes:          carcinoma, any type except intraosseous or odontogenic:

jaw bone NOS (143.9)

lower (143.1)

upper jaw bone (170.0)

170.2    Vertebral column, excluding sacrum and coccyx

Spinal column

Spine

Vertebra

Excludes:          sacrum and coccyx (170.6)

170.3    Ribs, sternum, and clavicle

Costal cartilage

Costovertebral joint

Xiphoid process

170.4    Scapula and long bones of upper limb

Acromion

Bones NOS of upper limb

Humerus

Radius

Ulna

170.5    Short bones of upper limb

Carpal

Cuneiform, wrist

Metacarpal

Navicular, of hand

Phalanges of hand

Pisiform

Scaphoid (of hand)

Semilunar or lunate

Trapezium

Trapezoid

Unciform

170.6    Pelvic bones, sacrum, and coccyx

Coccygeal vertebra

Ilium

Ischium

Pubic bone

Sacral vertebra

170.7    Long bones of lower limb

Bones NOS of lower limb

Femur

Fibula

Tibia

170.8    Short bones of lower limb

Astragalus [talus]

Calcaneus

Cuboid

Cuneiform, ankle

Metatarsal

Navicular (of ankle)

Patella

Phalanges of foot

Tarsal

170.9    Bone and articular cartilage, site unspecified

171       Malignant neoplasm of connective and other soft tissue

Includes:           blood vessel

bursa

fascia

fat

ligament, except uterine

muscle

peripheral, sympathetic, and parasympathetic nerves and ganglia

synovia

tendon (sheath)

Excludes:          cartilage (of):

articular (170.0-170.9)

larynx (161.3)

nose (160.0)

connective tissue:

breast (174.0-175.9)

internal organs­code to malignant neoplasm of the site [e.g., leiomyosarcoma of stomach, 151.9]

heart (164.1)

uterine ligament (183.4)

171.0    Head, face, and neck

Cartilage of:

ear

eyelid

171.2    Upper limb, including shoulder

Arm

Finger

Forearm

Hand

171.3    Lower limb, including hip

Foot

Leg

Popliteal space

Thigh

Toe

171.4    Thorax

Axilla

Diaphragm

Great vessels

Excludes:          heart (164.1)

mediastinum (164.2-164.9)

thymus (164.0)

171.5    Abdomen

Abdominal wall

Hypochondrium

Excludes:          peritoneum (158.8)

retroperitoneum (158.0)

171.6    Pelvis

Buttock

Groin

Inguinal region

Perineum

Excludes:          pelvic peritoneum (158.8)

retroperitoneum (158.0)

uterine ligament, any (183.3-183.5)

171.7    Trunk, unspecified

Back NOS

Flank NOS

171.8    Other specified sites of connective and other soft tissue

Malignant neoplasm of contiguous or overlapping sites of connective tissue whose point of origin cannot be determined

171.9    Connective and other soft tissue, site unspecified

172       Malignant melanoma of skin

Includes:           melanocarcinoma

melanoma (skin) NOS

Excludes:          skin of genital organs (184.0-184.9, 187.1-187.9)

sites other than skin­code to malignant neoplasm of the site

172.0    Lip

Excludes:          vermilion border of lip (140.0-140.1, 140.9)

172.1    Eyelid, including canthus

172.2    Ear and external auditory canal

Auricle (ear)

Auricular canal, external

External [acoustic] meatus

Pinna

172.3    Other and unspecified parts of face

Cheek (external)

Chin

Eyebrow

Forehead

Nose, external

Temple

172.4    Scalp and neck

172.5    Trunk, except scrotum

Axilla

Breast

Buttock

Groin

Perianal skin

Perineum

Umbilicus

Excludes:          anal canal (154.2)

anus NOS (154.3)

scrotum (187.7)

172.6    Upper limb, including shoulder

Arm

Finger

Forearm

Hand

172.7    Lower limb, including hip

Ankle

Foot

Heel

Knee

Leg

Popliteal area

Thigh

Toe

172.8    Other specified sites of skin

Malignant melanoma of contiguous or overlapping sites of skin whose point of origin cannot be determined

172.9    Melanoma of skin, site unspecified

173       Other malignant neoplasm of skin

Includes:           malignant neoplasm of:

sebaceous glands

sudoriferous, sudoriparous glands

sweat glands

Excludes:          Kaposi's sarcoma (176.0-176.9)

malignant melanoma of skin (172.0-172.9)

skin of genital organs (184.0-184.9, 187.1-187.9)

173.0    Skin of lip

Excludes:          vermilion border of lip (140.0-140.1, 140.9)

173.1    Eyelid, including canthus

Excludes:          cartilage of eyelid (171.0)

173.2    Skin of ear and external auditory canal

Auricle (ear)

Auricular canal, external

External meatus

Pinna

Excludes:          cartilage of ear (171.0)

173.3    Skin of other and unspecified parts of face

Cheek, external

Chin

Eyebrow

Forehead

Nose, external

Temple

173.4    Scalp and skin of neck

173.5    Skin of trunk, except scrotum

Axillary fold

Perianal skin

Skin of:

abdominal wall

anus

back

breast

buttock

chest wall

groin

perineum

Umbilicus

Excludes:          anal canal (154.2)

anus NOS (154.3)

skin of scrotum (187.7)

173.6    Skin of upper limb, including shoulder

Arm

Finger

Forearm

Hand

173.7    Skin of lower limb, including hip

Ankle

Foot

Heel

Knee

Leg

Popliteal area

Thigh

Toe

173.8    Other specified sites of skin

Malignant neoplasm of contiguous or overlapping sites of skin whose point of origin cannot be determined

173.9    Skin, site unspecified

174       Malignant neoplasm of female breast

Includes:           breast (female)

connective tissue

soft parts

Paget's disease of:

breast

nipple

Excludes:          skin of breast (172.5, 173.5)

174.0    Nipple and areola

174.1    Central portion

174.2    Upper-inner quadrant

174.3    Lower-inner quadrant

174.4    Upper-outer quadrant

174.5    Lower-outer quadrant

174.6    Axillary tail

174.8    Other specified sites of female breast

Ectopic sites

Inner breast

Lower breast

Midline of breast

Outer breast

Upper breast

Malignant neoplasm of contiguous or overlapping sites of breast whose point of origin cannot be determined

174.9    Breast (female), unspecified

175       Malignant neoplasm of male breast

Excludes:          skin of breast (172.5, 173.5)

175.0    Nipple and areola

175.9    Other and unspecified sites of male breast

Ectopic breast tissue, male

176       Kaposi's sarcoma

176.0    Skin

176.1    Soft tissue

Blood vessel

Connective tissue

Fascia

Ligament

Lymphatic(s) NEC

Muscle

Excludes:          lymph glands and nodes (176.5)

176.2    Palate

176.3    Gastrointestinal sites

176.4    Lung

176.5    Lymph nodes

176.8    Other specified sites

Oral cavity NEC

176.9    Unspecified

Viscera NOS

MALIGNANT NEOPLASM OF GENITOURINARY ORGANS (179-189)

Excludes:         carcinoma in situ (233.1-233.9)

179       Malignant neoplasm of uterus, part unspecified

180       Malignant neoplasm of cervix uteri

Includes:           invasive malignancy [carcinoma]

Excludes:          carcinoma in situ (233.1)

180.0    Endocervix

Cervical canal NOS

Endocervical canal

Endocervical gland

180.1    Exocervix

180.8    Other specified sites of cervix

Cervical stump

Squamocolumnar junction of cervix

Malignant neoplasm of contiguous or overlapping sites of cervix uteri whose point of origin cannot be determined

180.9    Cervix uteri, unspecified

181       Malignant neoplasm of placenta

Choriocarcinoma NOS

Chorioepithelioma NOS

Excludes:          chorioadenoma (destruens) (236.1)

hydatidiform mole (630)

malignant (236.1)

invasive mole (236.1)

male choriocarcinoma NOS (186.0-186.9)

182       Malignant neoplasm of body of uterus

Excludes:          carcinoma in situ (233.2)

182.0    Corpus uteri, except isthmus

Cornu

Endometrium

Fundus

Myometrium

182.1    Isthmus

Lower uterine segment

182.8    Other specified sites of body of uterus

Malignant neoplasm of contiguous or overlapping sites of body of uterus whose point of origin cannot be determined

Excludes:          uterus NOS (179)

183       Malignant neoplasm of ovary and other uterine adnexa

Excludes:          Douglas' cul-de-sac (158.8)

183.0    Ovary

Use additional code to identify any functional activity

183.2    Fallopian tube

Oviduct

Uterine tube

183.3    Broad ligament

Mesovarium

Parovarian region

183.4    Parametrium

Uterine ligament NOS

Uterosacral ligament

183.5    Round ligament

183.8    Other specified sites of uterine adnexa

Tubo-ovarian

Utero-ovarian

Malignant neoplasm of contiguous or overlapping sites of ovary and other uterine adnexa whose point of origin cannot be determined

183.9    Uterine adnexa, unspecified

184       Malignant neoplasm of other and unspecified female genital organs

Excludes:          carcinoma in situ (233.3)

184.0    Vagina

Gartner's duct

Vaginal vault

184.1    Labia majora

Greater vestibular [Bartholin's] gland

184.2    Labia minora

184.3    Clitoris

184.4    Vulva, unspecified

External female genitalia NOS

Pudendum

184.8    Other specified sites of female genital organs

Malignant neoplasm of contiguous or overlapping sites of female genital organs whose point of origin cannot be determined

184.9    Female genital organ, site unspecified

Female genitourinary tract NOS

185       Malignant neoplasm of prostate

Excludes:          seminal vesicles (187.8)

186       Malignant neoplasm of testis

Use additional code to identify any functional activity

186.0    Undescended testis

Ectopic testis

Retained testis

186.9    Other and unspecified testis

Testis:

NOS

descended

scrotal

187       Malignant neoplasm of penis and other male genital organs

187.1    Prepuce

Foreskin

187.2    Glans penis

187.3    Body of penis

Corpus cavernosum

187.4    Penis, part unspecified

Skin of penis NOS

187.5    Epididymis

187.6    Spermatic cord

Vas deferens

187.7    Scrotum

Skin of scrotum

187.8    Other specified sites of male genital organs

Seminal vesicle

Tunica vaginalis

Malignant neoplasm of contiguous or overlapping sites of penis and other male genital organs whose point of origin cannot be determined

187.9    Male genital organ, site unspecified

Male genital organ or tract NOS

188       Malignant neoplasm of bladder

Excludes:          carcinoma in situ (233.7)

188.0    Trigone of urinary bladder

188.1    Dome of urinary bladder

188.2    Lateral wall of urinary bladder

188.3    Anterior wall of urinary bladder

188.4    Posterior wall of urinary bladder

188.5    Bladder neck

Internal urethral orifice

188.6    Ureteric orifice

188.7    Urachus

188.8    Other specified sites of bladder

Malignant neoplasm of contiguous or overlapping sites of bladder whose point of origin cannot be determined

188.9    Bladder, part unspecified

Bladder wall NOS

189       Malignant neoplasm of kidney and other and unspecified urinary organs

189.0    Kidney, except pelvis

Kidney NOS

Kidney parenchyma

189.1    Renal pelvis

Renal calyces

Ureteropelvic junction

189.2    Ureter

Excludes:          ureteric orifice of bladder (188.6)

189.3    Urethra

Excludes:          urethral orifice of bladder (188.5)

189.4    Paraurethral glands

189.8    Other specified sites of urinary organs

Malignant neoplasm of contiguous or overlapping sites of kidney and other urinary organs whose point of origin cannot be determined

189.9    Urinary organ, site unspecified

Urinary system NOS

MALIGNANT NEOPLASM OF OTHER AND UNSPECIFIED SITES (190-199)

Excludes:         carcinoma in situ (234.0-234.9)

190       Malignant neoplasm of eye

Excludes:          carcinoma in situ (234.0)

eyelid (skin) (172.1, 173.1)

cartilage (171.0)

optic nerve (192.0)

orbital bone (170.0)

190.0    Eyeball, except conjunctiva, cornea, retina, and choroid

Ciliary body

Crystalline lens

Iris

Sclera

Uveal tract

190.1    Orbit

Connective tissue of orbit

Extraocular muscle

Retrobulbar

Excludes:          bone of orbit (170.0)

190.2    Lacrimal gland

190.3    Conjunctiva

190.4    Cornea

190.5    Retina

190.6    Choroid

190.7    Lacrimal duct

Lacrimal sac

Nasolacrimal duct

190.8    Other specified sites of eye

Malignant neoplasm of contiguous or overlapping sites of eye whose point of origin cannot be determined

190.9    Eye, part unspecified

191       Malignant neoplasm of brain

Excludes:          cranial nerves (192.0)

retrobulbar area (190.1)

191.0    Cerebrum, except lobes and ventricles

Basal ganglia

Cerebral cortex

Corpus striatum

Globus pallidus

Hypothalamus

Thalamus

191.1    Frontal lobe

191.2    Temporal lobe

Hippocampus

Uncus

191.3    Parietal lobe

191.4    Occipital lobe

191.5    Ventricles

Choroid plexus

Floor of ventricle

191.6    Cerebellum NOS

Cerebellopontine angle

191.7    Brain stem

Cerebral peduncle

Medulla oblongata

Midbrain

Pons

191.8    Other parts of brain

Corpus callosum

Tapetum

Malignant neoplasm of contiguous or overlapping sites of brain whose point of origin cannot be determined

191.9    Brain, unspecified

Cranial fossa NOS

192       Malignant neoplasm of other and unspecified parts of nervous system

Excludes:          peripheral, sympathetic, and parasympathetic nerves and ganglia (171.0-171.9)

192.0    Cranial nerves

Olfactory bulb

192.1    Cerebral meninges

Dura (mater)

Falx (cerebelli) (cerebri)

Meninges NOS

Tentorium

192.2    Spinal cord

Cauda equina

192.3    Spinal meninges

192.8    Other specified sites of nervous system

Malignant neoplasm of contiguous or overlapping sites of other parts of nervous system whose point of origin cannot be determined

192.9    Nervous system, part unspecified

Nervous system (central) NOS

Excludes:          meninges NOS (192.1)

193       Malignant neoplasm of thyroid gland

Sipple's syndrome

Thyroglossal duct

Use additional code to identify any functional activity

194       Malignant neoplasm of other endocrine glands and related structures

Use additional code to identify any functional activity

Excludes:          islets of Langerhans (157.4)

ovary (183.0)

testis (186.0-186.9)

thymus (164.0)

194.0    Adrenal gland

Adrenal cortex

Adrenal medulla

Suprarenal gland

194.1    Parathyroid gland

194.3    Pituitary gland and craniopharyngeal duct

Craniobuccal pouch

Hypophysis

Rathke's pouch

Sella turcica

194.4    Pineal gland

194.5    Carotid body

194.6    Aortic body and other paraganglia

Coccygeal body

Glomus jugulare

Para-aortic body

194.8    Other

Pluriglandular involvement NOS

Note:    If the sites of multiple involvements are known, they should be coded separately.

194.9    Endocrine gland, site unspecified

195       Malignant neoplasm of other and ill-defined sites

Includes:           malignant neoplasms of contiguous sites, not elsewhere classified, whose point of origin cannot be determined

Excludes:          malignant neoplasm:

lymphatic and hematopoietic tissue (200.0-208.9)

secondary sites (196.0-198.8)

unspecified site (199.0-199.1)

195.0    Head, face, and neck

Cheek NOS

Jaw NOS

Nose NOS

Supraclavicular region NOS

195.1    Thorax

Axilla

Chest (wall) NOS

Intrathoracic NOS

195.2    Abdomen

Intra-abdominal NOS

195.3    Pelvis

Groin

Inguinal region NOS

Presacral region

Sacrococcygeal region

Sites overlapping systems within pelvis, as:

rectovaginal (septum)

rectovesical (septum)

195.4    Upper limb

195.5    Lower limb

195.8    Other specified sites

Back NOS

Flank NOS

Trunk NOS

196       Secondary and unspecified malignant neoplasm of lymph nodes

Excludes:          any malignant neoplasm of lymph nodes, specified as primary (200.0-202.9)

Hodgkin's disease (201.0-201.9)

lymphosarcoma (200.1)

reticulosarcoma (200.0)

other forms of lymphoma (202.0-202.9)

196.0    Lymph nodes of head, face, and neck

Cervical

Cervicofacial

Scalene

Supraclavicular

196.1    Intrathoracic lymph nodes

Bronchopulmonary

Intercostal

Mediastinal

Tracheobronchial

196.2    Intra-abdominal lymph nodes

Intestinal

Mesenteric

Retroperitoneal

196.3    Lymph nodes of axilla and upper limb

Brachial

Epitrochlear

Infraclavicular

Pectoral

196.5    Lymph nodes of inguinal region and lower limb

Femoral

Groin

Popliteal

Tibial

196.6    Intrapelvic lymph nodes

Hypogastric

Iliac

Obturator

Parametrial

196.8    Lymph nodes of multiple sites

196.9    Site unspecified

Lymph nodes NOS

197       Secondary malignant neoplasm of respiratory and digestive systems

Excludes:          lymph node metastasis (196.0-196.9)

197.0    Lung

Bronchus

197.1    Mediastinum

197.2    Pleura

197.3    Other respiratory organs

Trachea

197.4    Small intestine, including duodenum

197.5    Large intestine and rectum

197.6    Retroperitoneum and peritoneum

197.7    Liver, specified as secondary

197.8    Other digestive organs and spleen

198       Secondary malignant neoplasm of other specified sites

Excludes:          lymph node metastasis (196.0-196.9)

198.0    Kidney

198.1    Other urinary organs

198.2    Skin

Skin of breast

198.3    Brain and spinal cord

198.4    Other parts of nervous system

Meninges (cerebral) (spinal)

198.5    Bone and bone marrow

198.6    Ovary

198.7    Adrenal gland

Suprarenal gland

198.8    Other specified sites

198.81  Breast

Excludes:          skin of breast (198.2)

198.82  Genital organs

198.89  Other

Excludes:          retroperitoneal lymph nodes (196.2)

199       Malignant neoplasm without specification of site

199.0    Disseminated

Carcinomatosis unspecified site (primary) (secondary)

Generalized:

cancer unspecified site (primary) (secondary)

malignancy unspecified site (primary) (secondary)

Multiple cancer unspecified site (primary) (secondary)

199.1    Other

Cancer unspecified site (primary) (secondary)

Carcinoma unspecified site (primary) (secondary)

Malignancy unspecified site (primary) (secondary)

MALIGNANT NEOPLASM OF LYMPHATIC AND HEMATOPOIETIC TISSUE (200-208)

Excludes:         secondary neoplasm of:

bone marrow (198.5)

spleen (197.8)

secondary and unspecified neoplasm of lymph nodes (196.0-196.9)

The following fifth-digit subclassification is for use with categories 200-202:

0 unspecified site, extranodal and solid organ sites

1 lymph nodes of head, face, and neck

2 intrathoracic lymph nodes

3 intra-abdominal lymph nodes

4 lymph nodes of axilla and upper limb

5 lymph nodes of inguinal region and lower limb

6 intrapelvic lymph nodes

7 spleen

8 lymph nodes of multiple sites

200       Lymphosarcoma and reticulosarcoma

Requires fifth digit. See note before section 200 for codes and definitions.

200.0    Reticulosarcoma

Lymphoma (malignant):

histiocytic (diffuse):

nodular

pleomorphic cell type

reticulum cell type

Reticulum cell sarcoma:

NOS

pleomorphic cell type

200.1    Lymphosarcoma

Lymphoblastoma (diffuse)

Lymphoma (malignant):

lymphoblastic (diffuse)

lymphocytic (cell type) (diffuse)

lymphosarcoma type

Lymphosarcoma:

NOS

diffuse NOS

lymphoblastic (diffuse)

lymphocytic (diffuse)

prolymphocytic

Excludes:          lymphosarcoma:

follicular or nodular (202.0)

mixed cell type (200.8)

lymphosarcoma cell leukemia (207.8)

200.2    Burkitt's tumor or lymphoma

Malignant lymphoma, Burkitt's type

200.8    Other named variants

Lymphoma (malignant):

lymphoplasmacytoid type

mixed lymphocytic-histiocytic (diffuse)

Lymphosarcoma, mixed cell type (diffuse)

Reticulolymphosarcoma (diffuse)

201       Hodgkin's disease

Requires fifth digit. See note before section 200 for codes and definitions.

201.0    Hodgkin's paragranuloma

201.1    Hodgkin's granuloma

201.2    Hodgkin's sarcoma

201.4    Lymphocytic-histiocytic predominance

201.5    Nodular sclerosis

Hodgkin's disease, nodular sclerosis:

NOS

cellular phase

201.6    Mixed cellularity

201.7    Lymphocytic depletion

Hodgkin's disease, lymphocytic depletion:

NOS

diffuse fibrosis

reticular type

201.9    Hodgkin's disease, unspecified

Hodgkin's:

disease NOS

lymphoma NOS

Malignant:

lymphogranuloma

lymphogranulomatosis

202       Other malignant neoplasms of lymphoid and histiocytic tissue

Requires fifth digit. See note before section 200 for codes and definitions.

202.0    Nodular lymphoma

Brill-Symmers disease

Lymphoma:

follicular (giant)

lymphocytic, nodular

Lymphosarcoma:

follicular (giant)

nodular

Reticulosarcoma, follicular or nodular

202.1    Mycosis fungoides

202.2    Sézary's disease

202.3    Malignant histiocytosis

Histiocytic medullary reticulosis

Malignant:

reticuloendotheliosis

reticulosis

202.4    Leukemic reticuloendotheliosis

Hairy-cell leukemia

202.5    Letterer-Siwe disease

Acute:

differentiated progressive histiocytosis

histiocytosis X (progressive)

infantile reticuloendotheliosis

reticulosis of infancy

Excludes:          Hand-Schüller-Christian disease (277.89)

histiocytosis (acute) (chronic) (277.89)

histiocytosis X (chronic) (277.89)

202.6    Malignant mast cell tumors

Malignant:

mastocytoma

mastocytosis

Mast cell sarcoma

Systemic tissue mast cell disease

Excludes:          mast cell leukemia (207.8)

202.8    Other lymphomas

Lymphoma (malignant):

NOS

diffuse

Excludes:          benign lymphoma (229.0)

202.9    Other and unspecified malignant neoplasms of lymphoid and histiocytic tissue

Follicular dendritic cell sarcoma

Interdigitating dendritic cell sarcoma

Langerhans cell sarcoma

Malignant neoplasm of bone marrow NOS

203       Multiple myeloma and immunoproliferative neoplasms

The following fifth-digit subclassification is for use with category 203:

0 without mention of remission

1 in remission

203.0    Multiple myeloma

Kahler's disease

Myelomatosis

Excludes:          solitary myeloma (238.6)

203.1    Plasma cell leukemia

Plasmacytic leukemia

203.8    Other immunoproliferative neoplasms

204       Lymphoid leukemia

Includes:           leukemia:

lymphatic

lymphoblastic

lymphocytic

lymphogenous

The following fifth-digit subclassification is for use with category 204:

0 without mention of remission

1 in remission

204.0    Acute

Excludes:          acute exacerbation of chronic lymphoid leukemia (204.1)

204.1    Chronic

204.2    Subacute

204.8    Other lymphoid leukemia

Aleukemic leukemia:

lymphatic

lymphocytic

lymphoid

204.9    Unspecified lymphoid leukemia

205       Myeloid leukemia

Includes:           leukemia:

granulocytic

myeloblastic

myelocytic

myelogenous

myelomonocytic

myelosclerotic

myelosis

The following fifth-digit subclassification is for use with category 205:

0 without mention of remission

1 in remission

205.0    Acute

Acute promyelocytic leukemia

Excludes:          acute exacerbation of chronic myeloid leukemia (205.1)

205.1    Chronic

Eosinophilic leukemia

Neutrophilic leukemia

205.2    Subacute

205.3    Myeloid sarcoma

Chloroma

Granulocytic sarcoma

205.8    Other myeloid leukemia

Aleukemic leukemia:

granulocytic

myelogenous

myeloid

Aleukemic myelosis

205.9    Unspecified myeloid leukemia

206       Monocytic leukemia

Includes:           leukemia:

histiocytic

monoblastic

monocytoid

The following fifth-digit subclassification is for use with category 206:

0 without mention of remission

1 in remission

206.0    Acute

Excludes:          acute exacerbation of chronic monocytic leukemia (206.1)

206.1    Chronic

206.2    Subacute

206.8    Other monocytic leukemia

Aleukemic:

monocytic leukemia

monocytoid leukemia

206.9    Unspecified monocytic leukemia

207       Other specified leukemia

Excludes:          leukemic reticuloendotheliosis (202.4)

plasma cell leukemia (203.1)

The following fifth-digit subclassification is for use with category 207:

0 without mention of remission

1 in remission

207.0    Acute erythremia and erythroleukemia

Acute erythremic myelosis

Di Guglielmo's disease

Erythremic myelosis

207.1    Chronic erythremia

Heilmeyer-Schöner disease

207.2    Megakaryocytic leukemia

Megakaryocytic myelosis

Thrombocytic leukemia

207.8    Other specified leukemia

Lymphosarcoma cell leukemia

208       Leukemia of unspecified cell type

The following fifth-digit subclassification is for use with category 208:

0 without mention of remission

1 in remission

208.0    Acute

Acute leukemia NOS

Blast cell leukemia

Stem cell leukemia

Excludes:          acute exacerbation of chronic unspecified leukemia (208.1)

208.1    Chronic

Chronic leukemia NOS

208.2    Subacute

Subacute leukemia NOS

208.8    Other leukemia of unspecified cell type

208.9    Unspecified leukemia

Leukemia NOS

BENIGN NEOPLASMS (210-229)

210       Benign neoplasm of lip, oral cavity, and pharynx

Excludes:          cyst (of):

jaw (526.0-526.2, 526.89)

oral soft tissue (528.4)

radicular (522.8)

210.0    Lip

Frenulum labii

Lip (inner aspect) (mucosa) (vermilion border)

Excludes:          labial commissure (210.4)

skin of lip (216.0)

210.1    Tongue

Lingual tonsil

210.2    Major salivary glands

Gland:

parotid

sublingual

submandibular

Excludes:          benign neoplasms of minor salivary glands:

NOS (210.4)

buccal mucosa (210.4)

lips (210.0)

palate (hard) (soft) (210.4)

tongue (210.1)

tonsil, palatine (210.5)

210.3    Floor of mouth

210.4    Other and unspecified parts of mouth

Gingiva

Gum (upper) (lower)

Labial commissure

Oral cavity NOS

Oral mucosa

Palate (hard) (soft)

Uvula

Excludes:          benign odontogenic neoplasms of bone (213.0-213.1)

developmental odontogenic cysts (526.0)

mucosa of lips (210.0)

nasopharyngeal [posterior] [superior] surface of soft palate (210.7)

210.5    Tonsil

Tonsil (faucial) (palatine)

Excludes:          lingual tonsil (210.1)

pharyngeal tonsil (210.7)

tonsillar:

fossa (210.6)

pillars (210.6)

210.6    Other parts of oropharynx

Branchial cleft or vestiges

Epiglottis, anterior aspect

Fauces NOS

Mesopharynx NOS

Tonsillar:

fossa

pillars

Vallecula

Excludes:          epiglottis:

NOS (212.1)

suprahyoid portion (212.1)

210.7    Nasopharynx

Adenoid tissue

Lymphadenoid tissue

Pharyngeal tonsil

Posterior nasal septum

210.8    Hypopharynx

Arytenoid fold

Laryngopharynx

Postcricoid region

Pyriform fossa

210.9    Pharynx, unspecified

Throat NOS

211       Benign neoplasm of other parts of digestive system

211.0    Esophagus

211.1    Stomach

Body of stomach

Cardia of stomach

Fundus of stomach

Cardiac orifice

Pylorus

211.2    Duodenum, jejunum, and ileum

Small intestine NOS

Excludes:          ampulla of Vater (211.5)

ileocecal valve (211.3)

211.3    Colon

Appendix

Cecum

Ileocecal valve

Large intestine NOS

Excludes:          rectosigmoid junction (211.4)

211.4    Rectum and anal canal

Anal canal or sphincter

Anus NOS

Rectosigmoid junction

Excludes:          anus:

margin (216.5)

skin (216.5)

perianal skin (216.5)

211.5    Liver and biliary passages

Ampulla of Vater

Common bile duct

Cystic duct

Gallbladder

Hepatic duct

Sphincter of Oddi

211.6    Pancreas, except islets of Langerhans

211.7    Islets of Langerhans

Islet cell tumor

Use additional code to identify any functional activity

211.8    Retroperitoneum and peritoneum

Mesentery

Mesocolon

Omentum

Retroperitoneal tissue

211.9    Other and unspecified site

Alimentary tract NOS

Digestive system NOS

Gastrointestinal tract NOS

Intestinal tract NOS

Intestine NOS

Spleen, not elsewhere classified

212       Benign neoplasm of respiratory and intrathoracic organs

212.0    Nasal cavities, middle ear, and accessory sinuses

Cartilage of nose

Eustachian tube

Nares

Septum of nose

Sinus:

ethmoidal

frontal

maxillary

sphenoidal

Excludes:          auditory canal (external) (216.2)

bone of:

ear (213.0)

nose [turbinates] (213.0)

cartilage of ear (215.0)

ear (external) (skin) (216.2)

nose NOS (229.8)

skin (216.3)

olfactory bulb (225.1)

polyp of:

accessory sinus (471.8)

ear (385.30-385.35)

nasal cavity (471.0)

posterior margin of septum and choanae (210.7)

212.1    Larynx

Cartilage:

arytenoid

cricoid

cuneiform

thyroid

Epiglottis (suprahyoid portion) NOS

Glottis

Vocal cords (false) (true)

Excludes:          epiglottis, anterior aspect (210.6)

polyp of vocal cord or larynx (478.4)

212.2    Trachea

212.3    Bronchus and lung

Carina

Hilus of lung

212.4    Pleura

212.5    Mediastinum

212.6    Thymus

212.7    Heart

Excludes:          great vessels (215.4)

212.8    Other specified sites

212.9    Site unspecified

Respiratory organ NOS

Upper respiratory tract NOS

Excludes:          intrathoracic NOS (229.8)

thoracic NOS (229.8)

213       Benign neoplasm of bone and articular cartilage

Includes:           cartilage (articular) (joint)

periosteum

Excludes:          cartilage of:

ear (215.0)

eyelid (215.0)

larynx (212.1)

nose (212.0)

exostosis NOS (726.91)

synovia (215.0-215.9)

213.0    Bones of skull and face

Excludes:          lower jaw bone (213.1)

213.1    Lower jaw bone

213.2    Vertebral column, excluding sacrum and coccyx

213.3    Ribs, sternum, and clavicle

213.4    Scapula and long bones of upper limb

213.5    Short bones of upper limb

213.6    Pelvic bones, sacrum, and coccyx

213.7    Long bones of lower limb

213.8    Short bones of lower limb

213.9    Bone and articular cartilage, site unspecified

214       Lipoma

Includes:           angiolipoma

fibrolipoma

hibernoma

lipoma (fetal) (infiltrating) (intramuscular)

myelolipoma

myxolipoma

214.0    Skin and subcutaneous tissue of face

214.1    Other skin and subcutaneous tissue

214.2    Intrathoracic organs

214.3    Intra-abdominal organs

214.4    Spermatic cord

214.8    Other specified sites

214.9    Lipoma, unspecified site

215       Other benign neoplasm of connective and other soft tissue

Includes:           blood vessel

bursa

fascia

ligament

muscle

peripheral, sympathetic, and parasympathetic nerves and ganglia

synovia

tendon (sheath)

Excludes:          cartilage:

articular (213.0-213.9)

larynx (212.1)

nose (212.0)

connective tissue of:

breast (217)

internal organ, except lipoma and hemangioma­code to benign neoplasm of the site

lipoma (214.0-214.9)

215.0    Head, face, and neck

215.2    Upper limb, including shoulder

215.3    Lower limb, including hip

215.4    Thorax

Excludes:          heart (212.7)

mediastinum (212.5)

thymus (212.6)

215.5    Abdomen

Abdominal wall

Hypochondrium

215.6    Pelvis

Buttock

Groin

Inguinal region

Perineum

Excludes:          uterine:

leiomyoma (218.0-218.9)

ligament, any (221.0)

215.7    Trunk, unspecified

Back NOS

Flank NOS

215.8    Other specified sites

215.9    Site unspecified

216       Benign neoplasm of skin

Includes:           blue nevus

dermatofibroma

hydrocystoma

pigmented nevus

syringoadenoma

syringoma

Excludes:          skin of genital organs (221.0-222.9)

216.0    Skin of lip

Excludes:          vermilion border of lip (210.0)

216.1    Eyelid, including canthus

Excludes:          cartilage of eyelid (215.0)

216.2    Ear and external auditory canal

Auricle (ear)

Auricular canal, external

External meatus

Pinna

Excludes:          cartilage of ear (215.0)

216.3    Skin of other and unspecified parts of face

Cheek, external

Eyebrow

Nose, external

Temple

216.4    Scalp and skin of neck

216.5    Skin of trunk, except scrotum

Axillary fold

Perianal skin

Skin of:

abdominal wall

anus

back

breast

buttock

chest wall

groin

perineum

Umbilicus

Excludes:          anal canal (211.4)

anus NOS (211.4)

skin of scrotum (222.4)

216.6    Skin of upper limb, including shoulder

216.7    Skin of lower limb, including hip

216.8    Other specified sites of skin

216.9    Skin, site unspecified

217       Benign neoplasm of breast

Breast (male) (female)

connective tissue

glandular tissue

soft parts

Excludes:          adenofibrosis (610.2)

benign cyst of breast (610.0)

fibrocystic disease (610.1)

skin of breast (216.5)

218       Uterine leiomyoma

Includes:           fibroid (bleeding) (uterine)

uterine:

fibromyoma

myoma

218.0    Submucous leiomyoma of uterus

218.1    Intramural leiomyoma of uterus

Interstitial leiomyoma of uterus

218.2    Subserous leiomyoma of uterus

Subperitoneal leiomyoma of uterus

218.9    Leiomyoma of uterus, unspecified

219       Other benign neoplasm of uterus

219.0    Cervix uteri

219.1    Corpus uteri

Endometrium

Fundus

Myometrium

219.8    Other specified parts of uterus

219.9    Uterus, part unspecified

220       Benign neoplasm of ovary

Use additional code to identify any functional activity (256.0-256.1)

Excludes:          cyst:

corpus albicans (620.2)

corpus luteum (620.1)

endometrial (617.1)

follicular (atretic) (620.0)

graafian follicle (620.0)

ovarian NOS (620.2)

retention (620.2)

221       Benign neoplasm of other female genital organs

Includes:           adenomatous polyp

benign teratoma

Excludes:          cyst:

epoophoron (752.11)

fimbrial (752.11)

Gartner's duct (752.11)

parovarian (752.11)

221.0    Fallopian tube and uterine ligaments

Oviduct

Parametrium

Uterine ligament (broad) (round) (uterosacral)

Uterine tube

221.1    Vagina

221.2    Vulva

Clitoris

External female genitalia NOS

Greater vestibular [Bartholin's] gland

Labia (majora) (minora)

Pudendum

Excludes:          Bartholin's (duct) (gland) cyst (616.2)

221.8    Other specified sites of female genital organs

221.9    Female genital organ, site unspecified

Female genitourinary tract NOS

222       Benign neoplasm of male genital organs

222.0    Testis

Use additional code to identify any functional activity

222.1    Penis

Corpus cavernosum

Glans penis

Prepuce

222.2    Prostate

Excludes:          adenomatous hyperplasia of prostate (600.20-600.21)

prostatic:

adenoma (600.20-600.21)

enlargement (600.00-600.01)

hypertrophy (600.00-600.01)

222.3    Epididymis

222.4    Scrotum

Skin of scrotum

222.8    Other specified sites of male genital organs

Seminal vesicle

Spermatic cord

222.9    Male genital organ, site unspecified

Male genitourinary tract NOS

223       Benign neoplasm of kidney and other urinary organs

223.0    Kidney, except pelvis

Kidney NOS

Excludes:          renal:

calyces (223.1)

pelvis (223.1)

223.1    Renal pelvis

223.2    Ureter

Excludes:          ureteric orifice of bladder (223.3)

223.3    Bladder

223.8    Other specified sites of urinary organs

223.81  Urethra

Excludes:          urethral orifice of bladder (223.3)

223.89  Other

Paraurethral glands

223.9    Urinary organ, site unspecified

Urinary system NOS

224       Benign neoplasm of eye

Excludes:          cartilage of eyelid (215.0)

eyelid (skin) (216.1)

optic nerve (225.1)

orbital bone (213.0)

224.0    Eyeball, except conjunctiva, cornea, retina, and choroid

Ciliary body

Iris

Sclera

Uveal tract

224.1    Orbit

Excludes:          bone of orbit (213.0)

224.2    Lacrimal gland

224.3    Conjunctiva

224.4    Cornea

224.5    Retina

Excludes:          hemangioma of retina (228.03)

224.6    Choroid

224.7    Lacrimal duct

Lacrimal sac

Nasolacrimal duct

224.8    Other specified parts of eye

224.9    Eye, part unspecified

225       Benign neoplasm of brain and other parts of nervous system

Excludes:          hemangioma (228.02)

neurofibromatosis (237.7)

peripheral, sympathetic, and parasympathetic nerves and ganglia (215.0-215.9)

retrobulbar (224.1)

225.0    Brain

225.1    Cranial nerves

225.2    Cerebral meninges

Meninges NOS

Meningioma (cerebral)

225.3    Spinal cord

Cauda equina

225.4    Spinal meninges

Spinal meningioma

225.8    Other specified sites of nervous system

225.9    Nervous system, part unspecified

Nervous system (central) NOS

Excludes:          meninges NOS (225.2)

226       Benign neoplasm of thyroid glands

Use additional code to identify any functional activity

227       Benign neoplasm of other endocrine glands and related structures

Use additional code to identify any functional activity

Excludes:          ovary (220)

pancreas (211.6)

testis (222.0)

227.0    Adrenal gland

Suprarenal gland

227.1    Parathyroid gland

227.3    Pituitary gland and craniopharyngeal duct (pouch)

Craniobuccal pouch

Hypophysis

Rathke's pouch

Sella turcica

227.4    Pineal gland

Pineal body

227.5    Carotid body

227.6    Aortic body and other paraganglia

Coccygeal body

Glomus jugulare

Para-aortic body

227.8    Other

227.9    Endocrine gland, site unspecified

228       Hemangioma and lymphangioma, any site

Includes:           angioma (benign) (cavernous) (congenital) NOS

cavernous nevus

glomus tumor

hemangioma (benign) (congenital)

Excludes:          benign neoplasm of spleen, except hemangioma and lymphangioma (211.9)

glomus jugulare (227.6)

nevus:

NOS (216.0-216.9)

blue or pigmented (216.0-216.9)

vascular (757.32)

228.0    Hemangioma, any site

228.00  Of unspecified site

228.01  Of skin and subcutaneous tissue

228.02  Of intracranial structures

228.03  Of retina

228.04  Of intra-abdominal structures

Peritoneum

Retroperitoneal tissue

228.09  Of other sites

Systemic angiomatosis

228.1    Lymphangioma, any site

Congenital lymphangioma

Lymphatic nevus

229       Benign neoplasm of other and unspecified sites

229.0    Lymph nodes

Excludes:          lymphangioma (228.1)

229.8    Other specified sites

Intrathoracic NOS

Thoracic NOS

229.9    Site unspecified

CARCINOMA IN SITU (230-234)

Includes:          Bowen's disease

erythroplasia

Queyrat's erythroplasia

Excludes:         leukoplakia­see Alphabetic Index

230       Carcinoma in situ of digestive organs

230.0    Lip, oral cavity, and pharynx

Gingiva

Hypopharynx

Mouth [any part]

Nasopharynx

Oropharynx

Salivary gland or duct

Tongue

Excludes:          aryepiglottic fold or interarytenoid fold, laryngeal aspect (231.0)

epiglottis:

NOS (231.0)

suprahyoid portion (231.0)

skin of lip (232.0)

230.1    Esophagus

230.2    Stomach

Body of stomach

Cardia of stomach

Fundus of stomach

Cardiac orifice

Pylorus

230.3    Colon

Appendix

Cecum

Ileocecal valve

Large intestine NOS

Excludes:          rectosigmoid junction (230.4)

230.4    Rectum

Rectosigmoid junction

230.5    Anal canal

Anal sphincter

230.6    Anus, unspecified

Excludes:          anus:

margin (232.5)

skin (232.5)

perianal skin (232.5)

230.7    Other and unspecified parts of intestine

Duodenum

Ileum

Jejunum

Small intestine NOS

Excludes:          ampulla of Vater (230.8)

230.8    Liver and biliary system

Ampulla of Vater

Common bile duct

Cystic duct

Gallbladder

Hepatic duct

Sphincter of Oddi

230.9    Other and unspecified digestive organs

Digestive organ NOS

Gastrointestinal tract NOS

Pancreas

Spleen

231       Carcinoma in situ of respiratory system

231.0    Larynx

Cartilage:

arytenoid

cricoid

cuneiform

thyroid

Epiglottis:

NOS

posterior surface

suprahyoid portion

Vocal cords (false) (true)

Excludes:          aryepiglottic fold or interarytenoid fold:

NOS (230.0)

hypopharyngeal aspect (230.0)

marginal zone (230.0)

231.1    Trachea

231.2    Bronchus and lung

Carina

Hilus of lung

231.8    Other specified parts of respiratory system

Accessory sinuses

Middle ear

Nasal cavities

Pleura

Excludes:          ear (external) (skin) (232.2)

nose NOS (234.8)

skin (232.3)

231.9    Respiratory system, part unspecified

Respiratory organ NOS

232       Carcinoma in situ of skin

Includes:           pigment cells

232.0    Skin of lip

Excludes:          vermilion border of lip (230.0)

232.1    Eyelid, including canthus

232.2    Ear and external auditory canal

232.3    Skin of other and unspecified parts of face

232.4    Scalp and skin of neck

232.5    Skin of trunk, except scrotum

Anus, margin

Axillary fold

Perianal skin

Skin of:

abdominal wall

anus

back

breast

buttock

chest wall

groin

perineum

Umbilicus

Excludes:          anal canal (230.5)

anus NOS (230.6)

skin of genital organs (233.3, 233.5-233.6)

232.6    Skin of upper limb, including shoulder

232.7    Skin of lower limb, including hip

232.8    Other specified sites of skin

232.9    Skin, site unspecified

233       Carcinoma in situ of breast and genitourinary system

233.0    Breast

Excludes:          Paget's disease (174.0-174.9)

skin of breast (232.5)

233.1    Cervix uteri

Cervical intraepithelial neoplasia III [CIN III]

Severe dysplasia of cervix

Excludes:          cervical intraepithelial neoplasia II [CIN II] (622.12)

cytologic evidence of malignancy without histologic confirmation (795.04)

high grade squamous intraepithelial lesion (HGSIL) (795.04)

moderate dysplasia of cervix (622.12)

233.2    Other and unspecified parts of uterus

233.3    Other and unspecified female genital organs

233.4    Prostate

233.5    Penis

233.6    Other and unspecified male genital organs

233.7    Bladder

233.9    Other and unspecified urinary organs

234       Carcinoma in situ of other and unspecified sites

234.0    Eye

Excludes:          cartilage of eyelid (234.8)

eyelid (skin) (232.1)

optic nerve (234.8)

orbital bone (234.8)

234.8    Other specified sites

Endocrine gland [any]

234.9    Site unspecified

Carcinoma in situ NOS

NEOPLASMS OF UNCERTAIN BEHAVIOR (235-238)

Note:    Categories 235-238 classify by site certain histo-morphologically well-defined neoplasms, the subsequent behavior of which cannot be predicted from the present appearance.

235       Neoplasm of uncertain behavior of digestive and respiratory systems

235.0    Major salivary glands

Gland:

parotid

sublingual

submandibular

Excludes:          minor salivary glands (235.1)

235.1    Lip, oral cavity, and pharynx

Gingiva

Hypopharynx

Minor salivary glands

Mouth

Nasopharynx

Oropharynx

Tongue

Excludes:          aryepiglottic fold or interarytenoid fold, laryngeal aspect (235.6)

epiglottis:

NOS (235.6)

suprahyoid portion (235.6)

skin of lip (238.2)

235.2    Stomach, intestines, and rectum

235.3    Liver and biliary passages

Ampulla of Vater

Bile ducts [any]

Gallbladder

Liver

235.4    Retroperitoneum and peritoneum

235.5    Other and unspecified digestive organs

Anal:

canal

sphincter

Anus NOS

Esophagus

Pancreas

Spleen

Excludes:          anus:

margin (238.2)

skin (238.2)

perianal skin (238.2)

235.6    Larynx

Excludes:          aryepiglottic fold or interarytenoid fold:

NOS (235.1)

hypopharyngeal aspect (235.1)

marginal zone (235.1)

235.7    Trachea, bronchus, and lung

235.8    Pleura, thymus, and mediastinum

235.9    Other and unspecified respiratory organs

Accessory sinuses

Middle ear

Nasal cavities

Respiratory organ NOS

Excludes:          ear (external) (skin) (238.2)

nose (238.8)

skin (238.2)

236       Neoplasm of uncertain behavior of genitourinary organs

236.0    Uterus

236.1    Placenta

Chorioadenoma (destruens)

Invasive mole

Malignant hydatid(iform) mole

236.2    Ovary

Use additional code to identify any functional activity

236.3    Other and unspecified female genital organs

236.4    Testis

Use additional code to identify any functional activity

236.5    Prostate

236.6    Other and unspecified male genital organs

236.7    Bladder

236.9    Other and unspecified urinary organs

236.90  Urinary organ, unspecified

236.91  Kidney and ureter

236.99  Other

237       Neoplasm of uncertain behavior of endocrine glands and nervous system

237.0    Pituitary gland and craniopharyngeal duct

Use additional code to identify any functional activity

237.1    Pineal gland

237.2    Adrenal gland

Suprarenal gland

Use additional code to identify any functional activity

237.3    Paraganglia

Aortic body

Carotid body

Coccygeal body

Glomus jugulare

237.4    Other and unspecified endocrine glands

Parathyroid gland

Thyroid gland

237.5    Brain and spinal cord

237.6    Meninges

Meninges:

NOS

cerebral

spinal

237.7    Neurofibromatosis

von Recklinghausen's disease

237.70  Neurofibromatosis, unspecified

237.71  Neurofibromatosis, type 1 [von Recklinghausen's disease]

237.72  Neurofibromatosis, type 2 [acoustic neurofibromatosis]

237.9    Other and unspecified parts of nervous system

Cranial nerves

Excludes:          peripheral, sympathetic, and parasympathetic nerves and ganglia (238.1)

238       Neoplasm of uncertain behavior of other and unspecified sites and tissues

238.0    Bone and articular cartilage

Excludes:          cartilage:

ear (238.1)

eyelid (238.1)

larynx (235.6)

nose (235.9)

synovia (238.1)

238.1    Connective and other soft tissue

Peripheral, sympathetic, and parasympathetic nerves and ganglia

Excludes:          cartilage (of):

articular (238.0)

larynx (235.6)

nose (235.9)

connective tissue of breast (238.3)

238.2    Skin

Excludes:          anus NOS (235.5)

skin of genital organs (236.3, 236.6)

vermilion border of lip (235.1)

238.3    Breast

Excludes:          skin of breast (238.2)

238.4    Polycythemia vera

238.5    Histiocytic and mast cells

Mast cell tumor NOS

Mastocytoma NOS

238.6    Plasma cells

Plasmacytoma NOS

Solitary myeloma

238.7    Other lymphatic and hematopoietic tissues

Disease:

lymphoproliferative (chronic) NOS

myeloproliferative (chronic) NOS

Idiopathic thrombocythemia

Megakaryocytic myelosclerosis

Myelodysplastic syndrome

Myelosclerosis with myeloid metaplasia

Panmyelosis (acute)

Refractory anemia

Excludes:          myelofibrosis (289.89)

myelosclerosis NOS (289.89)

myelosis:

NOS (205.9)

megakaryocytic (207.2)

238.8    Other specified sites

Eye

Heart

Excludes:          eyelid (skin) (238.2)

cartilage (238.1)

238.9    Site unspecified

NEOPLASMS OF UNSPECIFIED NATURE (239)

239       Neoplasms of unspecified nature

Note:    Category 239 classifies by site neoplasms of unspecified morphology and behavior. The term "mass," unless otherwise stated, is not to be regarded as a neoplastic growth.

Includes:           "growth" NOS

neoplasm NOS

new growth NOS

tumor NOS

239.0    Digestive system

Excludes:          anus:

margin (239.2)

skin (239.2)

perianal skin (239.2)

239.1    Respiratory system

239.2    Bone, soft tissue, and skin

Excludes:          anal canal (239.0)

anus NOS (239.0)

bone marrow (202.9)

cartilage:

larynx (239.1)

nose (239.1)

connective tissue of breast (239.3)

skin of genital organs (239.5)

vermilion border of lip (239.0)

239.3    Breast

Excludes:          skin of breast (239.2)

239.4    Bladder

239.5    Other genitourinary organs

239.6    Brain

Excludes:          cerebral meninges (239.7)

cranial nerves (239.7)

239.7    Endocrine glands and other parts of nervous system

Excludes:          peripheral, sympathetic, and parasympathetic nerves and ganglia (239.2)

239.8    Other specified sites

Excludes:          eyelid (skin) (239.2)

cartilage (239.2)

great vessels (239.2)

optic nerve (239.7)

239.9    Site unspecified

3. ENDOCRINE, NUTRITIONAL AND METABOLIC DISEASES, AND IMMUNITY DISORDERS (240-279) back to top

Excludes:         endocrine and metabolic disturbances specific

to the fetus and newborn (775.0-775.9)

Note:    All neoplasms, whether functionally active or not, are classified in Chapter 2. Codes in Chapter 3 (i.e., 242.8, 246.0, 251-253, 255-259) may be used to identify such functional activity associated with any neoplasm, or by ectopic endocrine tissue.

DISORDERS OF THYROID GLAND (240-246)

240       Simple and unspecified goiter

240.0    Goiter, specified as simple

Any condition classifiable to 240.9, specified as simple

240.9    Goiter, unspecified

Enlargement of thyroid

Goiter or struma:

NOS

diffuse colloid

endemic

hyperplastic

nontoxic (diffuse)

parenchymatous

sporadic

Excludes:          congenital (dyshormonogenic) goiter (246.1)

241       Nontoxic nodular goiter

Excludes:          adenoma of thyroid (226)

cystadenoma of thyroid (226)

241.0    Nontoxic uninodular goiter

Thyroid nodule

Uninodular goiter (nontoxic)

241.1    Nontoxic multinodular goiter

Multinodular goiter (nontoxic)

241.9    Unspecified nontoxic nodular goiter

Adenomatous goiter

Nodular goiter (nontoxic) NOS

Struma nodosa (simplex)

242       Thyrotoxicosis with or without goiter

Excludes:          neonatal thyrotoxicosis (775.3)

The following fifth-digit subclassification is for use with category 242:

0 without mention of thyrotoxic crisis or storm

1 with mention of thyrotoxic crisis or storm

242.0    Toxic diffuse goiter

Basedow's disease

Exophthalmic or toxic goiter NOS

Graves' disease

Primary thyroid hyperplasia

242.1    Toxic uninodular goiter

Thyroid nodule, toxic or with hyperthyroidism

Uninodular goiter, toxic or with hyperthyroidism

242.2    Toxic multinodular goiter

Secondary thyroid hyperplasia

242.3    Toxic nodular goiter, unspecified

Adenomatous goiter, toxic or with hyperthyroidism

Nodular goiter, toxic or with hyperthyroidism

Struma nodosa, toxic or with hyperthyroidism

Any condition classifiable to 241.9 specified as toxic or with hyperthyroidism

242.4    Thyrotoxicosis from ectopic thyroid nodule

242.8    Thyrotoxicosis of other specified origin

Overproduction of thyroid-stimulating hormone [TSH]

Thyrotoxicosis:

factitia from ingestion of excessive thyroid material

Use additional E code to identify cause, if drug-induced

242.9    Thyrotoxicosis without mention of goiter or other cause

Hyperthyroidism NOS

Thyrotoxicosis NOS

243       Congenital hypothyroidism

Congenital thyroid insufficiency

Cretinism (athyrotic) (endemic)

Use additional code to identify associated mental retardation

Excludes:          congenital (dyshormonogenic) goiter (246.1)

244       Acquired hypothyroidism

Includes:           athyroidism (acquired)

hypothyroidism (acquired)

myxedema (adult) (juvenile)

thyroid (gland) insufficiency (acquired)

244.0    Postsurgical hypothyroidism

244.1    Other postablative hypothyroidism

Hypothyroidism following therapy, such as irradiation

244.2    Iodine hypothyroidism

Hypothyroidism resulting from administration or ingestion of iodide

Use additional E to identify drug

244.3    Other iatrogenic hypothyroidism

Hypothyroidism resulting from:

P-aminosalicylic acid [PAS]

Phenylbutazone

Resorcinol

Iatrogenic hypothyroidism NOS

Use additional E to identify drug

244.8    Other specified acquired hypothyroidism

Secondary hypothyroidism NEC

244.9    Unspecified hypothyroidism

Hypothyroidism, primary or NOS

Myxedema, primary or NOS

245       Thyroiditis

245.0    Acute thyroiditis

Abscess of thyroid

Thyroiditis:

nonsuppurative, acute

pyogenic

suppurative

Use additional code to identify organism

245.1    Subacute thyroiditis

Thyroiditis:

de Quervain's

giant cell

granulomatous

viral

245.2    Chronic lymphocytic thyroiditis

Hashimoto's disease

Struma lymphomatosa

Thyroiditis:

autoimmune

lymphocytic (chronic)

245.3    Chronic fibrous thyroiditis

Struma fibrosa

Thyroiditis:

invasive (fibrous)

ligneous

Riedel's

245.4    Iatrogenic thyroiditis

Use additional E to identify cause

245.8    Other and unspecified chronic thyroiditis

Chronic thyroiditis:

NOS

nonspecific

245.9    Thyroiditis, unspecified

Thyroiditis NOS

246       Other disorders of thyroid

246.0    Disorders of thyrocalcitonin secretion

Hypersecretion of calcitonin or thyrocalcitonin

246.1    Dyshormonogenic goiter

Congenital (dyshormonogenic) goiter

Goiter due to enzyme defect in synthesis of thyroid hormone

Goitrous cretinism (sporadic)

246.2    Cyst of thyroid

Excludes:          cystadenoma of thyroid (226)

246.3    Hemorrhage and infarction of thyroid

246.8    Other specified disorders of thyroid

Abnormality of thyroid-binding globulin

Atrophy of thyroid

Hyper-TBG-nemia

Hypo-TBG-nemia

246.9    Unspecified disorder of thyroid

DISEASES OF OTHER ENDOCRINE GLANDS (250-259)

250       Diabetes mellitus

Excludes:          gestational diabetes (648.8)

hyperglycemia NOS (790.6)

neonatal diabetes mellitus (775.1)

nonclinical diabetes (790.29)

The following fifth-digit subclassification is for use with category 250:

0 type II or unspecified type, not stated as uncontrolled

Fifth-digit 0 is for use for type II patients, even if the patient requires insulin

Use additional code, if applicable, for associated long-term (current) insulin use V58.67

1 type I [juvenile type], not stated as uncontrolled

2 type II or unspecified type, uncontrolled

Use additional code, if applicable, for associated long-term (current) insulin use V58.67

Fifth-digit 2 is for use for type II, adult-onset, diabetic patients, even if the patient requires insulin

3 type I [juvenile type], uncontrolled

250.0    Diabetes mellitus without mention of complication

Diabetes mellitus without mention of complication or manifestation classifiable to 250.1-250.9

Diabetes (mellitus) NOS

250.1    Diabetes with ketoacidosis

Diabetic:

acidosis without mention of coma

ketosis without mention of coma

250.2    Diabetes with hyperosmolarity

Hyperosmolar (nonketotic) coma

250.3    Diabetes with other coma

Diabetic coma (with ketoacidosis)

Diabetic hypoglycemic coma

Insulin coma NOS

Excludes:          diabetes with hyperosmolar coma (250.2)

250.4    Diabetes with renal manifestations

Use additional code to identify manifestation, as:

chronic kidney disease (585.1-585.9)

diabetic:

nephropathy NOS (583.81)

nephrosis (581.81)

intercapillary glomerulosclerosis (581.81)

Kimmelstiel-Wilson syndrome (581.81)

250.5    Diabetes with ophthalmic manifestations

Use additional code to identify manifestation, as:

diabetic:

blindness (369.00-369.9)

cataract (366.41)

glaucoma (365.44)

macular edema (362.07)

retinal edema (362.07)

retinopathy (362.01-362.07)

250.6    Diabetes with neurological manifestations

Use additional code to identify manifestation, as:

diabetic:

amyotrophy (358.1)

gastroparalysis (536.3)

gastroparesis (536.3)

mononeuropathy (354.0-355.9)

neurogenic arthropathy (713.5)

peripheral autonomic neuropathy (337.1)

polyneuropathy (357.2)

250.7    Diabetes with peripheral circulatory disorders

Use additional code to identify manifestation, as:

diabetic:

gangrene (785.4)

peripheral angiopathy (443.81)

250.8    Diabetes with other specified manifestations

Diabetic hypoglycemia

Hypoglycemic shock

Use additional code to identify manifestation, as:

any associated ulceration (707.10-707.9)

diabetic bone changes (731.8)

Use additional E code to identify cause, if drug-induced

250.9    Diabetes with unspecified complication

251       Other disorders of pancreatic internal secretion

251.0    Hypoglycemic coma

Iatrogenic hyperinsulinism

Non-diabetic insulin coma

Use additional E code to identify cause, if drug-induced

Excludes:          hypoglycemic coma in diabetes mellitus (250.3)

251.1    Other specified hypoglycemia

Hyperinsulinism:

NOS

ectopic

functional

Hyperplasia of pancreatic islet beta cells NOS

Excludes:          hypoglycemia in diabetes mellitus (250.8)

hypoglycemia in infant of diabetic mother (775.0)

hypoglycemic coma (251.0)

neonatal hypoglycemia (775.6)

Use additional E code to identify cause, if drug-induced

251.2    Hypoglycemia, unspecified

Hypoglycemia:

NOS

reactive

spontaneous

Excludes:          hypoglycemia:

with coma (251.0)

in diabetes mellitus (250.8)

leucine-induced (270.3)

251.3    Postsurgical hypoinsulinemia

Hypoinsulinemia following complete or partial pancreatectomy

Postpancreatectomy hyperglycemia

251.4    Abnormality of secretion of glucagon

Hyperplasia of pancreatic islet alpha cells with glucagon excess

251.5    Abnormality of secretion of gastrin

Hyperplasia of pancreatic alpha cells with gastrin excess

Zollinger-Ellison syndrome

251.8    Other specified disorders of pancreatic internal secretion

251.9    Unspecified disorder of pancreatic internal secretion

Islet cell hyperplasia NOS

252       Disorders of parathyroid gland

252.0    Hyperparathyroidism

Excludes:          ectopic hyperparathyroidism (259.3)

252.00  Hyperparathyroidism, unspecified

252.01  Primary hyperparathyroidism

Hyperplasia of parathyroid

252.02  Secondary hyperparathyroidism, non-renal

Excludes:          secondary hyperparathyroidism (of renal origin) (588.81)

252.08  Other hyperparathyroidism

Tertiary hyperparathyroidism

252.1    Hypoparathyroidism

Parathyroiditis (autoimmune)

Tetany:

parathyroid

parathyroprival

Excludes:          pseudohypoparathyroidism (275.49)

pseudopseudohypoparathyroidism (275.49)

tetany NOS (781.7)

transitory neonatal hypoparathyroidism (775.4)

252.8    Other specified disorders of parathyroid gland

Cyst of parathyroid gland

Hemorrhage of parathyroid gland

252.9    Unspecified disorder of parathyroid gland

253       Disorders of the pituitary gland and its hypothalamic control

Includes:           the listed conditions whether the disorder is in the pituitary or the hypothalamus

Excludes:          Cushing's syndrome (255.0)

253.0    Acromegaly and gigantism

Overproduction of growth hormone

253.1    Other and unspecified anterior pituitary hyperfunction

Forbes-Albright syndrome

Excludes:          overproduction of:

ACTH (255.3)

thyroid-stimulating hormone [TSH] (242.8)

253.2    Panhypopituitarism

Cachexia, pituitary

Necrosis of pituitary (postpartum)

Pituitary insufficiency NOS

Sheehan's syndrome

Simmonds' disease

Excludes:          iatrogenic hypopituitarism (253.7)

253.3    Pituitary dwarfism

Isolated deficiency of (human) growth hormone [HGH]

Lorain-Levi dwarfism

253.4    Other anterior pituitary disorders

Isolated or partial deficiency of an anterior pituitary hormone, other than growth hormone

Prolactin deficiency

253.5    Diabetes insipidus

Vasopressin deficiency

Excludes:          nephrogenic diabetes insipidus (588.1)

253.6    Other disorders of neurohypophysis

Syndrome of inappropriate secretion of antidiuretic hormone [ADH]

Excludes:          ectopic antidiuretic hormone secretion (259.3)

253.7    Iatrogenic pituitary disorders

Hypopituitarism:

hormone-induced

hypophysectomy-induced

postablative

radiotherapy-induced

Use additional E code to identify cause

253.8    Other disorders of the pituitary and other syndromes of diencephalohypophyseal origin

Abscess of pituitary

Adiposogenital dystrophy

Cyst of Rathke's pouch

Fröhlich's syndrome

Excludes:          craniopharyngioma (237.0)

253.9    Unspecified

Dyspituitarism

254       Diseases of thymus gland

Excludes:          aplasia or dysplasia with immunodeficiency (279.2)

hypoplasia with immunodeficiency (279.2)

myasthenia gravis (358.00-358.01)

254.0    Persistent hyperplasia of thymus

Hypertrophy of thymus

254.1    Abscess of thymus

254.8    Other specified diseases of thymus gland

Atrophy of thymus

Cyst of thymus

Excludes:          thymoma (212.6)

254.9    Unspecified disease of thymus gland

255       Disorders of adrenal glands

Includes:           the listed conditions whether the basic disorder is in the adrenals or is pituitary-induced

255.0    Cushing's syndrome

Adrenal hyperplasia due to excess ACTH

Cushing's syndrome:

NOS

iatrogenic

idiopathic

pituitary-dependent

Ectopic ACTH syndrome

Iatrogenic syndrome of excess cortisol

Overproduction of cortisol

Use additional E code to identify cause, if drug-induced

Excludes:          congenital adrenal hyperplasia (255.2)

255.1    Hyperaldosteronism

255.10  Primary aldosteronism

Aldosteronism NOS

Hyperaldosteronism, unspecified

Excludes:          Conn's syndrome (255.12)

255.11  Glucocorticoid-remediable aldosteronism

Familial aldosteronism type I

Excludes:          Conn's syndrome (255.12)

255.12  Conn's syndrome

255.13  Bartter's syndrome

255.14  Other secondary aldosteronism

255.2    Adrenogenital disorders

Adrenogenital syndromes, virilizing or feminizing, whether acquired or associated with congenital adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis

Achard-Thiers syndrome

Congenital adrenal hyperplasia

Female adrenal pseudohermaphroditism

Male:

macrogenitosomia praecox

sexual precocity with adrenal hyperplasia

Virilization (female) (suprarenal)

Excludes:          adrenal hyperplasia due to excess ACTH (255.0)

isosexual virilization (256.4)

255.3    Other corticoadrenal overactivity

Acquired benign adrenal androgenic overactivity

Overproduction of ACTH

255.4    Corticoadrenal insufficiency

Addisonian crisis

Addison's disease NOS

Adrenal:

atrophy (autoimmune)

calcification

crisis

hemorrhage

infarction

insufficiency NOS

Excludes:          tuberculous Addison's disease (017.6)

255.5    Other adrenal hypofunction

Adrenal medullary insufficiency

Excludes:          Waterhouse-Friderichsen syndrome (meningococcal) (036.3)

255.6    Medulloadrenal hyperfunction

Catecholamine secretion by pheochromocytoma

255.8    Other specified disorders of adrenal glands

Abnormality of cortisol-binding globulin

255.9    Unspecified disorder of adrenal glands

256       Ovarian dysfunction

256.0    Hyperestrogenism

256.1    Other ovarian hyperfunction

Hypersecretion of ovarian androgens

256.2    Postablative ovarian failure

Ovarian failure:

iatrogenic

postirradiation

postsurgical

Use additional code for states associated with artificial menopause (627.4)

Excludes:          acquired absence of ovary (V45.77)

asymptomatic age-related (natural) postmenopausal status (V49.81)

256.3    Other ovarian failure

Use additional code for states associated with natural menopause (627.2)

Excludes:          asymptomatic age-related (natural) postmenopausal status (V49.81)

256.31  Premature menopause

256.39  Other ovarian failure

Delayed menarche

Ovarian hypofunction

Primary ovarian failure NOS

256.4    Polycystic ovaries

Isosexual virilization Stein-Leventhal syndrome

256.8    Other ovarian dysfunction

256.9    Unspecified ovarian dysfunction

257       Testicular dysfunction

257.0    Testicular hyperfunction

Hypersecretion of testicular hormones

257.1    Postablative testicular hypofunction

Testicular hypofunction:

iatrogenic

postirradiation

postsurgical

257.2    Other testicular hypofunction

Defective biosynthesis of testicular androgen

Eunuchoidism:

NOS

hypogonadotropic

Failure:

Leydig's cell, adult

seminiferous tubule, adult

Testicular hypogonadism

Excludes:          azoospermia (606.0)

257.8    Other testicular dysfunction

Excludes:          androgen insensitivity syndrome (259.5)

257.9    Unspecified testicular dysfunction

258       Polyglandular dysfunction and related disorders

258.0    Polyglandular activity in multiple endocrine adenomatosis

Wermer's syndrome

258.1    Other combinations of endocrine dysfunction

Lloyd's syndrome

Schmidt's syndrome

258.8    Other specified polyglandular dysfunction

258.9    Polyglandular dysfunction, unspecified

259       Other endocrine disorders

259.0    Delay in sexual development and puberty, not elsewhere classified

Delayed puberty

259.1    Precocious sexual development and puberty, not elsewhere classified

Sexual precocity:

NOS

constitutional

cryptogenic

idiopathic

259.2    Carcinoid syndrome

Hormone secretion by carcinoid tumors

259.3    Ectopic hormone secretion, not elsewhere classified

Ectopic:

antidiuretic hormone secretion [ADH]

hyperparathyroidism

Excludes:          ectopic ACTH syndrome (255.0)

259.4    Dwarfism, not elsewhere classified

Dwarfism:

NOS

constitutional

Excludes:          dwarfism:

achondroplastic (756.4)

intrauterine (759.7)

nutritional (263.2)

pituitary (253.3)

renal (588.0)

progeria (259.8)

259.5    Androgen insensitivity syndrome

Partial androgen insensitivity

Reifenstein syndrome

259.8    Other specified endocrine disorders

Pineal gland dysfunction

Progeria

Werner's syndrome

259.9    Unspecified endocrine disorder

Disturbance:

endocrine NOS

hormone NOS

Infantilism NOS

NUTRITIONAL DEFICIENCIES (260-269)

Excludes:         deficiency anemias (280.0-281.9)

260       Kwashiorkor

Nutritional edema with dyspigmentation of skin and hair

261       Nutritional marasmus

Nutritional atrophy

Severe calorie deficiency

Severe malnutrition NOS

262       Other severe protein-calorie malnutrition

Nutritional edema without mention of dyspigmentation of skin and hair

263       Other and unspecified protein-calorie malnutrition

263.0    Malnutrition of moderate degree

263.1    Malnutrition of mild degree

263.2    Arrested development following protein-calorie malnutrition

Nutritional dwarfism

Physical retardation due to malnutrition

263.8    Other protein-calorie malnutrition

263.9    Unspecified protein-calorie malnutrition

Dystrophy due to malnutrition

Malnutrition (calorie) NOS

Excludes:          nutritional deficiency NOS (269.9)

264       Vitamin A deficiency

264.0    With conjunctival xerosis

264.1    With conjunctival xerosis and Bitot's spot

Bitot's spot in the young child

264.2    With corneal xerosis

264.3    With corneal ulceration and xerosis

264.4    With keratomalacia

264.5    With night blindness

264.6    With xerophthalmic scars of cornea

264.7    Other ocular manifestations of vitamin A deficiency

Xerophthalmia due to vitamin A deficiency

264.8    Other manifestations of vitamin A deficiency

Follicular keratosis due to vitamin A deficiency

Xeroderma due to vitamin A deficiency

264.9    Unspecified vitamin A deficiency

Hypovitaminosis A NOS

265       Thiamine and niacin deficiency states

265.0    Beriberi

265.1    Other and unspecified manifestations of thiamine deficiency

Other vitamin B1 deficiency states

265.2    Pellagra

Deficiency:

niacin (-tryptophan)

nicotinamide

nicotinic acid

vitamin PP

Pellagra (alcoholic)

266       Deficiency of B-complex components

266.0    Ariboflavinosis

Riboflavin [vitamin B2] deficiency

266.1    Vitamin B6 deficiency

Deficiency:

pyridoxal

pyridoxamine

pyridoxine

Vitamin B6 deficiency syndrome

Excludes:          vitamin B6-responsive sideroblastic anemia (285.0)

266.2    Other B-complex deficiencies

Deficiency:

cyanocobalamin

folic acid

vitamin B12

Excludes:          combined system disease with anemia (281.0-281.1)

deficiency anemias (281.0-281.9)

subacute degeneration of spinal cord with anemia (281.0-281.1)

266.9    Unspecified vitamin B deficiency

267       Ascorbic acid deficiency

Deficiency of vitamin C

Scurvy

Excludes:          scorbutic anemia (281.8)

268       Vitamin D deficiency

Excludes:          vitamin D-resistant:

osteomalacia (275.3)

rickets (275.3)

268.0    Rickets, active

Excludes:          celiac rickets (579.0)

renal rickets (588.0)

268.1    Rickets, late effect

Any condition specified as due to rickets and stated to be a late effect or sequela of rickets

Use additional code to identify the nature of late effect

268.2    Osteomalacia, unspecified

268.9    Unspecified vitamin D deficiency

Avitaminosis D

269       Other nutritional deficiencies

269.0    Deficiency of vitamin K

Excludes:          deficiency of coagulation factor due to vitamin K deficiency (286.7)

vitamin K deficiency of newborn (776.0)

269.1    Deficiency of other vitamins

Deficiency:

vitamin E

vitamin P

269.2    Unspecified vitamin deficiency

Multiple vitamin deficiency NOS

269.3    Mineral deficiency, not elsewhere classified

Deficiency:

calcium, dietary

iodine

Excludes:          deficiency:

calcium NOS (275.40)

potassium (276.8)

sodium (276.1)

269.8    Other nutritional deficiency

Excludes:          adult failure to thrive (783.7)

failure to thrive in childhood (783.41)

feeding problems (783.3)

newborn (779.3)

269.9    Unspecified nutritional deficiency

OTHER METABOLIC AND IMMUNITY DISORDERS (270-279)

Use additional code to identify any associated mental retardation

270       Disorders of amino-acid transport and metabolism

Excludes:          abnormal findings without manifest disease (790.0-796.9)

disorders of purine and pyrimidine metabolism (277.1-277.2)

gout (274.0-274.9)

270.0    Disturbances of amino-acid transport

Cystinosis

Cystinuria

Fanconi (-de Toni) (-Debré) syndrome

Glycinuria (renal)

Hartnup disease

270.1    Phenylketonuria [PKU]

Hyperphenylalaninemia

270.2    Other disturbances of aromatic amino-acid metabolism

Albinism

Alkaptonuria

Alkaptonuric ochronosis

Disturbances of metabolism of tyrosine and tryptophan

Homogentisic acid defects

Hydroxykynureninuria

Hypertyrosinemia

Indicanuria

Kynureninase defects

Oasthouse urine disease

Ochronosis

Tyrosinosis

Tyrosinuria

Waardenburg syndrome

Excludes:          vitamin B6-deficiency syndrome (266.1)

270.3    Disturbances of branched-chain amino-acid metabolism

Disturbances of metabolism of leucine, isoleucine, and valine

Hypervalinemia

Intermittent branched-chain ketonuria

Leucine-induced hypoglycemia

Leucinosis

Maple syrup urine disease

270.4    Disturbances of sulphur-bearing amino-acid metabolism

Cystathioninemia

Cystathioninuria

Disturbances of metabolism of methionine, homocystine, and cystathionine

Homocystinuria

Hypermethioninemia

Methioninemia

270.5    Disturbances of histidine metabolism

Carnosinemia

Histidinemia

Hyperhistidinemia

Imidazole aminoaciduria

270.6    Disorders of urea cycle metabolism

Argininosuccinic aciduria

Citrullinemia

Disorders of metabolism of ornithine, citrulline, argininosuccinic acid, arginine, and ammonia

Hyperammonemia

Hyperornithinemia

270.7    Other disturbances of straight-chain amino-acid metabolism

Glucoglycinuria

Glycinemia (with methylmalonic acidemia)

Hyperglycinemia

Hyperlysinemia

Pipecolic acidemia

Saccharopinuria

Other disturbances of metabolism of glycine, threonine, serine, glutamine, and lysine

270.8    Other specified disorders of amino-acid metabolism

Alaninemia

Ethanolaminuria

Glycoprolinuria

Hydroxyprolinemia

Hyperprolinemia

Iminoacidopathy

Prolinemia

Prolinuria

Sarcosinemia

270.9    Unspecified disorder of amino-acid metabolism

271       Disorders of carbohydrate transport and metabolism

Excludes:          abnormality of secretion of glucagon (251.4)

diabetes mellitus (250.0-250.9)

hypoglycemia NOS (251.2)

mucopolysaccharidosis (277.5)

271.0    Glycogenosis

Amylopectinosis

Glucose-6-phosphatase deficiency

Glycogen storage disease

McArdle's disease

Pompe's disease

von Gierke's disease

271.1    Galactosemia

Galactose-1-phosphate uridyl transferase deficiency

Galactosuria

271.2    Hereditary fructose intolerance

Essential benign fructosuria

Fructosemia

271.3    Intestinal disaccharidase deficiencies and disaccharide malabsorption

Intolerance or malabsorption (congenital) (of):

glucose-galactose

lactose

sucrose-isomaltose

271.4    Renal glycosuria

Renal diabetes

271.8    Other specified disorders of carbohydrate transport and metabolism

Essential benign pentosuria

Fucosidosis

Glycolic aciduria

Hyperoxaluria (primary)

Mannosidosis

Oxalosis

Xylosuria

Xylulosuria

271.9    Unspecified disorder of carbohydrate transport and metabolism

272       Disorders of lipoid metabolism

Excludes:          localized cerebral lipidoses (330.1)

272.0    Pure hypercholesterolemia

Familial hypercholesterolemia

Fredrickson Type IIa hyperlipoproteinemia

Hyperbetalipoproteinemia

Hyperlipidemia, Group A

Low-density-lipoid-type [LDL] hyperlipoproteinemia

272.1    Pure hyperglyceridemia

Endogenous hyperglyceridemia

Fredrickson Type IV hyperlipoproteinemia

Hyperlipidemia, Group B

Hyperprebetalipoproteinemia

Hypertriglyceridemia, essential

Very-low-density-lipoid-type [VLDL] hyperlipoproteinemia

272.2    Mixed hyperlipidemia

Broad- or floating-betalipoproteinemia

Fredrickson Type IIb or III hyperlipoproteinemia

Hypercholesterolemia with endogenous hyperglyceridemia

Hyperbetalipoproteinemia with prebetalipoproteinemia

Tubo-eruptive xanthoma

Xanthoma tuberosum

272.3    Hyperchylomicronemia

Bürger-Grütz syndrome

Fredrickson type I or V hyperlipoproteinemia

Hyperlipidemia, Group D

Mixed hyperglyceridemia

272.4    Other and unspecified hyperlipidemia

Alpha-lipoproteinemia

Combined hyperlipidemia

Hyperlipidemia NOS

Hyperlipoproteinemia NOS

272.5    Lipoprotein deficiencies

Abetalipoproteinemia

Bassen-Kornzweig syndrome

High-density lipoid deficiency

Hypoalphalipoproteinemia

Hypobetalipoproteinemia (familial)

272.6    Lipodystrophy

Barraquer-Simons disease

Progressive lipodystrophy

Use additional E code to identify cause, if iatrogenic

Excludes:          intestinal lipodystrophy (040.2)

272.7    Lipidoses

Chemically induced lipidosis

Disease:

Anderson's

Fabry's

Gaucher's

I cell [mucolipidosis I]

lipoid storage NOS

Niemann-Pick

pseudo-Hurler's or mucolipidosis III

triglyceride storage, Type I or II

Wolman's or triglyceride storage, Type III

Mucolipidosis II

Primary familial xanthomatosis

Excludes:          cerebral lipidoses (330.1)

Tay-Sachs disease (330.1)

272.8    Other disorders of lipoid metabolism

Hoffa's disease or liposynovitis prepatellaris

Launois-Bensaude's lipomatosis

Lipoid dermatoarthritis

272.9    Unspecified disorder of lipoid metabolism

273       Disorders of plasma protein metabolism

Excludes:          agammaglobulinemia and hypogammaglobulinemia (279.0-279.2)

coagulation defects (286.0-286.9)

hereditary hemolytic anemias (282.0-282.9)

273.0    Polyclonal hypergammaglobulinemia

Hypergammaglobulinemic purpura:

benign primary

Waldenström's

273.1    Monoclonal paraproteinemia

Benign monoclonal hypergammaglobulinemia [BMH]

Monoclonal gammopathy:

NOS

associated with lymphoplasmacytic dyscrasias

benign

Paraproteinemia:

benign (familial)

secondary to malignant or inflammatory disease

273.2    Other paraproteinemias

Cryoglobulinemic:

purpura

vasculitis

Mixed cryoglobulinemia

273.3    Macroglobulinemia

Macroglobulinemia (idiopathic) (primary)

Waldenström's macroglobulinemia

273.4    Alpha-1-antitrypsin deficiency

AAT deficiency

273.8    Other disorders of plasma protein metabolism

Abnormality of transport protein

Bisalbuminemia

273.9    Unspecified disorder of plasma protein metabolism

274       Gout

Excludes:          lead gout (984.0-984.9)

274.0    Gouty arthropathy

274.1    Gouty nephropathy

274.10  Gouty nephropathy, unspecified

274.11  Uric acid nephrolithiasis

274.19  Other

274.8    Gout with other specified manifestations

274.81  Gouty tophi of ear

274.82  Gouty tophi of other sites

Gouty tophi of heart

274.89  Other

Use additional code to identify manifestations, as:

gouty:

iritis (364.11)

neuritis (357.4)

274.9    Gout, unspecified

275       Disorders of mineral metabolism

Excludes:          abnormal findings without manifest disease (790.0-796.9)

275.0    Disorders of iron metabolism

Bronzed diabetes

Hemochromatosis

Pigmentary cirrhosis (of liver)

Excludes:          anemia:

iron deficiency (280.0-280.9)

sideroblastic (285.0)

275.1    Disorders of copper metabolism

Hepatolenticular degeneration

Wilson's disease

275.2    Disorders of magnesium metabolism

Hypermagnesemia

Hypomagnesemia

275.3    Disorders of phosphorus metabolism

Familial hypophosphatemia

Hypophosphatasia

Vitamin D-resistant:

osteomalacia

rickets

275.4    Disorders of calcium metabolism

Excludes:          parathyroid disorders (252.00-252.9)

vitamin D deficiency (268.0-268.9)

275.40  Unspecified disorder of calcium metabolism

275.41  Hypocalcemia

275.42  Hypercalcemia

275.49  Other disorders of calcium metabolism

Nephrocalcinosis

Pseudohypoparathyroidism

Pseudopseudohypoparathyroidism

275.8    Other specified disorders of mineral metabolism

275.9    Unspecified disorder of mineral metabolism

276       Disorders of fluid, electrolyte, and acid-base balance

Excludes:          diabetes insipidus (253.5)

familial periodic paralysis (359.3)

276.0    Hyperosmolality and/or hypernatremia

Sodium [Na] excess

Sodium [Na] overload

276.1    Hyposmolality and/or hyponatremia

Sodium [Na] deficiency

276.2    Acidosis

Acidosis:

NOS

lactic

metabolic

respiratory

Excludes:          diabetic acidosis (250.1)

276.3    Alkalosis

Alkalosis:

NOS

metabolic

respiratory

276.4    Mixed acid-base balance disorder

Hypercapnia with mixed acid-base disorder

276.5    Volume depletion

Excludes:          hypovolemic shock:

postoperative (998.0)

traumatic (958.4)

276.50  Volume depletion, unspecified

276.51  Dehydration

276.52  Hypovolemia

Depletion of volume of plasma

276.6    Fluid overload

Fluid retention

Excludes:          ascites (789.5)

localized edema (782.3)

276.7    Hyperpotassemia

Hyperkalemia

Potassium [K]:

excess

intoxication

overload

276.8    Hypopotassemia

Hypokalemia

Potassium [K] deficiency

276.9    Electrolyte and fluid disorders not elsewhere classified

Electrolyte imbalance

Hyperchloremia

Hypochloremia

Excludes:          electrolyte imbalance:

associated with hyperemesis gravidarum  (643.1)

complicating labor and delivery (669.0)

following abortion and ectopic or molar pregnancy (634-638 with .4, 639.4)

277       Other and unspecified disorders of metabolism

277.0    Cystic fibrosis

Fibrocystic disease of the pancreas

Mucoviscidosis

277.00  Without mention of meconium ileus

Cystic fibrosis NOS

277.01  With meconium ileus

Meconium:

ileus (of newborn)

obstruction of intestine in mucoviscidosis

277.02  With pulmonary manifestations

Cystic fibrosis with pulmonary exacerbation

Use additional code to identify any infectious organism present, such as:

pseudomonas (041.7)

277.03  With gastrointestinal manifestations

Excludes: with meconium ileus (277.01)

277.09  With other manifestations

277.1    Disorders of porphyrin metabolism

Hematoporphyria

Hematoporphyrinuria

Hereditary coproporphyria

Porphyria

Porphyrinuria

Protocoproporphyria

Protoporphyria

Pyrroloporphyria

277.2    Other disorders of purine and pyrimidine metabolism

Hypoxanthine-guanine-phosphoribosyltransferase deficiency [HG-PRT deficiency]

Lesch-Nyhan syndrome

Xanthinuria

Excludes:          gout (274.0-274.9)

orotic aciduric anemia (281.4)

277.3    Amyloidosis

Amyloidosis:

NOS

inherited systemic

nephropathic

neuropathic (Portuguese) (Swiss)

secondary

Benign paroxysmal peritonitis

Familial Mediterranean fever

Hereditary cardiac amyloidosis

277.4    Disorders of bilirubin excretion

Hyperbilirubinemia:

congenital

constitutional

Syndrome:

Crigler-Najjar

Dubin-Johnson

Gilbert's

Rotor's

Excludes:          hyperbilirubinemias specific to the perinatal period (774.0-774.7)

277.5    Mucopolysaccharidosis

Gargoylism

Hunter's syndrome

Hurler's syndrome

Lipochondrodystrophy

Maroteaux-Lamy syndrome

Morquio-Brailsford disease

Osteochondrodystrophy

Sanfilippo's syndrome

Scheie's syndrome

277.6    Other deficiencies of circulating enzymes

Hereditary angioedema

277.7    Dysmetabolic syndrome X

Use additional code for associated manifestation, such as:

cardiovascular disease (414.00-414.07)

obesity (278.00-278.01)

277.8    Other specified disorders of metabolism

277.81  Primary carnitine deficiency

277.82  Carnitine deficiency due to inborn errors of metabolism

277.83  Iatrogenic carnitine deficiency

Carnitine deficiency due to:

Hemodialysis

Valproic acid therapy

277.84  Other secondary carnitine deficiency

277.85  Disorders of fatty acid oxidation

Carnitine palmitoyltransferase deficiencies (CPT1, CPT2)

Glutaric aciduria type II (type IIA, IIB, IIC)

Long chain 3-hydroxyacyl CoA dehydrogenase deficiency (LCHAD)

Long chain/very long chain acyl CoA dehydrogenase deficiency (LCAD, VLCAD)

Medium chain acyl CoA dehydrogenase deficiency (MCAD)

Short chain acyl CoA dehydrogenase deficiency (SCAD)

Excludes:          primary carnitine deficiency (277.81)

277.86  Peroxisomal disorders

Adrenomyeloneuropathy

Neonatal adrenoleukodystrophy

Rhizomelic chrondrodysplasia punctata

X-linked adrenoleukodystrophy

Zellweger syndrome

Excludes: infantile Refsum disease (356.3)

277.87  Disorders of mitochondrial metabolism

Kearns-Sayre syndrome

Mitochondrial Encephalopathy, Lactic Acidosis and Stroke-like episodes  (MELAS syndrome)

Mitochondrial Neurogastrointestinal Encephalopathy syndrome (MNGIE)

Myoclonus with Epilepsy and with Ragged Red Fibers  (MERRF syndrome)

Neuropathy, Ataxia and Retinitis Pigmentosa  (NARP syndrome)

Use additional code for associated conditions

Excludes: disorders of pyruvate metabolism (271.8)

Leber's optic atrophy (377.16)

Leigh's subacute necrotizing encephalopathy (330.8)

Reye's syndrome (331.81)

277.89  Other specified disorders of metabolism

Hand-Schüller-Christian disease

Histiocytosis (acute) (chronic)

Histiocytosis X (chronic)

Excludes:          histiocytosis:

acute differentiated progressive (202.5)

X, acute (progressive) (202.5)

277.9    Unspecified disorder of metabolism

Enzymopathy NOS

278       Overweight, obesity and other hyperalimentation

Excludes:          hyperalimentation NOS (783.6)

poisoning by vitamins NOS (963.5)

polyphagia (783.6)

278.0    Overweight and obesity

Excludes:          adiposogenital dystrophy (253.8)

obesity of endocrine origin NOS (259.9)

Use additional code to identify Body Mass Index (BMI) if known (V85.21-V85.4)

278.00  Obesity, unspecified

Obesity NOS

278.01  Morbid obesity

Severe obesity

278.02  Overweight

278.1    Localized adiposity

Fat pad

278.2    Hypervitaminosis A

278.3    Hypercarotinemia

278.4    Hypervitaminosis D

278.8    Other hyperalimentation

279       Disorders involving the immune mechanism

279.0    Deficiency of humoral immunity

279.00  Hypogammaglobulinemia, unspecified

Agammaglobulinemia NOS

279.01  Selective IgA immunodeficiency

279.02  Selective IgM immunodeficiency

279.03  Other selective immunoglobulin deficiencies

Selective deficiency of IgG

279.04  Congenital hypogammaglobulinemia

Agammaglobulinemia:

Bruton's type

X-linked

279.05  Immunodeficiency with increased IgM

Immunodeficiency with hyper-IgM:

autosomal recessive

X-linked

279.06  Common variable immunodeficiency

Dysgammaglobulinemia (acquired) (congenital) (primary)

Hypogammaglobulinemia:

acquired primary

congenital non-sex-linked

sporadic

279.09  Other

Transient hypogammaglobulinemia of infancy

279.1    Deficiency of cell-mediated immunity

279.10  Immunodeficiency with predominant T-cell defect, unspecified

279.11  DiGeorge's syndrome

Pharyngeal pouch syndrome

Thymic hypoplasia

279.12  Wiskott-Aldrich syndrome

279.13  Nezelof's syndrome

Cellular immunodeficiency with abnormal immunoglobulin deficiency

279.19  Other

Excludes:          ataxia-telangiectasia (334.8)

279.2    Combined immunity deficiency

Agammaglobulinemia:

autosomal recessive

Swiss-type

X-linked recessive

Severe combined immunodeficiency [SCID]

Thymic:

alymphoplasia

aplasia or dysplasia with immunodeficiency

Excludes:          thymic hypoplasia (279.11)

279.3    Unspecified immunity deficiency

279.4    Autoimmune disease, not elsewhere classified

Autoimmune disease NOS

Excludes:          transplant failure or rejection (996.80-996.89)

279.8    Other specified disorders involving the immune mechanism

Single complement [C1-C9] deficiency or dysfunction

279.9    Unspecified disorder of immune mechanism

4. DISEASES OF THE BLOOD AND BLOOD-FORMING ORGANS (280-289) back to top

280       Iron deficiency anemias

Includes:           anemia:

asiderotic

hypochromic-microcytic

sideropenic

Excludes:          familial microcytic anemia (282.49)

280.0    Secondary to blood loss (chronic)

Normocytic anemia due to blood loss

Excludes:          acute posthemorrhagic anemia (285.1)

280.1    Secondary to inadequate dietary iron intake

280.8    Other specified iron deficiency anemias

Paterson-Kelly syndrome

Plummer-Vinson syndrome

Sideropenic dysphagia

280.9    Iron deficiency anemia, unspecified

Anemia:

achlorhydric

chlorotic

idiopathic hypochromic

iron [Fe] deficiency NOS

281       Other deficiency anemias

281.0    Pernicious anemia

Anemia:

Addison's

Biermer's

congenital pernicious

Congenital intrinsic factor [Castle's] deficiency

Excludes:          combined system disease without mention of anemia (266.2)

subacute degeneration of spinal cord without mention of anemia (266.2)

281.1    Other vitamin B12 deficiency anemia

Anemia:

vegan's

vitamin B12 deficiency (dietary)

due to selective vitamin B12 malabsorption with proteinuria

Syndrome:

Imerslund's

Imerslund-Gräsbeck

Excludes:          combined system disease without mention of anemia (266.2)

subacute degeneration of spinal cord without mention of anemia (266.2)

281.2    Folate-deficiency anemia

Congenital folate malabsorption

Folate or folic acid deficiency anemia:

NOS

dietary

drug-induced

Goat's milk anemia

Nutritional megaloblastic anemia (of infancy)

Use additional E code to identify drug

281.3    Other specified megaloblastic anemias, not elsewhere classified

Combined B12 and folate-deficiency anemia

Excludes:          refractory megaloblastic anemia (238.7)

281.4    Protein-deficiency anemia

Amino-acid-deficiency anemia

281.8    Anemia associated with other specified nutritional deficiency

Scorbutic anemia

281.9    Unspecified deficiency anemia

Anemia:

dimorphic

macrocytic

megaloblastic NOS

nutritional NOS

simple chronic

282       Hereditary hemolytic anemias

282.0    Hereditary spherocytosis

Acholuric (familial) jaundice

Congenital hemolytic anemia (spherocytic)

Congenital spherocytosis

Minkowski-Chauffard syndrome

Spherocytosis (familial)

Excludes:          hemolytic anemia of newborn (773.0-773.5)

282.1    Hereditary elliptocytosis

Elliptocytosis (congenital)

Ovalocytosis (congenital) (hereditary)

282.2    Anemias due to disorders of glutathione metabolism

Anemia:

6-phosphogluconic dehydrogenase deficiency

enzyme deficiency, drug-induced

erythrocytic glutathione deficiency

glucose-6-phosphate dehydrogenase [G-6-PD] deficiency

glutathione-reductase deficiency

hemolytic nonspherocytic (hereditary), type I

Disorder of pentose phosphate pathway

Favism

282.3    Other hemolytic anemias due to enzyme deficiency

Anemia:

hemolytic nonspherocytic (hereditary), type II

hexokinase deficiency

pyruvate kinase [PK] deficiency

triosephosphate isomerase deficiency

282.4    Thalassemias

Excludes:          sickle-cell:

disease (282.60-282.69)

trait (282.5)

282.41  Sickle-cell thalassemia without crisis

Sickle-cell thalassemia NOS

Thalassemia Hb-S disease without crisis

282.42  Sickle-cell thalassemia with crisis

Sickle-cell thalassemia with vaso-occlusive pain

Thalassemia Hb-S disease with crisis

Use additional code for type of crisis, such as:

Acute chest syndrome (517.3)

Splenic sequestration (289.52)

282.49  Other thalassemia

Cooley's anemia

Hb-Bart's disease

Hereditary leptocytosis

Mediterranean anemia (with other hemoglobinopathy)

Microdrepanocytosis

Thalassemia (alpha) (beta) (intermedia) (major) (minima) (minor) (mixed) (trait) (with other hemoglobinopathy)

Thalassemia NOS

282.5    Sickle-cell trait

Hb-AS genotype

Hemoglobin S [Hb-S] trait

Heterozygous:

hemoglobin S

Hb-S

Excludes:          that with other hemoglobinopathy (282.60-282.69)

that with thalassemia (282.49)

282.6    Sickle-cell disease

Sickle-cell anemia

Excludes:          sickle-cell thalassemia (282.41-282.42)

sickle-cell trait (282.5)

282.60  Sickle-cell disease, unspecified

Sickle-cell anemia NOS

282.61  Hb-SS disease without crisis

282.62  Hb-SS disease with crisis

Hb-SS disease with vaso-occlusive pain

Sickle-cell crisis NOS

Use additional code for type of crisis, such as:

Acute chest syndrome (517.3)

Splenic sequestration (289.52)

282.63  Sickle-cell/Hb-C disease without crisis

Hb-S/Hb-C disease without crisis

282.64  Sickle-cell/HB-C disease with crisis

Hb-S/Hb-C disease with crisis

Sickle-cell/Hb-C disease with vaso-occlusive pain

Use additional code for types of crisis, such as:

Acute chest syndrome (517.3)

Splenic sequestration (289.52)

282.68  Other sickle-cell disease without crisis

Hb-S/Hb-D disease without crisis

Hb-S/Hb-E disease without crisis

Sickle-cell/Hb-D disease without crisis

Sickle-cell/Hb-E disease without crisis

282.69  Other sickle-cell disease with crisis

Hb-S/Hb-D disease with crisis

Hb-S/Hb-E disease with crisis

Sickle-cell/Hb-D disease with crisis

Sickle-cell/Hb-E disease with crisis

Other sickle-cell disease with vaso-occlusive pain

Use additional code for type of crisis, such as:

Acute chest syndrome (517.3)

Splenic sequestration (289.52)

282.7    Other hemoglobinopathies

Abnormal hemoglobin NOS

Congenital Heinz-body anemia

Disease:

hemoglobin C [Hb-C]

hemoglobin D [Hb-D]

hemoglobin E [Hb-E]

hemoglobin Zurich [Hb-Zurich]

Hemoglobinopathy NOS

Hereditary persistence of fetal hemoglobin [HPFH]

Unstable hemoglobin hemolytic disease

Excludes:          familial polycythemia (289.6)

hemoglobin M [Hb-M] disease (289.7)

high-oxygen-affinity hemoglobin (289.0)

282.8    Other specified hereditary hemolytic anemias

Stomatocytosis

282.9    Hereditary hemolytic anemia, unspecified

Hereditary hemolytic anemia NOS

283       Acquired hemolytic anemias

283.0    Autoimmune hemolytic anemias

Autoimmune hemolytic disease (cold type) (warm type)

Chronic cold hemagglutinin disease

Cold agglutinin disease or hemoglobinuria

Hemolytic anemia:

cold type (secondary) (symptomatic)

drug-induced

warm type (secondary) (symptomatic)

Use additional E code to identify cause,  if drug-induced

Excludes:          Evans' syndrome (287.32)

hemolytic disease of newborn (773.0-773.5)

283.1    Non-autoimmune hemolytic anemias

283.10  Non-autoimmune hemolytic anemia, unspecified

283.11  Hemolytic-uremic syndrome

283.19  Other non-autoimmune hemolytic anemias

Hemolytic anemia:

mechanical

microangiopathic

toxic

Use additional E code to identify cause

283.2    Hemoglobinuria due to hemolysis from external causes

Acute intravascular hemolysis

Hemoglobinuria:

from exertion

march

paroxysmal (cold) (nocturnal)

due to other hemolysis

Marchiafava-Micheli syndrome

Use additional E code to identify cause

283.9    Acquired hemolytic anemia, unspecified

Acquired hemolytic anemia NOS

Chronic idiopathic hemolytic anemia

284       Aplastic anemia

284.0    Constitutional aplastic anemia

Aplasia, (pure) red cell:

congenital

of infants

primary

Blackfan-Diamond syndrome

Familial hypoplastic anemia

Fanconi's anemia

Pancytopenia with malformations

284.8    Other specified aplastic anemias

Aplastic anemia (due to):

chronic systemic disease

drugs

infection

radiation

toxic (paralytic)

Pancytopenia (acquired)

Red cell aplasia (acquired) (adult) (pure) (with thymoma)

Use additional E code to identify cause

284.9    Aplastic anemia, unspecified

Anemia:

aplastic (idiopathic) NOS

aregenerative

hypoplastic NOS

nonregenerative

Medullary hypoplasia

Excludes:          refractory anemia (238.7)

285       Other and unspecified anemias

285.0    Sideroblastic anemia

Anemia:

hypochromic with iron loading

sideroachrestic

sideroblastic:

acquired

congenital

hereditary

primary

secondary (drug-induced) (due to disease)

sex-linked hypochromic

vitamin B6-responsive

Pyridoxine-responsive (hypochromic) anemia

Excludes:          refractory sideroblastic anemia (238.7)

Use additional E code to identify cause, if drug-induced

285.1    Acute posthemorrhagic anemia

Anemia due to acute blood loss

Excludes:          anemia due to chronic blood loss (280.0)

blood loss anemia NOS (280.0)

285.2    Anemia in chronic illness

285.21  Anemia in chronic kidney disease

Anemia in end-stage renal disease

Erythropoietin-resistant anemia (EPO resistant anemia)

285.22  Anemia in neoplastic disease

285.29  Anemia of other chronic illness

285.8    Other specified anemias

Anemia:

dyserythropoietic (congenital)

dyshematopoietic (congenital)

leukoerythroblastic

von Jaksch's

Infantile pseudoleukemia

285.9    Anemia, unspecified

Anemia:

NOS

essential

normocytic, not due to blood loss

profound

progressive

secondary

Oligocythemia

Excludes:          anemia (due to):

blood loss:

acute (285.1)

chronic or unspecified (280.0)

iron deficiency (280.0-280.9)

286       Coagulation defects

286.0    Congenital factor VIII disorder

Antihemophilic globulin [AHG] deficiency

Factor VIII (functional) deficiency

Hemophilia:

NOS

A

classical

familial

hereditary

Subhemophilia

Excludes:          factor VIII deficiency with vascular defect (286.4)

286.1    Congenital factor IX disorder

Christmas disease

Deficiency:

factor IX (functional)

plasma thromboplastin component [PTC]

Hemophilia B

286.2    Congenital factor XI deficiency

Hemophilia C

Plasma thromboplastin antecedent [PTA] deficiency

Rosenthal's disease

286.3    Congenital deficiency of other clotting factors

Congenital afibrinogenemia

Deficiency:

AC globulin

factor:

I [fibrinogen]

II [prothrombin]

V [labile]

VII [stable]

X [Stuart-Prower]

XII [Hageman]

XIII [fibrin stabilizing]

Laki-Lorand factor

proaccelerin

Disease:

Owren's

Stuart-Prower

Dysfibrinogenemia (congenital)

Dysprothrombinemia (constitutional)

Hypoproconvertinemia

Hypoprothrombinemia (hereditary)

Parahemophilia

286.4    von Willebrand's disease

Angiohemophilia (A) (B)

Constitutional thrombopathy

Factor VIII deficiency with vascular defect

Pseudohemophilia type B

Vascular hemophilia

von Willebrand's (-Jürgens') disease

Excludes:          factor VIII deficiency:

NOS (286.0)

with functional defect (286.0)

hereditary capillary fragility (287.8)

286.5    Hemorrhagic disorder due to intrinsic circulating anticoagulants

Antithrombinemia

Antithromboplastinemia

Antithromboplastino-genemia

Hyperheparinemia

Increase in:

anti-VIIIa

anti-IXa

anti-Xa

anti-XIa

antithrombin

Secondary hemophilia

Systemic lupus erythematosus [SLE] inhibitor

286.6    Defibrination syndrome

Afibrinogenemia, acquired

Consumption coagulopathy

Diffuse or disseminated intravascular coagulation [DIC syndrome]

Fibrinolytic hemorrhage, acquired

Hemorrhagic fibrinogenolysis

Pathologic fibrinolysis

Purpura:

fibrinolytic

fulminans

Excludes:          that complicating:

abortion (634-638 with .1, 639.1)

pregnancy or the puerperium (641.3, 666.3)

disseminated intravascular coagulation in newborn (776.2)

286.7    Acquired coagulation factor deficiency

Deficiency of coagulation factor due to:

liver disease

vitamin K deficiency

Hypoprothrombinemia, acquired

Excludes:          vitamin K deficiency of newborn (776.0)

Use additional E-code to identify cause, if drug-induced

286.9    Other and unspecified coagulation defects

Defective coagulation NOS

Deficiency, coagulation factor NOS

Delay, coagulation

Disorder:

coagulation

hemostasis

Excludes:          abnormal coagulation profile (790.92)

hemorrhagic disease of newborn (776.0)

that complicating:

abortion (634-638 with .1, 639.1)

pregnancy or the puerperium (641.3, 666.3)

287       Purpura and other hemorrhagic conditions

Excludes:          hemorrhagic thrombocythemia (238.7)

purpura fulminans (286.6)

287.0    Allergic purpura

Peliosis rheumatica

Purpura:

anaphylactoid

autoimmune

Henoch's

nonthrombocytopenic:

hemorrhagic

idiopathic

rheumatica

Schönlein-Henoch

vascular

Vasculitis, allergic

Excludes:          hemorrhagic purpura (287.39)

purpura annularis telangiectodes (709.1)

287.1    Qualitative platelet defects

Thrombasthenia (hemorrhagic) (hereditary)

Thrombocytasthenia

Thrombocytopathy (dystrophic)

Thrombopathy (Bernard-Soulier)

Excludes:          von Willebrand's disease (286.4)

287.2    Other nonthrombocytopenic purpuras

Purpura:

NOS

senile

simplex

287.3    Primary thrombocytopenia

Excludes:          thrombotic thrombocytopenic purpura (446.6)

transient thrombocytopenia of newborn (776.1)

287.30  Primary thrombocytopenia unspecified

Megakaryocytic hypoplasia

287.31  Immune thrombocytopenic purpura

Idiopathic thrombocytopenic purpura

Tidal platelet dysgenesis

287.32  Evans' syndrome

287.33  Congenital and hereditary thrombocytopenic purpura

Congenital and hereditary thrombocytopenia

Thrombocytopenia with absent radii (TAR) syndrome

Excludes:          Wiskott-Aldrich syndrome (279.12)

287.39  Other primary thrombocytopenia

287.4    Secondary thrombocytopenia

Posttransfusion purpura

Thrombocytopenia (due to):

dilutional

drugs

extracorporeal circulation of blood

massive blood transfusion

platelet alloimmunization

Use additional E code to identify cause

Excludes:          transient thrombocytopenia of newborn (776.1)

287.5    Thrombocytopenia, unspecified

287.8    Other specified hemorrhagic conditions

Capillary fragility (hereditary)

Vascular pseudohemophilia

287.9    Unspecified hemorrhagic conditions

Hemorrhagic diathesis (familial)

288       Diseases of white blood cells

Excludes:          leukemia (204.0-208.9)

288.0    Agranulocytosis

Infantile genetic agranulocytosis

Kostmann's syndrome

Neutropenia:

NOS

cyclic

drug-induced

immune

periodic

toxic

Neutropenic splenomegaly

Use additional E code to identify drug or other cause

Excludes:          transitory neonatal neutropenia (776.7)

288.1    Functional disorders of polymorphonuclear neutrophils

Chronic (childhood) granulomatous disease

Congenital dysphagocytosis

Job's syndrome

Lipochrome histiocytosis (familial)

Progressive septic granulomatosis

288.2    Genetic anomalies of leukocytes

Anomaly (granulation) (granulocyte) or syndrome:

Alder's (-Reilly)

Chédiak-Steinbrinck (-Higashi)

Jordan's

May-Hegglin

Pelger-Huet

Hereditary:

hypersegmentation

hyposegmentation

leukomelanopathy

288.3    Eosinophilia

Eosinophilia

allergic

hereditary

idiopathic

secondary

Eosinophilic leukocytosis

Excludes:          Löffler's syndrome (518.3)

pulmonary eosinophilia (518.3)

288.8    Other specified disease of white blood cells

Leukemoid reaction

lymphocytic

monocytic

myelocytic

Leukocytosis

Lymphocytopenia

Lymphocytosis (symptomatic)

Lymphopenia

Monocytosis (symptomatic)

Plasmacytosis

Excludes:          immunity disorders (279.0-279.9)

288.9    Unspecified disease of white blood cells

289       Other diseases of blood and blood-forming organs

289.0    Polycythemia, secondary

High-oxygen-affinity hemoglobin

Polycythemia:

acquired

benign

due to:

fall in plasma volume

high altitude

emotional

erythropoietin

hypoxemic

nephrogenous

relative

spurious

stress

Excludes:          polycythemia:

neonatal (776.4)

primary (238.4)

vera (238.4)

289.1    Chronic lymphadenitis

Chronic:

adenitis any lymph node, except mesenteric

lymphadenitis any lymph node, except mesenteric

Excludes:          acute lymphadenitis (683)

mesenteric (289.2)

enlarged glands NOS (785.6)

289.2    Nonspecific mesenteric lymphadenitis

Mesenteric lymphadenitis (acute) (chronic)

289.3    Lymphadenitis, unspecified, except mesenteric

289.4    Hypersplenism

"Big spleen" syndrome

Dyssplenism

Hypersplenia

Excludes:          primary splenic neutropenia (288.0)

289.5    Other diseases of spleen

289.50  Disease of spleen, unspecified

289.51  Chronic congestive splenomegaly

289.52  Splenic sequestration

Code first sickle-cell disease in crisis (282.42, 282.62, 282.64, 282.69)

289.59  Other

Lien migrans

Perisplenitis

Splenic:

abscess

atrophy

cyst

fibrosis

infarction

rupture, nontraumatic

Splenitis

Wandering spleen

Excludes:          bilharzial splenic fibrosis (120.0-120.9)

hepatolienal fibrosis (571.5)

splenomegaly NOS (789.2)

289.6    Familial polycythemia

Familial:

benign polycythemia

erythrocytosis

289.7    Methemoglobinemia

Congenital NADH [DPNH]-methemoglobin-reductase deficiency

Hemoglobin M [Hb-M] disease

Methemoglobinemia:

NOS

acquired (with sulfhemoglobinemia)

hereditary

toxic

Stokvis' disease

Sulfhemoglobinemia

Use additional E code to identify cause

289.8    Other specified diseases of blood and blood-forming organs

289.81  Primary hypercoagulable state

Activated protein C resistance

Antithrombin III deficiency

Factor V Leiden mutation

Lupus anticoagulant

Protein C deficiency

Protein S deficiency

Prothrombin gene mutation

289.82  Secondary hypercoagulable state

289.89  Other specified diseases of blood and blood-forming organs

Hypergammaglobulinemia

Myelofibrosis

Pseudocholinesterase deficiency

289.9    Unspecified diseases of blood and blood-forming organs

Blood dyscrasia NOS

Erythroid hyperplasia

5. MENTAL DISORDERS (290-319) back to top

PSYCHOSES (290-299)

Excludes:         mental retardation (317-319)

ORGANIC PSYCHOTIC CONDITIONS (290-294)

Includes:          psychotic organic brain syndrome

Excludes:         nonpsychotic syndromes of organic etiology (310.0-310.9)

psychoses classifiable to 295-298 and without impairment of orientation, comprehension, calculation, learning capacity, and judgement, but associated with physical disease, injury, or condition affecting the brain [e.g., following childbirth] (295.0-298.8)

290       Dementias

Code first the associated neurological condition

Excludes:          dementia due to alcohol (291.0-291.2)

dementia due to drugs (292.82)

dementia not classified as senile, presenile, or arteriosclerotic (294.10-294.11)

psychoses classifiable to 295-298 occurring in the senium without dementia or delirium (295.0-298.8)

senility with mental changes of nonpsychotic severity (310.1)

transient organic psychotic conditions (293.0-293.9)

290.0    Senile dementia, uncomplicated

Senile dementia:

NOS

simple type

Excludes:          mild memory disturbances, not amounting to dementia, associated with senile brain disease (310.1)

senile dementia with:

delirium or confusion (290.3)

delusional [paranoid] features (290.20)

depressive features (290.21)

290.1    Presenile dementia

Brain syndrome with presenile brain disease

Excludes:          arteriosclerotic dementia (290.40-290.43)

dementia associated with other cerebral conditions (294.10-294.11)

290.10  Presenile dementia, uncomplicated

Presenile dementia:

NOS

simple type

290.11  Presenile dementia with delirium

Presenile dementia with acute confusional state

290.12  Presenile dementia with delusional features

Presenile dementia, paranoid type

290.13  Presenile dementia with depressive features

Presenile dementia, depressed type

290.2    Senile dementia with delusional or depressive features

Excludes:          senile dementia:

NOS (290.0)

with delirium and/or confusion (290.3)

290.20  Senile dementia with delusional features

Senile dementia, paranoid type

Senile psychosis NOS

290.21  Senile dementia with depressive features

290.3    Senile dementia with delirium

Senile dementia with acute confusional state

Excludes:          senile:

dementia NOS (290.0)

psychosis NOS (290.20)

290.4    Vascular dementia

Multi-infarct dementia or psychosis

Use additional code to identify cerebral atherosclerosis (437.0)

Excludes:          suspected cases with no clear evidence of arteriosclerosis (290.9)

290.40  Vascular dementia, uncomplicated

Arteriosclerotic dementia:

NOS

simple type

290.41  Vascular dementia with delirium

Arteriosclerotic dementia with acute confusional state

290.42  Vascular dementia with delusions

Arteriosclerotic dementia, paranoid type

290.43  Vascular dementia with depressed mood

Arteriosclerotic dementia, depressed type

290.8    Other specified senile psychotic conditions

Presbyophrenic psychosis

290.9    Unspecified senile psychotic condition

291       Alcohol-induced mental disorders

Excludes:          alcoholism without psychosis (303.0-303.9)

291.0    Alcohol withdrawal delirium

Alcoholic delirium

Delirium tremens

Excludes:          alcohol withdrawal (291.81)

291.1    Alcohol-induced persisting amnestic disorder

Alcoholic polyneuritic psychosis

Korsakoff's psychosis, alcoholic

Wernicke-Korsakoff syndrome (alcoholic)

291.2    Alcohol-induced persisting dementia

Alcoholic dementia NOS

Alcoholism associated with dementia NOS

Chronic alcoholic brain syndrome

291.3    Alcohol-induced psychotic disorder with hallucinations

Alcoholic:

hallucinosis (acute)

psychosis with hallucinosis

Excludes:          alcohol withdrawal with delirium (291.0)

schizophrenia (295.0-295.9) and paranoid states (297.0-297.9) taking the form of chronic hallucinosis with clear consciousness in an alcoholic

291.4    Idiosyncratic alcohol intoxication

Pathologic:

alcohol intoxication

drunkenness

Excludes:          acute alcohol intoxication (305.0)

in alcoholism (303.0)

simple drunkenness (305.0)

291.5    Alcohol-induced psychotic disorder with delusions

Alcoholic:

paranoia

psychosis, paranoid type

Excludes:          nonalcoholic paranoid states (297.0-297.9)

schizophrenia, paranoid type (295.3)

291.8    Other specified alcohol-induced mental disorders

291.81  Alcohol withdrawal

Alcohol:

abstinence syndrome or symptoms

withdrawal syndrome or symptoms

Excludes:          alcohol withdrawal:

delirium (291.0)

hallucinosis (291.3)

delirium tremens (291.0)

291.82  Alcohol induced sleep disorders

Alcohol induced circadian rhythm sleep disorders

Alcohol induced hypersomnia

Alcohol induced insomnia

Alcohol induced parasomnia

291.89  Other

Alcohol-induced anxiety disorder

Alcohol-induced mood disorder

Alcohol-induced sexual dysfunction

291.9    Unspecified alcohol-induced mental disorders

Alcoholic:

mania NOS

psychosis NOS

Alcoholism (chronic) with psychosis

Alcohol-related disorder NOS

292       Drug-induced mental disorders

Includes:           organic brain syndrome associated with consumption of drugs

Use additional code for any associated drug dependence (304.0-304.9)

Use additional E code to identify drug

292.0    Drug withdrawal

Drug:

abstinence syndrome or symptoms

withdrawal syndrome or symptoms

292.1    Drug-induced psychotic disorders

292.11  Drug-induced psychotic disorder with delusions

Paranoid state induced by drugs

292.12  Drug-induced psychotic disorder with hallucinations

Hallucinatory state induced by drugs

Excludes:          states following LSD or other hallucinogens, lasting only a few days or less ["bad trips"] (305.3)

292.2    Pathological drug intoxication

Drug reaction resulting in brief psychotic states

NOS

idiosyncratic

pathologic

Excludes:          expected brief psychotic reactions to hallucinogens ["bad trips"] (305.3)

physiological side-effects of drugs (e.g., dystonias)

292.8    Other specified drug-induced mental disorders

292.81  Drug-induced delirium

292.82  Drug-induced persisting dementia

292.83  Drug-induced persisting amnestic disorder

292.84  Drug-induced mood disorder

Depressive state induced by drugs

292.85  Drug induced sleep disorders

Drug induced circadian rhythm sleep disorder

Drug induced hypersomnia

Drug induced insomnia

Drug induced parasomnia

292.89  Other

Drug-induced anxiety disorder

Drug-induced organic personality syndrome

Drug-induced sexual dysfunction

Drug intoxication

292.9    Unspecified drug-induced mental disorder

Drug-related disorder NOS

Organic psychosis NOS due to or associated with drugs

293       Transient mental disorders due to conditions classified elsewhere

Includes:           transient organic mental disorders not associated with alcohol or drugs

Code first the associated physical or neurological condition

Excludes:          confusional state or delirium superimposed on  senile dementia (290.3)

dementia due to:

alcohol (291.0-291.9)

arteriosclerosis (290.40-290.43)

drugs (292.82)

senility (290.0)

293.0    Delirium due to conditions classified elsewhere

Acute:

confusional state

infective psychosis

organic reaction

posttraumatic organic psychosis

psycho-organic syndrome

Acute psychosis associated with endocrine, metabolic, or cerebrovascular disorder

Epileptic:

confusional state

twilight state

293.1    Subacute delirium

Subacute:

confusional state

infective psychosis

organic reaction

posttraumatic organic psychosis

psycho-organic syndrome

psychosis associated with endocrine or metabolic disorder

293.8    Other specified transient mental disorders due to conditions classified elsewhere

293.81  Psychotic disorder with delusions in conditions classified elsewhere

Transient organic psychotic condition, paranoid type

293.82  Psychotic disorder with hallucinations in conditions classified elsewhere

Transient organic psychotic condition, hallucinatory type

293.83  Mood disorder in conditions classified elsewhere

Transient organic psychotic condition, depressive type

293.84  Anxiety disorder in conditions classified elsewhere

293.89  Other

Catatonic disorder in conditions classified elsewhere

293.9    Unspecified transient mental disorder in conditions classified elsewhere

Organic psychosis:

infective NOS

posttraumatic NOS

transient NOS

Psycho-organic syndrome

294       Persistent mental disorders due to conditions classified elsewhere

Includes:           organic psychotic brain syndromes (chronic), not elsewhere classified

294.0    Amnestic disorder in conditions classified elsewhere

Korsakoff's psychosis or syndrome (nonalcoholic)

Code first underlying condition

Excludes: alcoholic:

amnestic syndrome (291.1)

Korsakoff's psychosis (291.1)

294.1    Dementia in conditions classified elsewhere

Dementia of the Alzheimer's type

Code first any underlying physical condition as:

dementia in:

Alzheimer's disease (331.0)

cerebral lipidoses (330.1)

dementia with Lewy bodies (331.82)

dementia with Parkinsonism (331.82)

epilepsy (345.0-345.9)

frontal dementia (331.19)

frontotemporal dementia (331.19)

general paresis [syphilis] (094.1)

hepatolenticular degeneration (275.1)

Huntington's chorea (333.4)

Jakob-Creutzfeldt disease (046.1)

multiple sclerosis (340)

Pick's disease of the brain (331.11)

polyarteritis nodosa (446.0)

syphilis (094.1)

Excludes:          dementia:

arteriosclerotic (290.40-290.43)

presenile (290.10-290.13)

senile (290.0)

epileptic psychosis NOS (294.8)

294.10  Dementia in conditions classified elsewhere without behavioral disturbance

Dementia in conditions classified elsewhere NOS

294.11  Dementia in conditions classified elsewhere with behavioral disturbance

Aggressive behavior

Combative behavior

Violent behavior

Wandering off

294.8    Other persistent mental disorders due to conditions classified elsewhere

Amnestic disorder NOS

Dementia NOS

Epileptic psychosis NOS

Mixed paranoid and affective organic psychotic states

Use additional code for associated epilepsy (345.0-345.9)

Excludes:          mild memory disturbances, not amounting to dementia (310.1)

294.9    Unspecified persistent mental disorders due to conditions classified elsewhere

Cognitive disorder NOS

Organic psychosis (chronic)

OTHER PSYCHOSES (295-299)

Use additional code to identify any associated physical disease, injury, or condition affecting the brain with psychoses classifiable to 295-298

295       Schizophrenic disorders

Includes:           schizophrenia of the types described in 295.0-295.9 occurring in children

Excludes:          childhood type schizophrenia (299.9)

infantile autism (299.0)

The following fifth-digit subclassification is for use with category 295:

0 unspecified

1 subchronic

2 chronic

3 subchronic with acute exacerbation

4 chronic with acute exacerbation

5 in remission

295.0    Simple type

Schizophrenia simplex

Excludes:          latent schizophrenia (295.5)

295.1    Disorganized type

Hebephrenia

Hebephrenic type schizophrenia

295.2    Catatonic type

Catatonic (schizophrenia):

agitation

excitation

excited type

stupor

withdrawn type

Schizophrenic:

catalepsy

catatonia

flexibilitas cerea

295.3    Paranoid type

Paraphrenic schizophrenia

Excludes:          involutional paranoid state (297.2)

paranoia (297.1)

paraphrenia (297.2)

295.4    Schizophreniform disorder

Oneirophrenia

Schizophreniform:

attack

psychosis, confusional type

Excludes:          acute forms of schizophrenia of:

catatonic type (295.2)

hebephrenic type (295.1)

paranoid type (295.3)

simple type (295.0)

undifferentiated type (295.8)

295.5    Latent schizophrenia

Latent schizophrenic reaction

Schizophrenia:

borderline

incipient

prepsychotic

prodromal

pseudoneurotic

pseudopsychopathic

Excludes:          schizoid personality (301.20-301.22)

295.6    Residual type

Chronic undifferentiated schizophrenia

Restzustand (schizophrenic)

Schizophrenic residual state

295.7    Schizoaffective disorder

Cyclic schizophrenia

Mixed schizophrenic and affective psychosis

Schizo-affective psychosis

Schizophreniform psychosis, affective type

295.8    Other specified types of schizophrenia

Acute (undifferentiated) schizophrenia

Atypical schizophrenia

Cenesthopathic schizophrenia

Excludes:          infantile autism (299.0)

295.9    Unspecified schizophrenia

Schizophrenia:

NOS

mixed NOS

undifferentiated NOS

undifferentiated type

Schizophrenic reaction NOS

Schizophreniform psychosis NOS

296       Episodic mood disorders

Includes:           episodic affective disorders

Excludes:          neurotic depression (300.4)

reactive depressive psychosis (298.0)

reactive excitation (298.1)

The following fifth-digit subclassification is for use with categories 296.0-296.6:

0 unspecified

1 mild

2 moderate

3 severe, without mention of psychotic behavior

4 severe, specified as with psychotic behavior

5 in partial or unspecified remission

6 in full remission

296.0    Bipolar I disorder, single manic episode

Hypomania (mild) NOS single episode or unspecified

Hypomanic psychosis single episode or unspecified

Mania (monopolar) NOS single episode or unspecified

Manic-depressive psychosis or reaction, single episode or unspecified:

hypomanic, single episode or unspecified

manic, single episode or unspecified

Excludes:          circular type, if there was a previous attack of depression (296.4)

296.1    Manic disorder, recurrent episode

Any condition classifiable to 296.0, stated to be recurrent

Excludes:          circular type, if there was a previous attack of depression (296.4)

296.2    Major depressive disorder, single episode

Depressive psychosis, single episode or unspecified

Endogenous depression, single episode or unspecified

Involutional melancholia, single episode or unspecified

Manic-depressive psychosis or reaction, depressed type, single episode or unspecified

Monopolar depression, single episode or unspecified

Psychotic depression, single episode or unspecified

Excludes:          circular type, if previous attack was of manic type (296.5)

depression NOS (311)

reactive depression (neurotic) (300.4)

psychotic (298.0)

296.3    Major depressive disorder, recurrent episode

Any condition classifiable to 296.2, stated to be recurrent

Excludes:          circular type, if previous attack was of manic type (296.5)

depression NOS (311)

reactive depression (neurotic) (300.4)

psychotic (298.0)

296.4    Bipolar I disorder, most recent episode (or current) manic

Bipolar disorder, now manic

Manic-depressive psychosis, circular type but currently manic

Excludes:          brief compensatory or rebound mood swings (296.99)

296.5    Bipolar I disorder, most recent episode (or current) depressed

Bipolar disorder, now depressed

Manic-depressive psychosis, circular type but currently depressed

Excludes:          brief compensatory or rebound mood swings (296.99)

296.6    Bipolar I disorder, most recent episode (or current) mixed

Manic-depressive psychosis, circular type, mixed

296.7    Bipolar I disorder, most recent episode (or current) unspecified

Atypical bipolar affective disorder NOS

Manic-depressive psychosis, circular type, current condition not specified as either manic or depressive

296.8    Other and unspecified bipolar disorders

296.80  Bipolar disorder, unspecified

Bipolar disorder NOS

Manic-depressive:

reaction NOS

syndrome NOS

296.81  Atypical manic disorder

296.82  Atypical depressive disorder

296.89  Other

Bipolar II disorder

Manic-depressive psychosis, mixed type

296.9    Other and unspecified episodic mood disorder

Excludes:          psychogenic affective psychoses (298.0-298.8)

296.90  Unspecified episodic mood disorder

Affective psychosis NOS

Melancholia NOS

Mood disorder NOS

296.99  Other specified episodic mood disorder

Mood swings:

brief compensatory

rebound

297       Delusional disorders

Includes:           paranoid disorders

Excludes:          acute paranoid reaction (298.3)

alcoholic jealousy or paranoid state (291.5)

paranoid schizophrenia (295.3)

297.0    Paranoid state, simple

297.1    Delusional disorder

Chronic paranoid psychosis

Sander's disease

Systematized delusions

Excludes:          paranoid personality disorder (301.0)

297.2    Paraphrenia

Involutional paranoid state

Late paraphrenia

Paraphrenia (involutional)

297.3    Shared psychotic disorder

Folie à deux

Induced psychosis or paranoid disorder

297.8    Other specified paranoid states

Paranoia querulans

Sensitiver Beziehungswahn

Excludes:          acute paranoid reaction or state (298.3)

senile paranoid state (290.20)

297.9    Unspecified paranoid state

Paranoid:

disorder NOS

psychosis NOS

reaction NOS

state NOS

298       Other nonorganic psychoses

Includes:           psychotic conditions due to or provoked by:

emotional stress

environmental factors as major part of etiology

298.0    Depressive type psychosis

Psychogenic depressive psychosis

Psychotic reactive depression

Reactive depressive psychosis

Excludes:          manic-depressive psychosis, depressed type (296.2-296.3)

neurotic depression (300.4)

reactive depression NOS (300.4)

298.1    Excitative type psychosis

Acute hysterical psychosis

Psychogenic excitation

Reactive excitation

Excludes:          manic-depressive psychosis, manic type (296.0-296.1)

298.2    Reactive confusion

Psychogenic confusion

Psychogenic twilight state

Excludes:          acute confusional state (293.0)

298.3    Acute paranoid reaction

Acute psychogenic paranoid psychosis

Bouffée délirante

Excludes:          paranoid states (297.0-297.9)

298.4    Psychogenic paranoid psychosis

Protracted reactive paranoid psychosis

298.8    Other and unspecified reactive psychosis

Brief psychotic disorder

Brief reactive psychosis NOS

Hysterical psychosis

Psychogenic psychosis NOS

Psychogenic stupor

Excludes:          acute hysterical psychosis (298.1)

298.9    Unspecified psychosis

Atypical psychosis

Psychosis NOS

Psychotic disorder NOS

299       Pervasive developmental disorders

Excludes:          adult type psychoses occurring in childhood, as:

affective disorders (296.0-296.9)

manic-depressive disorders (296.0-296.9)

schizophrenia (295.0-295.9)

The following fifth-digit subclassification is for use with category 299:

0 current or active state

1 residual state

299.0    Autistic disorder

Childhood autism

Infantile psychosis

Kanner's syndrome

Excludes:          disintegrative psychosis (299.1)

Heller's syndrome (299.1)

schizophrenic syndrome of childhood (299.9)

299.1    Childhood disintegrative disorder

Heller's syndrome

Use additional code to identify any associated neurological disorder

Excludes:          infantile autism (299.0)

schizophrenic syndrome of childhood (299.9)

299.8    Other specified pervasive developmental disorders

Asperger's disorder

Atypical childhood psychosis

Borderline psychosis of childhood

Excludes:          simple stereotypes without psychotic disturbance (307.3)

299.9    Unspecified pervasive developmental disorder

Child psychosis NOS

Pervasive developmental disorder NOS

Schizophrenia, childhood type NOS

Schizophrenic syndrome of childhood NOS

Excludes:          schizophrenia of adult type occurring in childhood (295.0-295.9)

NEUROTIC DISORDERS, PERSONALITY DISORDERS, AND OTHER NONPSYCHOTIC MENTAL DISORDERS (300-316)

300       Anxiety, dissociative and somatoform disorders

300.0    Anxiety states

Excludes:          anxiety in:

acute stress reaction (308.0)

transient adjustment reaction (309.24)

neurasthenia (300.5)

psychophysiological disorders (306.0-306.9)

separation anxiety (309.21)

300.00  Anxiety state, unspecified

Anxiety:

neurosis

reaction

state (neurotic)

Atypical anxiety disorder

300.01  Panic disorder without agoraphobia

Panic:

attack

state

Excludes:          panic disorder with agoraphobia (300.21)

300.02  Generalized anxiety disorder

300.09  Other

300.1    Dissociative, conversion and factitious disorders

Excludes:          adjustment reaction (309.0-309.9)

anorexia nervosa (307.1)

gross stress reaction (308.0-308.9)

hysterical personality (301.50-301.59)

psychophysiologic disorders (306.0-306.9)

300.10  Hysteria, unspecified

300.11  Conversion disorder

Astasia-abasia, hysterical

Conversion hysteria or reaction

Hysterical:

blindness

deafness

paralysis

300.12  Dissociative amnesia

Hysterical amnesia

300.13  Dissociative fugue

Hysterical fugue

300.14  Dissociative identity disorder

300.15  Dissociative disorder or reaction, unspecified

300.16  Factitious disorder with predominantly psychological signs and symptoms

Compensation neurosis

Ganser's syndrome, hysterical

300.19  Other and unspecified factitious illness

Factitious disorder (with combined psychological and physical signs and symptoms) (with predominantly physical signs and symptoms) NOS

Excludes:          multiple operations or hospital addiction syndrome (301.51)

300.2    Phobic disorders

Excludes:          anxiety state not associated with a specific situation or object (300.00-300.09)

obsessional phobias (300.3)

300.20  Phobia, unspecified

Anxiety-hysteria NOS

Phobia NOS

300.21  Agoraphobia with panic disorder

Fear of:

open spaces with panic attacks

streets with panic attacks

travel with panic attacks

Panic disorder with agoraphobia

Excludes:          agoraphobia without panic disorder (300.22)

panic disorder without agoraphobia (300.01)

300.22  Agoraphobia without mention of panic attacks

Any condition classifiable to 300.21 without mention of panic attacks

300.23  Social phobia

Fear of:

eating in public

public speaking

washing in public

300.29  Other isolated or specific phobias

Acrophobia

Animal phobias

Claustrophobia

Fear of crowds

300.3    Obsessive-compulsive disorders

Anancastic neurosis

Compulsive neurosis

Obsessional phobia [any]

Excludes:          obsessive-compulsive symptoms occurring in:

endogenous depression (296.2-296.3)

organic states (e.g., encephalitis) schizophrenia (295.0-295.9)

300.4    Dysthymic disorder

Anxiety depression

Depression with anxiety

Depressive reaction

Neurotic depressive state

Reactive depression

Excludes:          adjustment reaction with depressive symptoms (309.0-309.1)

depression NOS (311)

manic-depressive psychosis, depressed type (296.2-296.3)

reactive depressive psychosis (298.0)

300.5    Neurasthenia

Fatigue neurosis

Nervous debility

Psychogenic:

asthenia

general fatigue

Use additional code to identify any associated physical disorder

Excludes:          anxiety state (300.00-300.09)

neurotic depression (300.4)

psychophysiological disorders (306.0-306.9)

specific nonpsychotic mental disorders following organic brain damage (310.0-310.9)

300.6    Depersonalization disorder

Derealization (neurotic)

Neurotic state with depersonalization episode

Excludes:          depersonalization associated with:

anxiety (300.00-300.09)

depression (300.4)

manic-depressive disorder or psychosis (296.0-296.9)

schizophrenia (295.0-295.9)

300.7    Hypochondriasis

Body dysmorphic disorder

Excludes:          hypochondriasis in:

hysteria (300.10-300.19)

manic-depressive psychosis, depressed type (296.2-296.3)

neurasthenia (300.5)

obsessional disorder (300.3)

schizophrenia (295.0-295.9)

300.8    Somatoform disorders

300.81  Somatization disorder

Briquet's disorder

Severe somatoform disorder

300.82  Undifferentiated somatoform disorder

Atypical somatoform disorder

Somatoform disorder NOS

300.89  Other somatoform disorders

Occupational neurosis, including writers' cramp

Psychasthenia

Psychasthenic neurosis

300.9    Unspecified nonpsychotic mental disorder

Psychoneurosis NOS

301       Personality disorders

Includes:           character neurosis

Use additional code to identify any associated neurosis or psychosis, or physical condition

Excludes:          nonpsychotic personality disorder associated with organic brain syndromes (310.0-310.9)

301.0    Paranoid personality disorder

Fanatic personality

Paranoid personality (disorder)

Paranoid traits

Excludes:          acute paranoid reaction (298.3)

alcoholic paranoia (291.5)

paranoid schizophrenia (295.3)

paranoid states (297.0-297.9)

301.1    Affective personality disorder

Excludes:          affective psychotic disorders (296.0-296.9)

neurasthenia (300.5)

neurotic depression (300.4)

301.10  Affective personality disorder, unspecified

301.11  Chronic hypomanic personality disorder

Chronic hypomanic disorder

Hypomanic personality

301.12  Chronic depressive personality disorder

Chronic depressive disorder

Depressive character or personality

301.13  Cyclothymic disorder

Cycloid personality

Cyclothymia

Cyclothymic personality

301.2    Schizoid personality disorder

Excludes:          schizophrenia (295.0-295.9)

301.20  Schizoid personality disorder, unspecified

301.21  Introverted personality

301.22  Schizotypal personality disorder

301.3    Explosive personality disorder

Aggressive:

personality

reaction

Aggressiveness

Emotional instability (excessive)

Pathological emotionality

Quarrelsomeness

Excludes:          dyssocial personality (301.7)

hysterical neurosis (300.10-300.19)

301.4    Obsessive-compulsive personality disorder

Anancastic personality

Obsessional personality

Excludes:          obsessive-compulsive disorder (300.3)

phobic state (300.20-300.29)

301.5    Histrionic personality disorder

Excludes:          hysterical neurosis (300.10-300.19)

301.50  Histrionic personality disorder, unspecified

Hysterical personality NOS

301.51  Chronic factitious illness with physical symptoms

Hospital addiction syndrome

Multiple operations syndrome

Munchausen syndrome

301.59  Other histrionic personality disorder

Personality:

emotionally unstable

labile

psychoinfantile

301.6    Dependent personality disorder

Asthenic personality

Inadequate personality

Passive personality

Excludes:          neurasthenia (300.5)

passive-aggressive personality (301.84)

301.7    Antisocial personality disorder

Amoral personality

Asocial personality

Dyssocial personality

Personality disorder with predominantly sociopathic or asocial manifestation

Excludes:          disturbance of conduct without specifiable personality disorder (312.0-312.9)

explosive personality (301.3)

301.8    Other personality disorders

301.81  Narcissistic personality disorder

301.82  Avoidant personality disorder

301.83  Borderline personality disorder

301.84  Passive-aggressive personality

301.89  Other

Personality:

eccentric

"haltlose" type

immature

masochistic

psychoneurotic

Excludes:          psychoinfantile personality (301.59)

301.9    Unspecified personality disorder

Pathological personality NOS

Personality disorder NOS

Psychopathic:

constitutional state

personality (disorder)

302       Sexual and gender identity disorders

Excludes:          sexual disorder manifest in:

organic brain syndrome (290.0-294.9, 310.0-310.9)

psychosis (295.0-298.9)

302.0    Ego-dystonic sexual orientation

Ego-dystonic lesbianism

Sexual orientation conflict disorder

Excludes:          homosexual pedophilia (302.2)

302.1    Zoophilia

Bestiality

302.2    Pedophilia

302.3    Transvestic fetishism

Excludes:          trans-sexualism (302.5)

302.4    Exhibitionism

302.5    Trans-sexualism

Excludes:          transvestism (302.3)

302.50  With unspecified sexual history

302.51  With asexual history

302.52  With homosexual history

302.53  With heterosexual history

302.6    Gender identity disorder in children

Feminism in boys

Gender identity disorder NOS

Excludes:          gender identity disorder in adult (302.85)

trans-sexualism (302.50-302.53)

transvestism (302.3)

302.7    Psychosexual dysfunction

Excludes:          decreased sexual desire NOS (799.81)

impotence of organic origin (607.84)

normal transient symptoms from ruptured hymen

transient or occasional failures of erection due to fatigue, anxiety, alcohol, or drugs

302.70  Psychosexual dysfunction, unspecified

Sexual dysfunction NOS

302.71  Hypoactive sexual desire disorder

Excludes:          decreased sexual desire NOS (799.81)

302.72  With inhibited sexual excitement

Female sexual arousal disorder

Frigidity

Impotence

Male erectile disorder

302.73  Female orgasmic disorder

302.74  Male orgasmic disorder

302.75  Premature ejaculation

302.76  Dyspareunia, psychogenic

302.79  With other specified psychosexual dysfunctions

Sexual aversion disorder

302.8    Other specified psychosexual disorders

302.81  Fetishism

302.82  Voyeurism

302.83  Sexual masochism

302.84  Sexual sadism

302.85  Gender identity disorder in adolescents or adults

Excludes: gender identity disorder NOS (302.6)

gender identity disorder in children (302.6)

302.89  Other

Frotteurism

Nymphomania

Satyriasis

302.9    Unspecified psychosexual disorder

Paraphilia NOS

Pathologic sexuality NOS

Sexual deviation NOS

Sexual disorder NOS

303       Alcohol dependence syndrome

Use additional code to identify any associated condition, as:

alcoholic psychoses (291.0-291.9)

drug dependence (304.0-304.9)

physical complications of alcohol, such as:

cerebral degeneration (331.7)

cirrhosis of liver (571.2)

epilepsy (345.0-345.9)

gastritis (535.3)

hepatitis (571.1)

liver damage NOS (571.3)

Excludes:          drunkenness NOS (305.0)

The following fifth-digit subclassification is for use with category 303:

0 unspecified

1 continuous

2 episodic

3 in remission

303.0    Acute alcoholic intoxication

Acute drunkenness in alcoholism

303.9    Other and unspecified alcohol dependence

Chronic alcoholism

Dipsomania

304       Drug dependence

Excludes:          nondependent abuse of drugs (305.1-305.9)

The following fifth-digit subclassification is for use with category 304:

0 unspecified

1 continuous

2 episodic

3 in remission

304.0    Opioid type dependence

Heroin

Meperidine

Methadone

Morphine

Opium

Opium alkaloids and their derivatives

Synthetics with morphine-like effects

304.1    Sedative, hypnotic or anxiolytic dependence

Barbiturates

Nonbarbiturate sedatives and tranquilizers with a similar effect:

chlordiazepoxide

diazepam

glutethimide

meprobamate

methaqualone

304.2    Cocaine dependence

Coca leaves and derivatives

304.3    Cannabis dependence

Hashish

Hemp

Marihuana

304.4    Amphetamine and other psychostimulant dependence

Methylphenidate

Phenmetrazine

304.5    Hallucinogen dependence

Dimethyltryptamine [DMT]

Lysergic acid diethylamide [LSD] and derivatives

Mescaline

Psilocybin

304.6    Other specified drug dependence

Absinthe addiction

Glue sniffing

Inhalant dependence

Phencyclidine dependence

Excludes:          tobacco dependence (305.1)

304.7    Combinations of opioid type drug with any other

304.8    Combinations of drug dependence excluding opioid type drug

304.9    Unspecified drug dependence

Drug addiction NOS

Drug dependence NOS

305       Nondependent abuse of drugs

Note:    Includes cases where a person, for whom no other diagnosis is possible, has come under medical care because of the maladaptive effect of a drug on which he is not dependent and that he has taken on his own initiative to the detriment of his health or social functioning.

Excludes:          alcohol dependence syndrome (303.0-303.9)

drug dependence (304.0-304.9)

drug withdrawal syndrome (292.0)

poisoning by drugs or medicinal substances (960.0-979.9)

The following fifth-digit subclassification is for use with codes 305.0, 305.2-305.9

0 unspecified

1 continuous

2 episodic

3 in remission

305.0    Alcohol abuse

Drunkenness NOS

Excessive drinking of alcohol NOS

"Hangover" (alcohol)

Inebriety NOS

Excludes:          acute alcohol intoxication in alcoholism (303.0)

alcoholic psychoses (291.0-291.9)

305.1    Tobacco use disorder

Tobacco dependence

Excludes:          history of tobacco use (V15.82)

305.2    Cannabis abuse

305.3    Hallucinogen abuse

Acute intoxication from hallucinogens ["bad trips"]

LSD reaction

305.4    Sedative, hypnotic or anxiolytic abuse

305.5    Opioid abuse

305.6    Cocaine abuse

305.7    Amphetamine or related acting sympathomimetic abuse

305.8    Antidepressant type abuse

305.9    Other, mixed, or unspecified drug abuse

Caffeine intoxication

Inhalant abuse

"Laxative habit"

Misuse of drugs NOS

Nonprescribed use of drugs or patent medicinals

Phencyclidine abuse

306       Physiological malfunction arising from mental factors

Includes:           psychogenic:

physical symptoms not involving tissue damage

physiological manifestations not involving tissue damage

Excludes:          hysteria (300.11-300.19)

physical symptoms secondary to a psychiatric disorder classified elsewhere

psychic factors associated with physical conditions involving tissue damage classified elsewhere (316)

specific nonpsychotic mental disorders following organic brain damage (310.0-310.9)

306.0    Musculoskeletal

Psychogenic paralysis

Psychogenic torticollis

Excludes:          Gilles de la Tourette's syndrome (307.23)

paralysis as hysterical or conversion reaction (300.11)

tics (307.20-307.22)

306.1    Respiratory

Psychogenic:

air hunger

cough

hiccough

hyperventilation

yawning

Excludes:          psychogenic asthma (316 and 493.9)

306.2    Cardiovascular

Cardiac neurosis

Cardiovascular neurosis

Neurocirculatory asthenia

Psychogenic cardiovascular disorder

Excludes:          psychogenic paroxysmal tachycardia (316 and 427.2)

306.3    Skin

Psychogenic pruritus

Excludes:          psychogenic:

alopecia (316 and 704.00)

dermatitis (316 and 692.9)

eczema (316 and 691.8 or 692.9)

urticaria (316 and 708.0-708.9)

306.4    Gastrointestinal

Aerophagy

Cyclical vomiting, psychogenic

Diarrhea, psychogenic

Nervous gastritis

Psychogenic dyspepsia

Excludes:          cyclical vomiting NOS (536.2)

globus hystericus (300.11)

mucous colitis (316 and 564.9)

psychogenic:

cardiospasm (316 and 530.0)

duodenal ulcer (316 and 532.0-532.9)

gastric ulcer (316 and 531.0-531.9)

peptic ulcer NOS (316 and 533.0-533.9)

vomiting NOS (307.54)

306.5    Genitourinary

Excludes:          enuresis, psychogenic (307.6)

frigidity (302.72)

impotence (302.72)

psychogenic dyspareunia (302.76)

306.50  Psychogenic genitourinary malfunction, unspecified

306.51  Psychogenic vaginismus

Functional vaginismus

306.52  Psychogenic dysmenorrhea

306.53  Psychogenic dysuria

306.59  Other

306.6    Endocrine

306.7    Organs of special sense

Excludes:          hysterical blindness or deafness (300.11)

psychophysical visual disturbances (368.16)

306.8    Other specified psychophysiological malfunction

Bruxism

Teeth grinding

306.9    Unspecified psychophysiological malfunction

Psychophysiologic disorder NOS

Psychosomatic disorder NOS

307       Special symptoms or syndromes, not elsewhere classified

Note:    This category is intended for use if the psychopathology is manifested by a single specific symptom or group of symptoms which is not part of an organic illness or other mental disorder classifiable elsewhere.

Excludes:          those due to mental disorders classified elsewhere

those of organic origin

307.0    Stuttering

Excludes:          dysphasia (784.5)

lisping or lalling (307.9)

retarded development of speech (315.31-315.39)

307.1    Anorexia nervosa

Excludes:          eating disturbance NOS (307.50)

feeding problem (783.3)

of nonorganic origin (307.59)

loss of appetite (783.0)

of nonorganic origin (307.59)

307.2    Tics

Excludes:          nail-biting or thumb-sucking (307.9)

stereotypes occurring in isolation (307.3)

tics of organic origin (333.3)

307.20  Tic disorder, unspecified

Tic disorder NOS

307.21  Transient tic disorder

307.22  Chronic motor or vocal tic disorder

307.23  Tourette's disorder

Motor-verbal tic disorder

307.3    Stereotypic movement disorder

Body-rocking

Head banging

Spasmus nutans

Stereotypes NOS

Excludes:          tics (307.20-307.23)

of organic origin (333.3)

307.4    Specific disorders of sleep of nonorganic origin

Excludes:          narcolepsy (347.00-347.11)

organic hypersomnia (327.10-327.19)

organic insomnia (327.00-327.09)

those of unspecified cause (780.50-780.59)

307.40  Nonorganic sleep disorder, unspecified

307.41  Transient disorder of initiating or maintaining sleep

Adjustment insomnia

Hyposomnia associated with acute or intermittent emotional reactions or conflicts

Insomnia associated with acute or intermittent emotional reactions or conflicts

Sleeplessness associated with acute or intermittent emotional reactions or conflicts

307.42  Persistent disorder of initiating or maintaining sleep

Hyposomnia, insomnia, or sleeplessness associated with:

anxiety

conditioned arousal

depression (major) (minor)

psychosis

Idiopathic insomnia

Paradoxical insomnia

Primary insomnia

Psychophysiological insomnia

307.43  Transient disorder of initiating or maintaining wakefulness

Hypersomnia associated with acute or intermittent emotional reactions or conflicts

307.44  Persistent disorder of initiating or maintaining wakefulness

Hypersomnia associated with depression (major) (minor)

Insufficient sleep syndrome

Primary hypersomnia

Excludes:          sleep deprivation (V69.4)

307.45  Circadian rhythm sleep disorder of nonorganic origin

307.46  Sleep arousal disorder

Night terror disorder

Night terrors

Sleep terror disorder

Sleepwalking

Somnambulism

307.47  Other dysfunctions of sleep stages or arousal from sleep

Nightmare disorder

Nightmares:

NOS

REM-sleep type

Sleep drunkenness

307.48  Repetitive intrusions of sleep

Repetitive intrusion of sleep with:

atypical polysomnographic features

environmental disturbances

repeated REM-sleep interruptions

307.49  Other

"Short-sleeper"

Subjective insomnia complaint

307.5    Other and unspecified disorders of eating

Excludes:          anorexia:

nervosa (307.1)

of unspecified cause (783.0)

overeating, of unspecified cause (783.6)

vomiting:

NOS (787.0)

cyclical (536.2)

psychogenic (306.4)

307.50  Eating disorder, unspecified

Eating disorder NOS

307.51  Bulimia nervosa

Overeating of nonorganic origin

307.52  Pica

Perverted appetite of nonorganic origin

307.53  Rumination disorder

Regurgitation, of nonorganic origin, of food with reswallowing

Excludes:          obsessional rumination (300.3)

307.54  Psychogenic vomiting

307.59  Other

Feeding disorder of infancy or early childhood of nonorganic origin

Infantile feeding disturbances of nonorganic origin

Loss of appetite of nonorganic origin

307.6    Enuresis

Enuresis (primary) (secondary) of nonorganic origin

Excludes:          enuresis of unspecified cause (788.3)

307.7    Encopresis

Encopresis (continuous) (discontinuous) of nonorganic origin

Excludes:          encopresis of unspecified cause (787.6)

307.8    Pain disorders related to psychological factors

307.80  Psychogenic pain, site unspecified

307.81  Tension headache

Excludes:          headache:

NOS (784.0)

migraine (346.0-346.9)

307.89  Other

Code first to site of pain

Excludes: pain disorder exclusively attributed to psychological factors (307.80)

psychogenic pain (307.80)

307.9    Other and unspecified special symptoms or syndromes, not elsewhere classified

Communication disorder NOS

Hair plucking

Lalling

Lisping

Masturbation

Nail-biting

Thumb-sucking

308       Acute reaction to stress

Includes:           catastrophic stress

combat fatigue

gross stress reaction (acute)

transient disorders in response to exceptional physical or mental stress which usually subside within hours or days

Excludes:          adjustment reaction or disorder (309.0-309.9)

chronic stress reaction (309.1-309.9)

308.0    Predominant disturbance of emotions

Anxiety as acute reaction to exceptional [gross] stress

Emotional crisis as acute reaction to exceptional [gross] stress

Panic state as acute reaction to exceptional [gross] stress

308.1    Predominant disturbance of consciousness

Fugues as acute reaction to exceptional [gross] stress

308.2    Predominant psychomotor disturbance

Agitation states as acute reaction to exceptional [gross] stress

Stupor as acute reaction to exceptional [gross] stress

308.3    Other acute reactions to stress

Acute situational disturbance

Acute stress disorder

Excludes:          prolonged posttraumatic emotional disturbance (309.81)

308.4    Mixed disorders as reaction to stress

308.9    Unspecified acute reaction to stress

309       Adjustment reaction

Includes:           adjustment disorders

reaction (adjustment) to chronic stress

Excludes:          acute reaction to major stress (308.0-308.9)

neurotic disorders (300.0-300.9)

309.0    Adjustment disorder with depressed mood

Grief reaction

Excludes:          affective psychoses (296.0-296.9)

neurotic depression (300.4)

prolonged depressive reaction (309.1)

psychogenic depressive psychosis (298.0)

309.1    Prolonged depressive reaction

Excludes:          affective psychoses (296.0-296.9)

brief depressive reaction (309.0)

neurotic depression (300.4)

psychogenic depressive psychosis (298.0)

309.2    With predominant disturbance of other emotions

309.21  Separation anxiety disorder

309.22  Emancipation disorder of adolescence and early adult life

309.23  Specific academic or work inhibition

309.24  Adjustment disorder with anxiety

309.28  Adjustment disorder with mixed anxiety and depressed mood

Adjustment reaction with anxiety and depression

309.29  Other

Culture shock

309.3    Adjustment disorder with disturbance of conduct

Conduct disturbance as adjustment reaction

Destructiveness as adjustment reaction

Excludes:          destructiveness in child (312.9)

disturbance of conduct NOS (312.9)

dyssocial behavior without manifest psychiatric disorder (V71.01-V71.02)

personality disorder with predominantly sociopathic or asocial manifestations (301.7)

309.4    Adjustment disorder with mixed disturbance of emotions and conduct

309.8    Other specified adjustment reactions

309.81  Posttraumatic stress disorder

Chronic posttraumatic stress disorder

Concentration camp syndrome

Posttraumatic stress disorder NOS

Excludes:          acute stress disorder (308.3)

posttraumatic brain syndrome:

nonpsychotic (310.2)

psychotic (293.0-293.9)

309.82  Adjustment reaction with physical symptoms

309.83  Adjustment reaction with withdrawal

Elective mutism as adjustment reaction

Hospitalism (in children) NOS

309.89  Other

309.9    Unspecified adjustment reaction

Adaptation reaction NOS

Adjustment reaction NOS

310       Specific nonpsychotic mental disorders due to brain damage

Excludes:          neuroses, personality disorders, or other nonpsychotic conditions occurring in a form similar to that seen with functional disorders but in association with a physical condition (300.0-300.9, 301.0-301.9)

310.0    Frontal lobe syndrome

Lobotomy syndrome

Postleucotomy syndrome [state]

Excludes:          postcontusion syndrome (310.2)

310.1    Personality change due to conditions classified elsewhere

Cognitive or personality change of other type, of nonpsychotic severity

Organic psychosyndrome of nonpsychotic severity

Presbyophrenia NOS

Senility with mental changes of nonpsychotic severity

Excludes:          memory loss of unknown cause (780.93)

310.2    Postconcussion syndrome

Postcontusion syndrome or encephalopathy

Posttraumatic brain syndrome, nonpsychotic

Status postcommotio cerebri

Excludes:          any organic psychotic conditions following head injury (293.0-294.0)

frontal lobe syndrome (310.0)

postencephalitic syndrome (310.8)

310.8    Other specified nonpsychotic mental disorders following organic brain damage

Mild memory disturbance

Postencephalitic syndrome

Other focal (partial) organic psychosyndromes

310.9    Unspecified nonpsychotic mental disorder following organic brain damage

311       Depressive disorder, not elsewhere classified

Depressive disorder NOS

Depressive state NOS

Depression NOS

Excludes:          acute reaction to major stress with depressive symptoms (308.0)

affective personality disorder (301.10-301.13)

affective psychoses (296.0-296.9)

brief depressive reaction (309.0)

depressive states associated with stressful events (309.0-309.1)

disturbance of emotions specific to childhood and adolescence, with misery and unhappiness (313.1)

mixed adjustment reaction with depressive symptoms (309.4)

neurotic depression (300.4)

prolonged depressive adjustment reaction (309.1)

psychogenic depressive psychosis (298.0)

312       Disturbance of conduct, not elsewhere classified

Excludes:          adjustment reaction with disturbance of conduct (309.3)

drug dependence (304.0-304.9)

dyssocial behavior without manifest psychiatric disorder (V71.01-V71.02)

personality disorder with predominantly sociopathic or asocial manifestations (301.7)

sexual deviations (302.0-302.9)

The following fifth-digit subclassification is for use with categories 312.0-312.2:

0 unspecified

1 mild

2 moderate

3 severe

312.0    Undersocialized conduct disorder, aggressive type

Aggressive outburst

Anger reaction

Unsocialized aggressive disorder

312.1    Undersocialized conduct disorder, unaggressive type

Childhood truancy, unsocialized

Solitary stealing

Tantrums

312.2    Socialized conduct disorder

Childhood truancy, socialized

Group delinquency

Excludes:          gang activity without manifest psychiatric disorder (V71.01)

312.3    Disorders of impulse control, not elsewhere classified

312.30  Impulse control disorder, unspecified

312.31  Pathological gambling

312.32  Kleptomania

312.33  Pyromania

312.34  Intermittent explosive disorder

312.35  Isolated explosive disorder

312.39  Other

Trichotillomania

312.4    Mixed disturbance of conduct and emotions

Neurotic delinquency

Excludes:          compulsive conduct disorder (312.3)

312.8    Other specified disturbances of conduct, not elsewhere classified

312.81  Conduct disorder, childhood onset type

312.82  Conduct disorder, adolescent onset type

312.89  Other conduct disorder

Conduct disorder of unspecified onset

312.9    Unspecified disturbance of conduct

Delinquency (juvenile)

Disruptive behavior disorder NOS

313       Disturbance of emotions specific to childhood and adolescence

Excludes:          adjustment reaction (309.0-309.9)

emotional disorder of neurotic type (300.0-300.9)

masturbation, nail-biting, thumb-sucking, and other isolated symptoms (307.0-307.9)

313.0    Overanxious disorder

Anxiety and fearfulness of childhood and adolescence

Overanxious disorder of childhood and adolescence

Excludes:          abnormal separation anxiety (309.21)

anxiety states (300.00-300.09)

hospitalism in children (309.83)

phobic state (300.20-300.29)

313.1    Misery and unhappiness disorder

Excludes:          depressive neurosis (300.4)

313.2    Sensitivity, shyness, and social withdrawal disorder

Excludes:          infantile autism (299.0)

schizoid personality (301.20-301.22)

schizophrenia (295.0-295.9)

313.21  Shyness disorder of childhood

Sensitivity reaction of childhood or adolescence

313.22  Introverted disorder of childhood

Social withdrawal of childhood or  adolescence

Withdrawal reaction of childhood or  adolescence

313.23  Selective mutism

Excludes:          elective mutism as adjustment reaction (309.83)

313.3    Relationship problems

Sibling jealousy

Excludes:          relationship problems associated with aggression, destruction, or other forms of conduct disturbance (312.0-312.9)

313.8    Other or mixed emotional disturbances of childhood or adolescence

313.81  Oppositional defiant disorder

313.82  Identity disorder

Identity problem

313.83  Academic underachievement disorder

313.89  Other

Reactive attachment disorder of infancy or early childhood

313.9    Unspecified emotional disturbance of childhood or adolescence

Mental disorder of infancy, childhood or adolescence NOS

314       Hyperkinetic syndrome of childhood

Excludes:          hyperkinesis as symptom of underlying disorder­code the underlying disorder

314.0    Attention deficit disorder

Adult

Child

314.00  Without mention of hyperactivity

Predominantly inattentive type

314.01  With hyperactivity

Combined type

Overactivity NOS

Predominantly hyperactive/impulsive type

Simple disturbance of attention with overactivity

314.1    Hyperkinesis with developmental delay

Developmental disorder of hyperkinesis

Use additional code to identify any associated neurological disorder

314.2    Hyperkinetic conduct disorder

Hyperkinetic conduct disorder without developmental delay

Excludes:          hyperkinesis with significant delays in specific skills (314.1)

314.8    Other specified manifestations of hyperkinetic syndrome

314.9    Unspecified hyperkinetic syndrome

Hyperkinetic reaction of childhood or adolescence NOS

Hyperkinetic syndrome NOS

315       Specific delays in development

Excludes:          that due to a neurological disorder (320.0-389.9)

315.0    Specific reading disorder

315.00  Reading disorder, unspecified

315.01  Alexia

315.02  Developmental dyslexia

315.09  Other

Specific spelling difficulty

315.1    Mathematics disorder

Dyscalculia

315.2    Other specific learning difficulties

Disorder of written expression

Excludes:          specific arithmetical disorder (315.1)

specific reading disorder (315.00-315.09)

315.3    Developmental speech or language disorder

315.31  Expressive language disorder

Developmental aphasia

Word deafness

Excludes:          acquired aphasia (784.3)

elective mutism (309.83, 313.0, 313.23)

315.32  Mixed receptive-expressive language disorder

315.39  Other

Developmental articulation disorder

Dyslalia

Phonological disorder

Excludes:          lisping and lalling (307.9)

stammering and stuttering (307.0)

315.4    Developmental coordination disorder

Clumsiness syndrome

Dyspraxia syndrome

Specific motor development disorder

315.5    Mixed development disorder

315.8    Other specified delays in development

315.9    Unspecified delay in development

Developmental disorder NOS

Learning disorder NOS

316       Psychic factors associated with diseases classified elsewhere

Psychologic factors in physical conditions classified elsewhere

Use additional code to identify the associated physical condition, as:

psychogenic:

asthma (493.9)

dermatitis (692.9)

duodenal ulcer (532.0-532.9)

eczema (691.8, 692.9)

gastric ulcer (531.0-531.9)

mucous colitis (564.9)

paroxysmal tachycardia (427.2)

ulcerative colitis (556)

urticaria (708.0-708.9)

psychosocial dwarfism (259.4)

Excludes:          physical symptoms and physiological malfunctions, not involving tissue damage, of mental origin (306.0-306.9)

MENTAL RETARDATION (317-319)

Use additional code(s) to identify any associated psychiatric or physical condition(s)

317       Mild mental retardation

High-grade defect

IQ 50-70

Mild mental subnormality

318       Other specified mental retardation

318.0    Moderate mental retardation

IQ 35-49

Moderate mental subnormality

318.1    Severe mental retardation

IQ 20-34

Severe mental subnormality

318.2    Profound mental retardation

IQ under 20

Profound mental subnormality

319       Unspecified mental retardation

Mental deficiency NOS

Mental subnormality NOS

6. DISEASES OF THE NERVOUS SYSTEM AND SENSE ORGANS (320-389) back to top

INFLAMMATORY DISEASES OF THE CENTRAL NERVOUS SYSTEM (320-326)

320       Bacterial meningitis

Includes:           arachnoiditis bacterial

leptomeningitis bacterial

meningitis bacterial

meningoencephalitis bacterial

meningomyelitis bacterial

pachymeningitis bacterial

320.0    Hemophilus meningitis

Meningitis due to Hemophilus influenzae [H. influenzae]

320.1    Pneumococcal meningitis

320.2    Streptococcal meningitis

320.3    Staphylococcal meningitis

320.7    Meningitis in other bacterial diseases classified elsewhere

Code first underlying disease as:

actinomycosis (039.8)

listeriosis (027.0)

typhoid fever (002.0)

whooping cough (033.0-033.9)

Excludes:          meningitis (in):

epidemic (036.0)

gonococcal (098.82)

meningococcal (036.0)

salmonellosis (003.21)

syphilis:

NOS (094.2)

congenital (090.42)

meningovascular (094.2)

secondary (091.81)

tuberculosis (013.0)

320.8    Meningitis due to other specified bacteria

320.81  Anaerobic meningitis

Gram-negative anaerobes

Bacteroides (fragilis)

320.82  Meningitis due to gram-negative bacteria, not elsewhere classified

Aerobacter aerogenes

Escherichia coli [E. coli]

Friedlander bacillus

Klebsiella pneumoniae

Proteus morganii

Pseudomonas

Excludes:          gram-negative anaerobes (320.81)

320.89  Meningitis due to other specified bacteria

Bacillus pyocyaneus

320.9    Meningitis due to unspecified bacterium

Meningitis:

bacterial NOS

purulent NOS

pyogenic NOS

suppurative NOS

321       Meningitis due to other organisms

Includes:           arachnoiditis due to organisms other than bacteria

leptomeningitis due to organisms other than bacteria

meningitis due to organisms other than bacteria

pachymeningitis due to organisms other than bacteria

321.0    Cryptococcal meningitis

Code first underlying disease (117.5)

321.1    Meningitis in other fungal diseases

Code first underlying disease (110.0-118)

Excludes:          meningitis in:

candidiasis (112.83)

coccidioidomycosis (114.2)

histoplasmosis (115.01, 115.11, 115.91)

321.2    Meningitis due to viruses not elsewhere classified

Code first underlying disease, as:

meningitis due to arbovirus (060.0-066.9)

Excludes:          meningitis (due to):

abacterial (047.0-047.9)

adenovirus (049.1)

aseptic NOS (047.9)

Coxsackie (virus) (047.0)

ECHO virus (047.1)

enterovirus (047.0-047.9)

herpes simplex virus (054.72)

herpes zoster virus (053.0)

lymphocytic choriomeningitis virus (049.0)

mumps (072.1)

viral NOS (047.9)

meningo-eruptive syndrome (047.1)

321.3    Meningitis due to trypanosomiasis

Code first underlying disease (086.0-086.9)

321.4    Meningitis in sarcoidosis

Code first underlying disease (135)

321.8    Meningitis due to other nonbacterial organisms classified elsewhere

Code first underlying disease

Excludes:          leptospiral meningitis (100.81)

322       Meningitis of unspecified cause

Includes:           arachnoiditis with no organism specified as cause

leptomeningitis with no organism specified as cause

meningitis with no organism specified as cause

pachymeningitis with no organism specified as cause

322.0    Nonpyogenic meningitis

Meningitis with clear cerebrospinal fluid

322.1    Eosinophilic meningitis

322.2    Chronic meningitis

322.9    Meningitis, unspecified

323       Encephalitis, myelitis, and encephalomyelitis

Includes:           acute disseminated encephalomyelitis

meningoencephalitis, except bacterial

meningomyelitis, except bacterial

myelitis (acute):

ascending

transverse

Excludes:          bacterial:

meningoencephalitis (320.0-320.9)

meningomyelitis (320.0-320.9)

323.0    Encephalitis in viral diseases classified elsewhere

Code first underlying disease, as:

cat-scratch disease (078.3)

infectious mononucleosis (075)

ornithosis (073.7)

Excludes:          encephalitis (in):

arthropod-borne viral (062.0-064)

herpes simplex (054.3)

mumps (072.2)

poliomyelitis (045.0-045.9)

rubella (056.01)

slow virus infections of central nervous system (046.0-046.9)

other viral diseases of central nervous system (049.8-049.9)

viral NOS (049.9)

323.1    Encephalitis in rickettsial diseases classified elsewhere

Code first underlying disease (080-083.9)

323.2    Encephalitis in protozoal diseases classified elsewhere

Code first underlying disease, as:

malaria (084.0-084.9)

trypanosomiasis (086.0-086.9)

323.4    Other encephalitis due to infection classified elsewhere

Code first underlying disease

Excludes:          encephalitis (in):

meningococcal (036.1)

syphilis:

NOS (094.81)

congenital (090.41)

toxoplasmosis (130.0)

tuberculosis (013.6)

meningoencephalitis due to free-living ameba [Naegleria] (136.2)

323.5    Encephalitis following immunization procedures

Encephalitis postimmunization or postvaccinal

Encephalomyelitis postimmunization or postvaccinal

Use additional E code to identify vaccine

323.6    Postinfectious encephalitis

Infectious acute disseminated encephalomyelitis (ADEM)

Code first underlying disease

Excludes:          encephalitis:

postchickenpox (052.0)

postmeasles (055.0)

323.7    Toxic encephalitis

Code first underlying cause, as:

carbon tetrachloride (982.1)

hydroxyquinoline derivatives (961.3)

lead (984.0-984.9)

mercury (985.0)

thallium (985.8)

323.8    Other causes of encephalitis

Noninfectious acute disseminated encephalomyelitis (ADEM)

323.9    Unspecified cause of encephalitis

324       Intracranial and intraspinal abscess

324.0    Intracranial abscess

Abscess (embolic):

cerebellar

cerebral

Abscess (embolic) of brain [any part]:

epidural

extradural

otogenic

subdural

Excludes:          tuberculous (013.3)

324.1    Intraspinal abscess

Abscess (embolic) of spinal cord [any part]:

epidural

extradural

subdural

Excludes:          tuberculous (013.5)

324.9    Of unspecified site

Extradural or subdural abscess NOS

325       Phlebitis and thrombophlebitis of intracranial venous sinuses

Embolism of cavernous, lateral, or other intracranial or unspecified intracranial venous sinus

Endophlebitis of cavernous, lateral, or other intracranial or unspecified intracranial venous sinus

Phlebitis, septic or suppurative of cavernous, lateral, or other intracranial or unspecified intracranial venous sinus

Thrombophlebitis of cavernous, lateral, or other intracranial or unspecified intracranial venous sinus

Thrombosis of cavernous, lateral, or other intracranial or unspecified intracranial venous sinus

Excludes:          that specified as:

complicating pregnancy, childbirth, or the puerperium (671.5)

of nonpyogenic origin (437.6)

326       Late effects of intracranial abscess or pyogenic infection

Note:    This category is to be used to indicate conditions whose primary classification is to 320-325 [excluding 320.7, 321.0-321.8, 323.0-323.4, 323.6-323.7] as the cause of late effects, themselves classifiable elsewhere. The "late effects" include conditions specified as such, or as sequelae, which may occur at any time after the resolution of the causal condition.

Use additional code to identify condition, as:

hydrocephalus (331.4)

paralysis (342.0-342.9, 344.0-344.9)

327       Organic sleep disorders

327.0    Organic disorders of initiating and maintaining sleep [Organic insomnia]

Excludes:          insomnia NOS (780.52)

insomnia not due to a substance or known physiological condition (307.41-307.42)

insomnia with sleep apnea NOS (780.51)

327.00  Organic insomnia, unspecified

327.01  Insomnia due to medical condition classified elsewhere

Code first underlying condition

Excludes:          insomnia due to mental disorder (327.02)

327.02  Insomnia due to mental disorder

Code first mental disorder

Excludes:          alcohol induced insomnia (291.82)

drug induced insomnia (292.85)

327.09  Other organic insomnia

327.1    Organic disorder of excessive somnolence [Organic hypersomnia]

Excludes:          hypersomnia NOS (780.54)

hypersomnia not due to a substance or known physiological condition (307.43-307.44)

hypersomnia with sleep apnea NOS (780.53)

327.10  Organic hypersomnia, unspecified

327.11  Idiopathic hypersomnia with long sleep time

327.12  Idiopathic hypersomnia without long sleep time

327.13  Recurrent hypersomnia

Kleine-Levin syndrome

Menstrual related hypersomnia

327.14  Hypersomnia due to medical condition classified elsewhere

Code first underlying condition

Excludes:          hypersomnia due to mental disorder (327.15)

327.15  Hypersomnia due to mental disorder

Code first mental disorder

Excludes:          alcohol induced insomnia (291.82)

drug induced insomnia (292.85)

327.19  Other organic hypersomnia

327.2    Organic sleep apnea

Excludes:          Cheyne-Stokes breathing (786.04)

hypersomnia with sleep apnea NOS (780.53)

insomnia with sleep apnea NOS (780.51)

sleep apnea in newborn  (770.81-770.82)

sleep apnea NOS (780.57)

327.20  Organic sleep apnea, unspecified

327.21  Primary central sleep apnea

327.22  High altitude periodic breathing

327.23  Obstructive sleep apnea (adult) (pediatric)

327.24  Idiopathic sleep related nonobstructive alveolar hypoventilation

Sleep related hypoxia

327.25  Congenital central alveolar hypoventilation syndrome

327.26  Sleep related hypoventilation/hypoxemia in conditions classifiable elsewhere

Code first underlying condition

327.27  Central sleep apnea in conditions classified elsewhere

Code first underlying condition

327.29  Other organic sleep apnea

327.3    Circadian rhythm sleep disorder

Organic disorder of sleep wake cycle

Organic disorder of sleep wake schedule

Excludes:          alcohol induced circadian rhythm sleep disorder (291.82)

circadian rhythm sleep disorder of nonorganic origin (307.45)

disruption of 24 hour sleep wake cycle NOS (780.55)

drug induced circadian rhythm sleep disorder (292.85)

327.30  Circadian rhythm sleep disorder, unspecified

327.31  Circadian rhythm sleep disorder, delayed sleep phase type

327.32  Circadian rhythm sleep disorder, advanced sleep phase type

327.33  Circadian rhythm sleep disorder, irregular sleep-wake type

327.34  Circadian rhythm sleep disorder, free-running type

327.35  Circadian rhythm sleep disorder, jet lag type

327.36  Circadian rhythm sleep disorder, shift work type

327.37  Circadian rhythm sleep disorder in conditions classified elsewhere

Code first underlying condition

327.39  Other circadian rhythm sleep disorder

327.4    Organic parasomnia

Excludes:          alcohol induced parasomnia (291.82)

drug induced parasomnia (292.85)

parasomnia not due to a known physiological conditions (307.47)

327.40  Organic parasomnia, unspecified

327.41  Confusional arousals

327.42  REM sleep behavior disorder

327.43  Recurrent isolated sleep paralysis

327.44  Parasomnia in conditions classified elsewhere

Code first underlying condition

327.49  Other organic parasomnia

327.5    Organic sleep related movement disorders

Excludes:          restless leg syndrome (333.99)

sleep related movement disorder NOS (780.58)

327.51  Periodic limb movement disorder

Periodic limb movement sleep disorder

327.52  Sleep related leg cramps

327.53  Sleep related bruxism

327.59  Other organic sleep related movement disorders

327.8    Other organic sleep disorders

HEREDITARY AND DEGENERATIVE DISEASES OF THE CENTRAL NERVOUS SYSTEM (330-337)

Excludes:         hepatolenticular degeneration (275.1)

multiple sclerosis (340)

other demyelinating diseases of central nervous system (341.0-341.9)

330       Cerebral degenerations usually manifest in childhood

Use additional code to identify associated mental retardation

330.0    Leukodystrophy

Krabbe's disease

Leukodystrophy:

NOS

globoid cell

metachromatic

sudanophilic

Pelizaeus-Merzbacher disease

Sulfatide lipidosis

330.1    Cerebral lipidoses

Amaurotic (familial) idiocy

Disease:

Batten

Jansky-Bielschowsky

Kufs'

Spielmeyer-Vogt

Tay-Sachs

Gangliosidosis

330.2    Cerebral degeneration in generalized lipidoses

Code first underlying disease, as:

Fabry's disease (272.7)

Gaucher's disease (272.7)

Niemann-Pick disease (272.7)

sphingolipidosis (272.7)

330.3    Cerebral degeneration of childhood in other diseases classified elsewhere

Code first underlying disease, as:

Hunter's disease (277.5)

mucopolysaccharidosis (277.5)

330.8    Other specified cerebral degenerations in childhood

Alpers' disease or gray-matter degeneration

Infantile necrotizing encephalomyelopathy

Leigh's disease

Subacute necrotizing encephalopathy or encephalomyelopathy

330.9    Unspecified cerebral degeneration in childhood

331       Other cerebral degenerations

331.0    Alzheimer's disease

331.1    Frontotemporal dementia

Use additional code for associated behavioral disturbances (294.10-294.11)

331.11  Pick's disease

331.19  Other frontotemporal dementia

Frontal dementia

331.2    Senile degeneration of brain

Excludes:          senility NOS (797)

331.3    Communicating hydrocephalus

Excludes:          congenital hydrocephalus (741.0, 742.3)

331.4    Obstructive hydrocephalus

Acquired hydrocephalus NOS

Excludes:          congenital hydrocephalus (741.0, 742.3)

331.7    Cerebral degeneration in diseases classified elsewhere

Code first underlying disease, as:

alcoholism (303.0-303.9)

beriberi (265.0)

cerebrovascular disease (430-438)

congenital hydrocephalus (741.0, 742.3)

neoplastic disease (140.0-239.9)

myxedema (244.0-244.9)

vitamin B12 deficiency (266.2)

Excludes:          cerebral degeneration in:

Jakob-Creutzfeldt disease (046.1)

progressive multifocal leukoencephalopathy (046.3)

subacute spongiform encephalopathy (046.1)

331.8    Other cerebral degeneration

331.81  Reye's syndrome

331.82  Dementia with Lewy bodies

Dementia with Parkinsonism

Lewy body dementia

Lewy body disease

Use additional code for associated behavioral disturbances (294.10-294.11)

331.89  Other

Cerebral ataxia

331.9    Cerebral degeneration, unspecified

332       Parkinson's disease

Excludes:          dementia with Parkinsonism (331.82)

332.0    Paralysis agitans

Parkinsonism or Parkinson's disease:

NOS

idiopathic

primary

332.1    Secondary Parkinsonism

Neuroleptic-induced Parkinsonism

Parkinsonism due to drugs

Use additional E code to identify drug, if drug-induced

Excludes:          Parkinsonism (in):

Huntington's disease (333.4)

progressive supranuclear palsy (333.0)

Shy-Drager syndrome (333.0)

syphilitic (094.82)

333       Other extrapyramidal disease and abnormal movement disorders

Includes:           other forms of extrapyramidal, basal ganglia, or striatopallidal disease

Excludes:          abnormal movements of head NOS (781.0)

sleep related movement disorders (327.51-327.59)

333.0    Other degenerative diseases of the basal ganglia

Atrophy or degeneration:

olivopontocerebellar [Déjérine-Thomas syndrome]

pigmentary pallidal [Hallervorden-Spatz disease] striatonigral

Parkinsonian syndrome associated with:

idiopathic orthostatic hypotension

symptomatic orthostatic hypotension

Progressive supranuclear ophthalmoplegia

Shy-Drager syndrome

333.1    Essential and other specified forms of tremor

Benign essential tremor

Familial tremor

Medication-induced postural tremor

Use additional E code to identify drug, if drug-induced

Excludes:          tremor NOS (781.0)

333.2    Myoclonus

Familial essential myoclonus

Progressive myoclonic epilepsy

Unverricht-Lundborg disease

Use additional E code to identify drug, if drug-induced

333.3    Tics of organic origin

Excludes:          Gilles de la Tourette's syndrome (307.23)

habit spasm (307.22)

tic NOS (307.20)

Use additional E code to identify drug, if drug-induced

333.4    Huntington's chorea

333.5    Other choreas

Hemiballism(us)

Paroxysmal choreo-athetosis

Excludes:          Sydenham's or rheumatic chorea (392.0-392.9)

Use additional E code to identify drug, if drug-induced

333.6    Idiopathic torsion dystonia

Dystonia:

deformans progressiva

musculorum deformans

(Schwalbe-) Ziehen-Oppenheim disease

333.7    Symptomatic torsion dystonia

Athetoid cerebral palsy [Vogt's disease]

Double athetosis (syndrome)

Neuroleptic-induced acute dystonia

Use additional E code to identify drug, if drug-induced

333.8    Fragments of torsion dystonia

Use additional E code to identify drug, if drug-induced

333.81  Blepharospasm

333.82  Orofacial dyskinesia

Neuroleptic-induced tardive dyskinesia

333.83  Spasmodic torticollis

Excludes:          torticollis:

NOS (723.5)

hysterical (300.11)

psychogenic (306.0)

333.84  Organic writers' cramp

Excludes:          psychogenic (300.89)

333.89  Other

333.9    Other and unspecified extrapyramidal diseases and abnormal movement disorders

333.90  Unspecified extrapyramidal disease and abnormal movement disorder

Medication-induced movement disorders NOS

Use additional E code to identify drug, if drug-induced

333.91  Stiff-man syndrome

333.92  Neuroleptic malignant syndrome

Use additional E to identify drug

333.93  Benign shuddering attacks

333.99  Other

Neuroleptic-induced acute akathisia

Restless legs

Use additional E code to identify drug, if drug-induced

334       Spinocerebellar disease

Excludes:          olivopontocerebellar degeneration (333.0)

peroneal muscular atrophy (356.1)

334.0    Friedreich's ataxia

334.1    Hereditary spastic paraplegia

334.2    Primary cerebellar degeneration

Cerebellar ataxia:

Marie's

Sanger-Brown

Dyssynergia cerebellaris myoclonica

Primary cerebellar degeneration:

NOS

hereditary

sporadic

334.3    Other cerebellar ataxia

Cerebellar ataxia NOS

Use additional E code to identify drug, if drug-induced

334.4    Cerebellar ataxia in diseases classified elsewhere

Code first underlying disease, as:

alcoholism (303.0-303.9)

myxedema (244.0-244.9)

neoplastic disease (140.0-239.9)

334.8    Other spinocerebellar diseases

Ataxia-telangiectasia [Louis-Bar syndrome]

Corticostriatal-spinal degeneration

334.9    Spinocerebellar disease, unspecified

335       Anterior horn cell disease

335.0    Werdnig-Hoffmann disease

Infantile spinal muscular atrophy

Progressive muscular atrophy of infancy

335.1    Spinal muscular atrophy

335.10  Spinal muscular atrophy, unspecified

335.11  Kugelberg-Welander disease

Spinal muscular atrophy:

familial

juvenile

335.19  Other

Adult spinal muscular atrophy

335.2    Motor neuron disease

335.20  Amyotrophic lateral sclerosis

Motor neuron disease (bulbar) (mixed type)

335.21  Progressive muscular atrophy

Duchenne-Aran muscular atrophy

Progressive muscular atrophy (pure)

335.22  Progressive bulbar palsy

335.23  Pseudobulbar palsy

335.24  Primary lateral sclerosis

335.29  Other

335.8    Other anterior horn cell diseases

335.9    Anterior horn cell disease, unspecified

336       Other diseases of spinal cord

336.0    Syringomyelia and syringobulbia

336.1    Vascular myelopathies

Acute infarction of spinal cord (embolic) (nonembolic)

Arterial thrombosis of spinal cord

Edema of spinal cord

Hematomyelia

Subacute necrotic myelopathy

336.2    Subacute combined degeneration of spinal cord in diseases classified elsewhere

Code first underlying disease, as:

pernicious anemia (281.0)

other vitamin B12 deficiency anemia (281.1)

vitamin B12 deficiency (266.2)

336.3    Myelopathy in other diseases classified elsewhere

Code first underlying disease, as:

myelopathy in neoplastic disease (140.0-239.9)

Excludes:          myelopathy in:

intervertebral disc disorder (722.70-722.73)

spondylosis (721.1, 721.41-721.42, 721.91)

336.8    Other myelopathy

Myelopathy:

drug-induced

radiation-induced

Use additional E code to identify cause

336.9    Unspecified disease of spinal cord

Cord compression NOS

Myelopathy NOS

Excludes:          myelitis (323.0-323.9)

spinal (canal) stenosis (723.0, 724.00-724.09)

337       Disorders of the autonomic nervous system

Includes:           disorders of peripheral autonomic, sympathetic, parasympathetic, or vegetative system

Excludes:          familial dysautonomia [Riley-Day syndrome] (742.8)

337.0    Idiopathic peripheral autonomic neuropathy

Carotid sinus syncope or syndrome

Cervical sympathetic dystrophy or paralysis

337.1    Peripheral autonomic neuropathy in disorders classified elsewhere

Code first underlying disease, as:

amyloidosis (277.3)

diabetes (250.6)

337.2    Reflex sympathetic dystrophy

337.20  Reflex sympathetic dystrophy, unspecified

337.21  Reflex sympathetic dystrophy of the upper limb

337.22  Reflex sympathetic dystrophy of the lower limb

337.29  Reflex sympathetic dystrophy of other specified site

337.3    Autonomic dysreflexia

Use additional code to identify the cause, such as:

decubitus ulcer (707.00-707.09)

fecal impaction (560.39)

urinary tract infection (599.0)

337.9    Unspecified disorder of autonomic nervous system

OTHER DISORDERS OF THE CENTRAL NERVOUS SYSTEM (340-349)

340       Multiple sclerosis

Disseminated or multiple sclerosis:

NOS

brain stem

cord

generalized

341       Other demyelinating diseases of central nervous system

341.0    Neuromyelitis optica

341.1    Schilder's disease

Balo's concentric sclerosis

Encephalitis periaxialis:

concentrica [Balo's]

diffusa [Schilder's]

341.8    Other demyelinating diseases of central nervous system

Central demyelination of corpus callosum

Central pontine myelinosis

Marchiafava (-Bignami) disease

341.9    Demyelinating disease of central nervous system, unspecified

342       Hemiplegia and hemiparesis

Note:    This category is to be used when hemiplegia (complete) (incomplete) is reported without further specification, or is stated to be old or long-standing but of unspecified cause.  The category is also for use in multiple coding to identify these types of hemiplegia resulting from any cause.

Excludes:          congenital (343.1)

hemiplegia due to late effect of cerebrovascular accident (438.20-438.22)

infantile NOS (343.4)

The following fifth-digits are for use with codes 342.0-342.9

0 affecting unspecified side

1 affecting dominant side

2 affecting nondominant side

342.0    Flaccid hemiplegia

342.1    Spastic hemiplegia

342.8    Other specified hemiplegia

342.9    Hemiplegia, unspecified

343       Infantile cerebral palsy

Includes:           cerebral:

palsy NOS

spastic infantile paralysis

congenital spastic paralysis (cerebral)

Little's disease

paralysis (spastic) due to birth injury:

intracranial

spinal

Excludes:          hereditary cerebral paralysis, such as:

hereditary spastic paraplegia (334.1)

Vogt's disease (333.7)

spastic paralysis specified as noncongenital or noninfantile (344.0-344.9)

343.0    Diplegic

Congenital diplegia

Congenital paraplegia

343.1    Hemiplegic

Congenital hemiplegia

Excludes:          infantile hemiplegia NOS (343.4)

343.2    Quadriplegic

Tetraplegic

343.3    Monoplegic

343.4    Infantile hemiplegia

Infantile hemiplegia (postnatal) NOS

343.8    Other specified infantile cerebral palsy

343.9    Infantile cerebral palsy, unspecified

Cerebral palsy NOS

344       Other paralytic syndromes

Note:    This category is to be used when the listed conditions are reported without further specification or are stated to be old or long-standing but of unspecified cause. The category is also for use in multiple coding to identify these conditions resulting from any cause.

Includes:           paralysis (complete) (incomplete), except as classifiable to 342 and 343

Excludes:          congenital or infantile cerebral palsy (343.0-343.9)

hemiplegia (342.0-342.9)

congenital or infantile (343.1, 343.4)

344.0    Quadriplegia and quadriparesis

344.00  Quadriplegia, unspecified

344.01  C1-C4, complete

344.02  C1-C4, incomplete

344.03  C5-C7, complete

344.04  C5-C7, incomplete

344.09  Other

344.1    Paraplegia

Paralysis of both lower limbs

Paraplegia (lower)

344.2    Diplegia of upper limbs

Diplegia (upper)

Paralysis of both upper limbs

344.3    Monoplegia of lower limb

Paralysis of lower limb

Excludes:          monoplegia of lower limb due to late effect of cerebrovascular accident (438.40-438.42)

344.30  Affecting unspecified side

344.31  Affecting dominant side

344.32  Affecting nondominant side

344.4    Monoplegia of upper limb

Paralysis of upper limb

Excludes:          monoplegia of upper limb due to late effect of cerebrovascular accident (438.30-438.32)

344.40  Affecting unspecified side

344.41  Affecting dominant side

344.42  Affecting nondominant side

344.5    Unspecified monoplegia

344.6    Cauda equina syndrome

344.60  Without mention of neurogenic bladder

344.61  With neurogenic bladder

Acontractile bladder

Autonomic hyperreflexia of bladder

Cord bladder

Detrusor hyperreflexia

344.8    Other specified paralytic syndromes

344.81  Locked-in state

344.89  Other specified paralytic syndrome

344.9    Paralysis, unspecified

345       Epilepsy

The following fifth-digit subclassification is for use with categories 345.0, .1, .4-.9:

0 without mention of intractable epilepsy

1 with intractable epilepsy

Excludes:          progressive myoclonic epilepsy (333.2)

345.0    Generalized nonconvulsive epilepsy

Absences:

atonic

typical

Minor epilepsy

Petit mal

Pykno-epilepsy

Seizures:

akinetic

atonic

345.1    Generalized convulsive epilepsy

Epileptic seizures:

clonic

myoclonic

tonic

tonic-clonic

Grand mal

Major epilepsy

Excludes:          convulsions:

NOS (780.3)

infantile (780.3)

newborn (779.0)

infantile spasms (345.6)

345.2    Petit mal status

Epileptic absence status

345.3    Grand mal status

Status epilepticus NOS

Excludes:          epilepsia partialis continua (345.7) status:

psychomotor (345.7)

temporal lobe (345.7)

345.4    Partial epilepsy, with impairment of consciousness

Epilepsy:

limbic system

partial:

secondarily generalized

with memory and ideational disturbances

psychomotor

psychosensory

temporal lobe

Epileptic automatism

345.5    Partial epilepsy, without mention of impairment of consciousness

Epilepsy:

Bravais-Jacksonian NOS

focal (motor) NOS

Jacksonian NOS

motor partial

partial NOS

sensory-induced

somatomotor

somatosensory

visceral

visual

345.6    Infantile spasms

Hypsarrhythmia

Lightning spasms

Salaam attacks

Excludes:          salaam tic (781.0)

345.7    Epilepsia partialis continua

Kojevnikov's epilepsy

345.8    Other forms of epilepsy

Epilepsy:

cursive [running]

gelastic

345.9    Epilepsy, unspecified

Epileptic convulsions, fits, or seizures NOS

Excludes:          convulsive seizure or fit NOS (780.3)

346       Migraine

The following fifth-digit subclassification is for use with category 346:

0 without mention of intractable migraine

1 with intractable migraine, so stated

346.0    Classical migraine

Migraine preceded or accompanied by transient focal neurological phenomena

Migraine with aura

346.1    Common migraine

Atypical migraine

Sick headache

346.2    Variants of migraine

Cluster headache

Histamine cephalgia

Horton's neuralgia

Migraine:

abdominal

basilar

lower half

retinal

Neuralgia:

ciliary

migrainous

346.8    Other forms of migraine

Migraine:

hemiplegic

ophthalmoplegic

346.9    Migraine, unspecified

347       Cataplexy and narcolepsy

347.0    Narcolepsy

347.00  Without cataplexy

Narcolepsy NOS

347.01  With cataplexy

347.1    Narcolepsy in conditions classified elsewhere

Code first underlying condition

347.10  Without cataplexy

347.11  With cataplexy 

348       Other conditions of brain

348.0    Cerebral cysts

Arachnoid cyst

Porencephalic cyst

Porencephaly, acquired

Pseudoporencephaly

348.1    Anoxic brain damage

Excludes:          that occurring in:

abortion (634-638 with .7, 639.8)

ectopic or molar pregnancy (639.8)

labor or delivery (668.2, 669.4)

that of newborn (767.0, 768.0-768.9, 772.1-772.2)

Use additional E code to identify cause

348.2    Benign intracranial hypertension

Pseudotumor cerebri

Excludes:          hypertensive encephalopathy (437.2)

348.3    Encephalopathy, not elsewhere classified

348.30  Encephalopathy, unspecified

348.31  Metabolic encephalopathy

Septic encephalopathy

348.39  Other encephalopathy

Excludes:          encephalopathy:

alcoholic (291.2)

hepatic (572.2)

hypertensive (437.2)

toxic (349.82)

348.4    Compression of brain

Compression brain (stem)

Herniation brain (stem)

Posterior fossa compression syndrome

348.5    Cerebral edema

348.8    Other conditions of brain

Cerebral:

calcification

fungus

348.9    Unspecified condition of brain

349       Other and unspecified disorders of the nervous system

349.0    Reaction to spinal or lumbar puncture

Headache following lumbar puncture

349.1    Nervous system complications from surgically implanted device

Excludes:          immediate postoperative complications (997.00-997.09)

mechanical complications of nervous system device (996.2)

349.2    Disorders of meninges, not elsewhere classified

Adhesions, meningeal (cerebral) (spinal)

Cyst, spinal meninges

Meningocele, acquired

Pseudomeningocele, acquired

349.8    Other specified disorders of nervous system

349.81  Cerebrospinal fluid rhinorrhea

Excludes:          cerebrospinal fluid otorrhea (388.61)

349.82  Toxic encephalopathy

Use additional E code to identify cause

349.89  Other

349.9    Unspecified disorders of nervous system

Disorder of nervous system (central) NOS

DISORDERS OF THE PERIPHERAL NERVOUS SYSTEM (350-359)

Excludes:         diseases of:

acoustic [8th] nerve (388.5)

oculomotor [3rd, 4th, 6th] nerves (378.0-378.9)

optic [2nd] nerve (377.0-377.9)

peripheral autonomic nerves (337.0-337.9)

neuralgia NOS or "rheumatic" (729.2)

neuritis NOS or "rheumatic" (729.2)

radiculitis NOS or "rheumatic" (729.2)

peripheral neuritis in pregnancy (646.4)

350       Trigeminal nerve disorders

Includes:           disorders of 5th cranial nerve

350.1    Trigeminal neuralgia

Tic douloureux

Trifacial neuralgia

Trigeminal neuralgia NOS

Excludes:          postherpetic (053.12)

350.2    Atypical face pain

350.8    Other specified trigeminal nerve disorders

350.9    Trigeminal nerve disorder, unspecified

351       Facial nerve disorders

Includes:           disorders of 7th cranial nerve

Excludes:          that in newborn (767.5)

351.0    Bell's palsy

Facial palsy

351.1    Geniculate ganglionitis

Geniculate ganglionitis NOS

Excludes:          herpetic (053.11)

351.8    Other facial nerve disorders

Facial myokymia

Melkersson's syndrome

351.9    Facial nerve disorder, unspecified

352       Disorders of other cranial nerves

352.0    Disorders of olfactory [1st] nerve

352.1    Glossopharyngeal neuralgia

352.2    Other disorders of glossopharyngeal [9th] nerve

352.3    Disorders of pneumogastric [10th] nerve

Disorders of vagal nerve

Excludes:          paralysis of vocal cords or larynx (478.30-478.34)

352.4    Disorders of accessory [11th] nerve

352.5    Disorders of hypoglossal [12th] nerve

352.6    Multiple cranial nerve palsies

Collet-Sicard syndrome

Polyneuritis cranialis

352.9    Unspecified disorder of cranial nerves

353       Nerve root and plexus disorders

Excludes:          conditions due to:

intervertebral disc disorders (722.0-722.9)

spondylosis (720.0-721.9)

vertebrogenic disorders (723.0-724.9)

353.0    Brachial plexus lesions

Cervical rib syndrome

Costoclavicular syndrome

Scalenus anticus syndrome

Thoracic outlet syndrome

Excludes:          brachial neuritis or radiculitis NOS (723.4)

that in newborn (767.6)

353.1    Lumbosacral plexus lesions

353.2    Cervical root lesions, not elsewhere classified

353.3    Thoracic root lesions, not elsewhere classified

353.4    Lumbosacral root lesions, not elsewhere classified

353.5    Neuralgic amyotrophy

Parsonage-Aldren-Turner syndrome

353.6    Phantom limb (syndrome)

353.8    Other nerve root and plexus disorders

353.9    Unspecified nerve root and plexus disorder

354       Mononeuritis of upper limb and mononeuritis multiplex

354.0    Carpal tunnel syndrome

Median nerve entrapment

Partial thenar atrophy

354.1    Other lesion of median nerve

Median nerve neuritis

354.2    Lesion of ulnar nerve

Cubital tunnel syndrome

Tardy ulnar nerve palsy

354.3    Lesion of radial nerve

Acute radial nerve palsy

354.4    Causalgia of upper limb

Excludes:          causalgia:

NOS (355.9)

lower limb (355.71)

354.5    Mononeuritis multiplex

Combinations of single conditions classifiable to 354 or 355

354.8    Other mononeuritis of upper limb

354.9    Mononeuritis of upper limb, unspecified

355       Mononeuritis of lower limb

355.0    Lesion of sciatic nerve

Excludes:          sciatica NOS (724.3)

355.1    Meralgia paresthetica

Lateral cutaneous femoral nerve of thigh compression or syndrome

355.2    Other lesion of femoral nerve

355.3    Lesion of lateral popliteal nerve

Lesion of common peroneal nerve

355.4    Lesion of medial popliteal nerve

355.5    Tarsal tunnel syndrome

355.6    Lesion of plantar nerve

Morton's metatarsalgia, neuralgia, or neuroma

355.7    Other mononeuritis of lower limb

355.71  Causalgia of lower limb

Excludes:          causalgia:

NOS (355.9)

upper limb (354.4)

355.79  Other mononeuritis of lower limb

355.8    Mononeuritis of lower limb, unspecified

355.9    Mononeuritis of unspecified site

Causalgia NOS

Excludes:          causalgia:

lower limb (355.71)

upper limb (354.4)

356       Hereditary and idiopathic peripheral neuropathy

356.0    Hereditary peripheral neuropathy

Déjérine-Sottas disease

356.1    Peroneal muscular atrophy

Charcot-Marie-Tooth disease

Neuropathic muscular atrophy

356.2    Hereditary sensory neuropathy

356.3    Refsum's disease

Heredopathia atactica polyneuritiformis

356.4    Idiopathic progressive polyneuropathy

356.8    Other specified idiopathic peripheral neuropathy

Supranuclear paralysis

356.9    Unspecified

357       Inflammatory and toxic neuropathy

357.0    Acute infective polyneuritis

Guillain-Barre syndrome

Postinfectious polyneuritis

357.1    Polyneuropathy in collagen vascular disease

Code first underlying disease, as:

disseminated lupus erythematosus (710.0)

polyarteritis nodosa (446.0)

rheumatoid arthritis (714.0)

357.2    Polyneuropathy in diabetes

Code first underlying disease (250.6)

357.3    Polyneuropathy in malignant disease

Code first underlying disease (140.0-208.9)

357.4    Polyneuropathy in other diseases classified elsewhere

Code first underlying disease, as:

amyloidosis (277.3)

beriberi (265.0)

deficiency of B vitamins (266.0-266.9)

diphtheria (032.0-032.9)

hypoglycemia (251.2)

pellagra (265.2)

porphyria (277.1)

sarcoidosis (135)

uremia (585.9)

Excludes:          polyneuropathy in:

herpes zoster (053.13)

mumps (072.72)

357.5    Alcoholic polyneuropathy

357.6    Polyneuropathy due to drugs

Use additional E code to identify drug

357.7    Polyneuropathy due to other toxic agents

Use additional E code to identify toxic agent

357.8    Other

357.81  Chronic inflammatory demyelinating polyneuritis

357.82  Critical illness polyneuropathy

Acute motor neuropathy

357.89  Other inflammatory and toxic neuropathy

357.9    Unspecified

358       Myoneural disorders

358.0    Myasthenia gravis

358.00  Myasthenia gravis without (acute) exacerbation

358.01  Myasthenia gravis with (acute) exacerbation

Myasthenia gravis in crisis

358.1    Myasthenic syndromes in diseases classified elsewhere

Amyotrophy from stated cause classified elsewhere

Eaton-Lambert syndrome from stated cause classified elsewhere

Code first underlying disease, as:

botulism (005.1)

diabetes mellitus (250.6)

hypothyroidism (244.0-244.9)

malignant neoplasm (140.0-208.9)

pernicious anemia (281.0)

thyrotoxicosis (242.0-242.9)

358.2    Toxic myoneural disorders

Use additional E code to identify toxic agent

358.8    Other specified myoneural disorders

358.9    Myoneural disorders, unspecified

359       Muscular dystrophies and other myopathies

Excludes:          idiopathic polymyositis (710.4)

359.0    Congenital hereditary muscular dystrophy

Benign congenital myopathy

Central core disease

Centronuclear myopathy

Myotubular myopathy

Nemaline body disease

Excludes:          arthrogryposis multiplex congenita (754.89)

359.1    Hereditary progressive muscular dystrophy

Muscular dystrophy:

NOS

distal

Duchenne

Erb's

fascioscapulohumeral

Gower's

Landouzy-Déjérine

limb-girdle

ocular

oculopharyngeal

359.2    Myotonic disorders

Dystrophia myotonica

Eulenburg's disease

Myotonia congenita

Paramyotonia congenita

Steinert's disease

Thomsen's disease

359.3    Familial periodic paralysis

Hypokalemic familial periodic paralysis

359.4    Toxic myopathy

Use additional E code to identify toxic agent

359.5    Myopathy in endocrine diseases classified elsewhere

Code first underlying disease, as:

Addison's disease (255.4)

Cushing's syndrome (255.0)

hypopituitarism (253.2)

myxedema (244.0-244.9)

thyrotoxicosis (242.0-242.9)

359.6    Symptomatic inflammatory myopathy in diseases classified elsewhere

Code first underlying disease, as:

amyloidosis (277.3)

disseminated lupus erythematosus (710.0)

malignant neoplasm (140.0-208.9)

polyarteritis nodosa (446.0)

rheumatoid arthritis (714.0)

sarcoidosis (135)

scleroderma (710.1)

Sjögren's disease (710.2)

359.8    Other myopathies

359.81  Critical illness myopathy

Acute necrotizing myopathy

Acute quadriplegic myopathy

Intensive care (ICU) myopathy

Myopathy of critical illness

359.89  Other myopathies

359.9    Myopathy, unspecified

DISORDERS OF THE EYE AND ADNEXA (360-379)

360       Disorders of the globe

Includes:           disorders affecting multiple structures of eye

360.0    Purulent endophthalmitis

360.00  Purulent endophthalmitis, unspecified

360.01  Acute endophthalmitis

360.02  Panophthalmitis

360.03  Chronic endophthalmitis

360.04  Vitreous abscess

360.1    Other endophthalmitis

360.11  Sympathetic uveitis

360.12  Panuveitis

360.13  Parasitic endophthalmitis NOS

360.14  Ophthalmia nodosa

360.19  Other

Phacoanaphylactic endophthalmitis

360.2    Degenerative disorders of globe

360.20  Degenerative disorder of globe, unspecified

360.21  Progressive high (degenerative) myopia

Malignant myopia

360.23  Siderosis

360.24  Other metallosis

Chalcosis

360.29  Other

Excludes:          xerophthalmia (264.7)

360.3    Hypotony of eye

360.30  Hypotony, unspecified

360.31  Primary hypotony

360.32  Ocular fistula causing hypotony

360.33  Hypotony associated with other ocular disorders

360.34  Flat anterior chamber

360.4    Degenerated conditions of globe

360.40  Degenerated globe or eye, unspecified

360.41  Blind hypotensive eye

Atrophy of globe

Phthisis bulbi

360.42  Blind hypertensive eye

Absolute glaucoma

360.43  Hemophthalmos, except current injury

Excludes:          traumatic (871.0-871.9, 921.0-921.9)

360.44  Leucocoria

360.5    Retained (old) intraocular foreign body, magnetic

Excludes:          current penetrating injury with magnetic foreign body (871.5)

retained (old) foreign body of orbit (376.6)

360.50  Foreign body, magnetic, intraocular, unspecified

360.51  Foreign body, magnetic, in anterior chamber

360.52  Foreign body, magnetic, in iris or ciliary body

360.53  Foreign body, magnetic, in lens

360.54  Foreign body, magnetic, in vitreous

360.55  Foreign body, magnetic, in posterior wall

360.59  Foreign body, magnetic, in other or multiple sites

360.6    Retained (old) intraocular foreign body, nonmagnetic

Retained (old) foreign body:

NOS

nonmagnetic

Excludes:          current penetrating injury with (nonmagnetic) foreign body (871.6)

retained (old) foreign body in orbit (376.6)

360.60  Foreign body, intraocular, unspecified

360.61  Foreign body in anterior chamber

360.62  Foreign body in iris or ciliary body

360.63  Foreign body in lens

360.64  Foreign body in vitreous

360.65  Foreign body in posterior wall

360.69  Foreign body in other or multiple sites

360.8    Other disorders of globe

360.81  Luxation of globe

360.89  Other

360.9    Unspecified disorder of globe

361       Retinal detachments and defects

361.0    Retinal detachment with retinal defect

Rhegmatogenous retinal detachment

Excludes:          detachment of retinal pigment epithelium (362.42-362.43)

retinal detachment (serous) (without defect) (361.2)

361.00  Retinal detachment with retinal defect, unspecified

361.01  Recent detachment, partial, with single defect

361.02  Recent detachment, partial, with multiple defects

361.03  Recent detachment, partial, with giant tear

361.04  Recent detachment, partial, with retinal dialysis

Dialysis (juvenile) of retina (with detachment)

361.05  Recent detachment, total or subtotal

361.06  Old detachment, partial

Delimited old retinal detachment

361.07  Old detachment, total or subtotal

361.1    Retinoschisis and retinal cysts

Excludes:          juvenile retinoschisis (362.73)

microcystoid degeneration of retina (362.62)

parasitic cyst of retina (360.13)

361.10  Retinoschisis, unspecified

361.11  Flat retinoschisis

361.12  Bullous retinoschisis

361.13  Primary retinal cysts

361.14  Secondary retinal cysts

361.19  Other

Pseudocyst of retina

361.2    Serous retinal detachment

Retinal detachment without retinal defect

Excludes:          central serous retinopathy (362.41)

retinal pigment epithelium detachment (362.42-362.43)

361.3    Retinal defects without detachment

Excludes:          chorioretinal scars after surgery for detachment (363.30-363.35)

peripheral retinal degeneration without defect (362.60-362.66)

361.30  Retinal defect, unspecified

Retinal break(s) NOS

361.31  Round hole of retina without detachment

361.32  Horseshoe tear of retina without detachment

Operculum of retina without mention of detachment

361.33  Multiple defects of retina without detachment

361.8    Other forms of retinal detachment

361.81  Traction detachment of retina

Traction detachment with vitreoretinal organization

361.89  Other

361.9    Unspecified retinal detachment

362       Other retinal disorders

Excludes:          chorioretinal scars (363.30-363.35)

chorioretinitis (363.0-363.2)

362.0    Diabetic retinopathy

Code first diabetes (250.5)

362.01  Background diabetic retinopathy

Diabetic retinal microaneurysms

Diabetic retinopathy NOS

362.02  Proliferative diabetic retinopathy

362.03  Nonproliferative diabetic retinopathy NOS

362.04  Mild nonproliferative diabetic retinopathy

362.05  Moderate nonproliferative diabetic retinopathy

362.06  Severe nonproliferative diabetic retinopathy

362.07  Diabetic macular edema

Diabetic retinal edema

Note: Code 362.07 must be used with a code for diabetic retinopathy (362.01-362.06)

362.1    Other background retinopathy and retinal vascular changes

362.10  Background retinopathy, unspecified

362.11  Hypertensive retinopathy

362.12  Exudative retinopathy

Coats' syndrome

362.13  Changes in vascular appearance

Vascular sheathing of retina

Use additional code for any associated atherosclerosis (440.8)

362.14  Retinal microaneurysms NOS

362.15  Retinal telangiectasia

362.16  Retinal neovascularization NOS

Neovascularization:

choroidal

subretinal

362.17  Other intraretinal microvascular abnormalities

Retinal varices

362.18  Retinal vasculitis

Eales' disease

Retinal:

arteritis

endarteritis

perivasculitis

phlebitis

362.2    Other proliferative retinopathy

362.21  Retrolental fibroplasia

362.29  Other nondiabetic proliferative retinopathy

362.3    Retinal vascular occlusion

362.30  Retinal vascular occlusion, unspecified

362.31  Central retinal artery occlusion

362.32  Arterial branch occlusion

362.33  Partial arterial occlusion

Hollenhorst plaque

Retinal microembolism

362.34  Transient arterial occlusion

Amaurosis fugax

362.35  Central retinal vein occlusion

362.36  Venous tributary (branch) occlusion

362.37  Venous engorgement

Occlusion:

of retinal vein

incipient of retinal vein

partial of retinal vein

362.4    Separation of retinal layers

Excludes:          retinal detachment (serous) (361.2)

rhegmatogenous (361.00-361.07)

362.40  Retinal layer separation, unspecified

362.41  Central serous retinopathy

362.42  Serous detachment of retinal pigment epithelium

Exudative detachment of retinal pigment epithelium

362.43  Hemorrhagic detachment of retinal pigment epithelium

362.5    Degeneration of macula and posterior pole

Excludes:          degeneration of optic disc (377.21-377.24)

hereditary retinal degeneration [dystrophy] (362.70-362.77)

362.50  Macular degeneration (senile), unspecified

362.51  Nonexudative senile macular degeneration

Senile macular degeneration:

atrophic

dry

362.52  Exudative senile macular degeneration

Kuhnt-Junius degeneration

Senile macular degeneration:

disciform

wet

362.53  Cystoid macular degeneration

Cystoid macular edema

362.54  Macular cyst, hole, or pseudohole

362.55  Toxic maculopathy

Use additional E to identify drug, if drug induced

362.56  Macular puckering

Preretinal fibrosis

362.57  Drusen (degenerative)

362.6    Peripheral retinal degenerations

Excludes:          hereditary retinal degeneration [dystrophy] (362.70-362.77)

retinal degeneration with retinal defect (361.00-361.07)

362.60  Peripheral retinal degeneration, unspecified

362.61  Paving stone degeneration

362.62  Microcystoid degeneration

Blessig's cysts

Iwanoff's cysts

362.63  Lattice degeneration

Palisade degeneration of retina

362.64  Senile reticular degeneration

362.65  Secondary pigmentary degeneration

Pseudoretinitis pigmentosa

362.66  Secondary vitreoretinal degenerations

362.7    Hereditary retinal dystrophies

362.70  Hereditary retinal dystrophy, unspecified

362.71  Retinal dystrophy in systemic or cerebroretinal lipidoses

Code first underlying disease, as:

cerebroretinal lipidoses (330.1)

systemic lipidoses (272.7)

362.72  Retinal dystrophy in other systemic disorders and syndromes

Code first underlying disease, as:

Bassen-Kornzweig syndrome (272.5)

Refsum's disease (356.3)

362.73  Vitreoretinal dystrophies

Juvenile retinoschisis

362.74  Pigmentary retinal dystrophy

Retinal dystrophy, albipunctate

Retinitis pigmentosa

362.75  Other dystrophies primarily involving the sensory retina

Progressive cone (-rod) dystrophy

Stargardt's disease

362.76  Dystrophies primarily involving the retinal pigment epithelium

Fundus flavimaculatus

Vitelliform dystrophy

362.77  Dystrophies primarily involving Bruch's membrane

Dystrophy:

hyaline

pseudoinflammatory foveal

Hereditary drusen

362.8    Other retinal disorders

Excludes:          chorioretinal inflammations (363.0-363.2)

chorioretinal scars (363.30-363.35)

362.81  Retinal hemorrhage

Hemorrhage:

preretinal

retinal (deep) (superficial)

subretinal

362.82  Retinal exudates and deposits

362.83  Retinal edema

Retinal:

cotton wool spots

edema (localized) (macular) (peripheral)

362.84  Retinal ischemia

362.85  Retinal nerve fiber bundle defects

362.89  Other retinal disorders

362.9    Unspecified retinal disorder

363       Chorioretinal inflammations, scars, and other disorders of choroid

363.0    Focal chorioretinitis and focal retinochoroiditis

Excludes:          focal chorioretinitis or retinochoroiditis in:

histoplasmosis (115.02, 115.12, 115.92)

toxoplasmosis (130.2)

congenital infection (771.2)

363.00  Focal chorioretinitis, unspecified

Focal:

choroiditis or chorioretinitis NOS

retinitis or retinochoroiditis NOS

363.01  Focal choroiditis and chorioretinitis, juxtapapillary

363.03  Focal choroiditis and chorioretinitis of other posterior pole

363.04  Focal choroiditis and chorioretinitis, peripheral

363.05  Focal retinitis and retinochoroiditis, juxtapapillary

Neuroretinitis

363.06  Focal retinitis and retinochoroiditis, macular or paramacular

363.07  Focal retinitis and retinochoroiditis of other posterior pole

363.08  Focal retinitis and retinochoroiditis, peripheral

363.1    Disseminated chorioretinitis and disseminated retinochoroiditis

Excludes:          disseminated choroiditis or chorioretinitis in secondary syphilis (091.51)

neurosyphilitic disseminated retinitis or retinochoroiditis (094.83)

retinal (peri)vasculitis (362.18)

363.10  Disseminated chorioretinitis, unspecified

Disseminated:

choroiditis or chorioretinitis NOS

retinitis or retinochoroiditis NOS

363.11  Disseminated choroiditis and chorioretinitis, posterior pole

363.12  Disseminated choroiditis and chorioretinitis, peripheral

363.13  Disseminated choroiditis and chorioretinitis, generalized

Code first any underlying disease, as:

tuberculosis (017.3)

363.14  Disseminated retinitis and retinochoroiditis, metastatic

363.15  Disseminated retinitis and retinochoroiditis, pigment epitheliopathy

Acute posterior multifocal placoid pigment epitheliopathy

363.2    Other and unspecified forms of chorioretinitis and retinochoroiditis

Excludes:          panophthalmitis (360.02)

sympathetic uveitis (360.11)

uveitis NOS (364.3)

363.20  Chorioretinitis, unspecified

Choroiditis NOS

Retinitis NOS

Uveitis, posterior NOS

363.21  Pars planitis

Posterior cyclitis

363.22  Harada's disease

363.3    Chorioretinal scars

Scar (postinflammatory) (postsurgical) (posttraumatic):

choroid

retina

363.30  Chorioretinal scar, unspecified

363.31  Solar retinopathy

363.32  Other macular scars

363.33  Other scars of posterior pole

363.34  Peripheral scars

363.35  Disseminated scars

363.4    Choroidal degenerations

363.40  Choroidal degeneration, unspecified

Choroidal sclerosis NOS

363.41  Senile atrophy of choroid

363.42  Diffuse secondary atrophy of choroid

363.43  Angioid streaks of choroid

363.5    Hereditary choroidal dystrophies

Hereditary choroidal atrophy:

partial [choriocapillaris]

total [all vessels]

363.50  Hereditary choroidal dystrophy or atrophy, unspecified

363.51  Circumpapillary dystrophy of choroid, partial

363.52  Circumpapillary dystrophy of choroid, total

Helicoid dystrophy of choroid

363.53  Central dystrophy of choroid, partial

Dystrophy, choroidal:

central areolar

circinate

363.54  Central choroidal atrophy, total

Dystrophy, choroidal:

central gyrate

serpiginous

363.55  Choroideremia

363.56  Other diffuse or generalized dystrophy, partial

Diffuse choroidal sclerosis

363.57  Other diffuse or generalized dystrophy, total

Generalized gyrate atrophy, choroid

363.6    Choroidal hemorrhage and rupture

363.61  Choroidal hemorrhage, unspecified

363.62  Expulsive choroidal hemorrhage

363.63  Choroidal rupture

363.7    Choroidal detachment

363.70  Choroidal detachment, unspecified

363.71  Serous choroidal detachment

363.72  Hemorrhagic choroidal detachment

363.8    Other disorders of choroid

363.9    Unspecified disorder of choroid

364       Disorders of iris and ciliary body

364.0    Acute and subacute iridocyclitis

Anterior uveitis, acute, subacute

Cyclitis, acute, subacute

Iridocyclitis, acute, subacute

Iritis, acute, subacute

Excludes:          gonococcal (098.41)

herpes simplex (054.44)

herpes zoster (053.22)

364.00  Acute and subacute iridocyclitis, unspecified

364.01  Primary iridocyclitis

364.02  Recurrent iridocyclitis

364.03  Secondary iridocyclitis, infectious

364.04  Secondary iridocyclitis, noninfectious

Aqueous:

cells

fibrin

flare

364.05  Hypopyon

364.1    Chronic iridocyclitis

Excludes:          posterior cyclitis (363.21)

364.10  Chronic iridocyclitis, unspecified

364.11  Chronic iridocyclitis in diseases classified elsewhere

Code first underlying disease, as:

sarcoidosis (135)

tuberculosis (017.3)

Excludes:          syphilitic iridocyclitis (091.52)

364.2    Certain types of iridocyclitis

Excludes:          posterior cyclitis (363.21)

sympathetic uveitis (360.11)

364.21  Fuchs' heterochromic cyclitis

364.22  Glaucomatocyclitic crises

364.23  Lens-induced iridocyclitis

364.24  Vogt-Koyanagi syndrome

364.3    Unspecified iridocyclitis

Uveitis NOS

364.4    Vascular disorders of iris and ciliary body

364.41  Hyphema

Hemorrhage of iris or ciliary body

364.42  Rubeosis iridis

Neovascularization of iris or ciliary body

364.5    Degenerations of iris and ciliary body

364.51  Essential or progressive iris atrophy

364.52  Iridoschisis

364.53  Pigmentary iris degeneration

Acquired heterochromia of iris

Pigment dispersion syndrome of iris

Translucency of iris

364.54  Degeneration of pupillary margin

Atrophy of sphincter of iris

Ectropion of pigment epithelium of iris

364.55  Miotic cysts of pupillary margin

364.56  Degenerative changes of chamber angle

364.57  Degenerative changes of ciliary body

364.59  Other iris atrophy

Iris atrophy (generalized) (sector shaped)

364.6    Cysts of iris, ciliary body, and anterior chamber

Excludes:          miotic pupillary cyst (364.55)

parasitic cyst (360.13)

364.60  Idiopathic cysts

364.61  Implantation cysts

Epithelial down-growth, anterior chamber

Implantation cysts (surgical) (traumatic)

364.62  Exudative cysts of iris or anterior chamber

364.63  Primary cyst of pars plana

364.64  Exudative cyst of pars plana

364.7    Adhesions and disruptions of iris and ciliary body

Excludes:          flat anterior chamber (360.34)

364.70  Adhesions of iris, unspecified

Synechiae (iris) NOS

364.71  Posterior synechiae

364.72  Anterior synechiae

364.73  Goniosynechiae

Peripheral anterior synechiae

364.74  Pupillary membranes

Iris bombé

Pupillary:

occlusion

seclusion

364.75  Pupillary abnormalities

Deformed pupil

Ectopic pupil

Rupture of sphincter, pupil

364.76  Iridodialysis

364.77  Recession of chamber angle

364.8    Other disorders of iris and ciliary body

Prolapse of iris NOS

Excludes:          prolapse of iris in recent wound (871.1)

364.9    Unspecified disorder of iris and ciliary body

365       Glaucoma

Excludes:          blind hypertensive eye [absolute glaucoma] (360.42)

congenital glaucoma (743.20-743.22)

365.0    Borderline glaucoma [glaucoma suspect]

365.00  Preglaucoma, unspecified

365.01  Open angle with borderline findings

Open angle with:

borderline intraocular pressure

cupping of optic discs

365.02  Anatomical narrow angle

365.03  Steroid responders

365.04  Ocular hypertension

365.1    Open-angle glaucoma

365.10  Open-angle glaucoma, unspecified

Wide-angle glaucoma NOS

365.11  Primary open angle glaucoma

Chronic simple glaucoma

365.12  Low tension glaucoma

365.13  Pigmentary glaucoma

365.14  Glaucoma of childhood

Infantile or juvenile glaucoma

365.15  Residual stage of open angle glaucoma

365.2    Primary angle-closure glaucoma

365.20  Primary angle-closure glaucoma, unspecified

365.21  Intermittent angle-closure glaucoma

Angle-closure glaucoma:

interval

subacute

365.22  Acute angle-closure glaucoma

365.23  Chronic angle-closure glaucoma

365.24  Residual stage of angle-closure glaucoma

365.3    Corticosteroid-induced glaucoma

365.31  Glaucomatous stage

365.32  Residual stage

365.4    Glaucoma associated with congenital anomalies, dystrophies, and systemic syndromes

365.41  Glaucoma associated with chamber angle anomalies

Code first associated disorder, as:

Axenfeld's anomaly (743.44)

Rieger's anomaly or syndrome (743.44)

365.42  Glaucoma associated with anomalies of iris

Code first associated disorder, as:

aniridia (743.45)

essential iris atrophy (364.51)

365.43  Glaucoma associated with other anterior segment anomalies

Code first associated disorder, as:

microcornea (743.41)

365.44  Glaucoma associated with systemic syndromes

Code first associated disease, as:

neurofibromatosis (237.7)

Sturge-Weber (-Dimitri) syndrome (759.6)

365.5    Glaucoma associated with disorders of the lens

365.51  Phacolytic glaucoma

Use additional code for associated hypermature cataract (366.18)

365.52  Pseudoexfoliation glaucoma

Use additional code for associated pseudoexfoliation of capsule (366.11)

365.59  Glaucoma associated with other lens disorders

Use additional code for associated disorder, as:

dislocation of lens (379.33-379.34)

spherophakia (743.36)

365.6    Glaucoma associated with other ocular disorders

365.60  Glaucoma associated with unspecified ocular disorder

365.61  Glaucoma associated with pupillary block

Use additional code for associated disorder, as:

seclusion of pupil [iris bombé] (364.74)

365.62  Glaucoma associated with ocular inflammations

Use additional code for associated disorder, as:

glaucomatocyclitic crises (364.22)

iridocyclitis (364.0-364.3)

365.63  Glaucoma associated with vascular disorders

Use additional code for associated disorder, as:

central retinal vein occlusion (362.35)

hyphema (364.41)

365.64  Glaucoma associated with tumors or cysts

Use additional code for associated disorder, as:

benign neoplasm (224.0-224.9)

epithelial down-growth (364.61)

malignant neoplasm (190.0-190.9)

365.65  Glaucoma associated with ocular trauma

Use additional code for associated condition, as:

contusion of globe (921.3)

recession of chamber angle (364.77)

365.8    Other specified forms of glaucoma

365.81  Hypersecretion glaucoma

365.82  Glaucoma with increased episcleral venous pressure

365.83  Aqueous misdirection

Malignant glaucoma

365.89  Other specified glaucoma

365.9    Unspecified glaucoma

366       Cataract

Excludes:          congenital cataract (743.30-743.34)

366.0    Infantile, juvenile, and presenile cataract

366.00  Nonsenile cataract, unspecified

366.01  Anterior subcapsular polar cataract

366.02  Posterior subcapsular polar cataract

366.03  Cortical, lamellar, or zonular cataract

366.04  Nuclear cataract

366.09  Other and combined forms of nonsenile cataract

366.1    Senile cataract

366.10  Senile cataract, unspecified

366.11  Pseudoexfoliation of lens capsule

366.12  Incipient cataract

Cataract:

coronary

immature NOS

punctate

Water clefts

366.13  Anterior subcapsular polar senile cataract

366.14  Posterior subcapsular polar senile cataract

366.15  Cortical senile cataract

366.16  Nuclear sclerosis

Cataracta brunescens

Nuclear cataract

366.17  Total or mature cataract

366.18  Hypermature cataract

Morgagni cataract

366.19  Other and combined forms of senile cataract

366.2    Traumatic cataract

366.20  Traumatic cataract, unspecified

366.21  Localized traumatic opacities

Vossius' ring

366.22  Total traumatic cataract

366.23  Partially resolved traumatic cataract

366.3    Cataract secondary to ocular disorders

366.30  Cataracta complicata, unspecified

366.31  Glaucomatous flecks (subcapsular)

Code first underlying glaucoma (365.0-365.9)

366.32  Cataract in inflammatory disorders

Code first underlying condition, as:

chronic choroiditis (363.0-363.2)

366.33  Cataract with neovascularization

Code first underlying condition, as:

chronic iridocyclitis (364.10)

366.34  Cataract in degenerative disorders

Sunflower cataract

Code first underlying condition, as:

chalcosis (360.24)

degenerative myopia (360.21)

pigmentary retinal dystrophy (362.74)

366.4    Cataract associated with other disorders

366.41  Diabetic cataract

Code first diabetes (250.5)

366.42  Tetanic cataract

Code first underlying disease as:

calcinosis (275.40)

hypoparathyroidism (252.1)

366.43  Myotonic cataract

Code first underlying disorder (359.2)

366.44  Cataract associated with other syndromes

Code first underlying condition, as:

craniofacial dysostosis (756.0)

galactosemia (271.1)

366.45  Toxic cataract

Drug-induced cataract

Use additional E to identify drug or other toxic substance

366.46  Cataract associated with radiation and other physical influences

Use additional E to identify cause

366.5    After-cataract

366.50  After-cataract, unspecified

Secondary cataract NOS

366.51  Soemmering's ring

366.52  Other after-cataract, not obscuring vision

366.53  After-cataract, obscuring vision

366.8    Other cataract

Calcification of lens

366.9    Unspecified cataract

367       Disorders of refraction and accommodation

367.0    Hypermetropia

Far-sightedness

Hyperopia

367.1    Myopia

Near-sightedness

367.2    Astigmatism

367.20  Astigmatism, unspecified

367.21  Regular astigmatism

367.22  Irregular astigmatism

367.3    Anisometropia and aniseikonia

367.31  Anisometropia

367.32  Aniseikonia

367.4    Presbyopia

367.5    Disorders of accommodation

367.51  Paresis of accommodation

Cycloplegia

367.52  Total or complete internal ophthalmoplegia

367.53  Spasm of accommodation

367.8    Other disorders of refraction and accommodation

367.81  Transient refractive change

367.89  Other

Drug-induced disorders of refraction and accommodation

Toxic disorders of refraction and accommodation

367.9    Unspecified disorder of refraction and accommodation

368       Visual disturbances

Excludes:          electrophysiological disturbances (794.11-794.14)

368.0    Amblyopia ex anopsia

368.00  Amblyopia, unspecified

368.01  Strabismic amblyopia

Suppression amblyopia

368.02  Deprivation amblyopia

368.03  Refractive amblyopia

368.1    Subjective visual disturbances

368.10  Subjective visual disturbance, unspecified

368.11  Sudden visual loss

368.12  Transient visual loss

Concentric fading

Scintillating scotoma

368.13  Visual discomfort

Asthenopia

Eye strain

Photophobia

368.14  Visual distortions of shape and size

Macropsia

Metamorphopsia

Micropsia

368.15  Other visual distortions and entoptic phenomena

Photopsia

Refractive:

diplopia

polyopia

Visual halos

368.16  Psychophysical visual disturbances

Visual:

agnosia

disorientation syndrome

hallucinations

368.2    Diplopia

Double vision

368.3    Other disorders of binocular vision

368.30  Binocular vision disorder, unspecified

368.31  Suppression of binocular vision

368.32  Simultaneous visual perception without fusion

368.33  Fusion with defective stereopsis

368.34  Abnormal retinal correspondence

368.4    Visual field defects

368.40  Visual field defect, unspecified

368.41  Scotoma involving central area

Scotoma:

central

centrocecal

paracentral

368.42  Scotoma of blind spot area

Enlarged:

angioscotoma

blind spot

Paracecal scotoma

368.43  Sector or arcuate defects

Scotoma:

arcuate

Bjerrum

Seidel

368.44  Other localized visual field defect

Scotoma:

NOS

ring

Visual field defect:

nasal step

peripheral

368.45  Generalized contraction or constriction

368.46  Homonymous bilateral field defects

Hemianopsia (altitudinal) (homonymous)

Quadrant anopia

368.47  Heteronymous bilateral field defects

Hemianopsia:

binasal

bitemporal

368.5    Color vision deficiencies

Color blindness

368.51  Protan defect

Protanomaly

Protanopia

368.52  Deutan defect

Deuteranomaly

Deuteranopia

368.53  Tritan defect

Tritanomaly

Tritanopia

368.54  Achromatopsia

Monochromatism (cone) (rod)

368.55  Acquired color vision deficiencies

368.59  Other color vision deficiencies

368.6    Night blindness

368.60  Night blindness, unspecified

368.61  Congenital night blindness

Hereditary night blindness

Oguchi's disease

368.62  Acquired night blindness

Excludes:          that due to vitamin A deficiency (264.5)

368.63  Abnormal dark adaptation curve

Abnormal threshold of cones or rods

Delayed adaptation of cones or rods

368.69  Other night blindness

368.8    Other specified visual disturbances

Blurred vision NOS

368.9    Unspecified visual disturbance

369       Blindness and low vision

Excludes:          correctable impaired vision due to refractive errors (367.0-367.9)

Note:    Visual impairment refers to a functional limitation of the eye (e.g., limited visual acuity or visual field). It should be distinguished from visual disability, indicating a limitation of the abilities of the individual (e.g., limited reading skills, vocational skills), and from visual handicap, indicating a limitation of personal and socioeconomic independence (e.g., limited mobility, limited employability).

The levels of impairment defined in the table after 369.9 are based on the recommendations of the WHO Study Group on Prevention of Blindness (Geneva, November 6-10, 1972; WHO Technical Report Series 518), and of the International Council of Ophthalmology (1976).

Note that definitions of blindness vary in different settings.

For international reporting, WHO defines blindness as profound impairment. This definition can be applied to blindness of one eye (369.1, 369.6) and to blindness of the individual (369.0).

For determination of benefits in the U.S.A., the definition of legal blindness as severe impairment is often used.  This definition applies to blindness of the individual only.

369.0    Profound impairment, both eyes

369.00  Impairment level not further specified

Blindness:

NOS according to WHO definition

both eyes

369.01  Better eye:  total impairment; lesser eye:  total impairment

369.02  Better eye:  near-total impairment; lesser eye:  not further specified

369.03  Better eye:  near-total impairment; lesser eye:  total impairment

369.04  Better eye:  near-total impairment; lesser eye:  near-total impairment

369.05  Better eye:  profound impairment; lesser eye:  not further specified

369.06  Better eye:  profound impairment; lesser eye:  total impairment

369.07  Better eye:  profound impairment; lesser eye:  near-total impairment

369.08  Better eye:  profound impairment; lesser eye:  profound impairment

369.1    Moderate or severe impairment, better eye, profound impairment lesser eye

369.10  Impairment level not further specified

Blindness, one eye, low vision other eye

369.11  Better eye:  severe impairment; lesser eye:  blind, not further specified

369.12  Better eye:  severe impairment; lesser eye:  total impairment

369.13  Better eye:  severe impairment; lesser eye:  near-total impairment

369.14  Better eye:  severe impairment; lesser eye:  profound impairment

369.15  Better eye:  moderate impairment; lesser eye:  blind, not further specified

369.16  Better eye:  moderate impairment; lesser eye:  total impairment

369.17  Better eye:  moderate impairment; lesser eye:  near-total impairment

369.18  Better eye:  moderate impairment; lesser eye:  profound impairment

369.2    Moderate or severe impairment, both eyes

369.20  Impairment level not further specified

Low vision, both eyes NOS

369.21  Better eye:  severe impairment; lesser eye:  not further specified

369.22  Better eye:  severe impairment; lesser eye:  severe impairment

369.23  Better eye:  moderate impairment; lesser eye:  not further specified

369.24  Better eye:  moderate impairment; lesser eye:  severe impairment

369.25  Better eye:  moderate impairment; lesser eye:  moderate impairment

369.3    Unqualified visual loss, both eyes

Excludes:          blindness NOS:

legal [U.S.A. definition] (369.4)

WHO definition (369.00)

369.4    Legal blindness, as defined in U.S.A.

Blindness NOS according to U.S.A. definition

Excludes:          legal blindness with specification of impairment level (369.01-369.08, 369.11-369.14, 369.21-369.22)

369.6    Profound impairment, one eye

369.60  Impairment level not further specified

Blindness, one eye

369.61  One eye:  total impairment; other eye:  not specified

369.62  One eye:  total impairment; other eye:  near-normal vision

369.63  One eye:  total impairment; other eye:  normal vision

369.64  One eye:  near-total impairment; other eye:  not specified

369.65  One eye:  near-total impairment; other eye:  near-normal vision

369.66  One eye:  near-total impairment; other eye:  normal vision

369.67  One eye:  profound impairment; other eye:  not specified

369.68  One eye:  profound impairment; other eye:  near-normal vision

369.69  One eye:  profound impairment; other eye:  normal vision

369.7    Moderate or severe impairment, one eye

369.70  Impairment level not further specified

Low vision, one eye

369.71  One eye:  severe impairment; other eye:  not specified

369.72  One eye:  severe impairment; other eye:  near-normal vision

369.73  One eye:  severe impairment; other eye:  normal vision

369.74  One eye:  moderate impairment; other eye:  not specified

369.75  One eye:  moderate impairment; other eye:  near-normal vision

369.76  One eye:  moderate impairment; other eye:  normal vision

369.8    Unqualified visual loss, one eye

369.9    Unspecified visual loss

----------------------------------------------------------------------
                   |                                   |  Additional
Classification     |   LEVELS OF VISUAL IMPAIRMENT     |   descriptors
-------------------------------------------------------|   which may
        |          | Visual acuity and/or visual field |   be en-
"legal" |  WHO     |  limitation (whichever is worse)  |   countered
--------|----------|-----------------------------------|--------------
        |          |                                   |
        |          |     RANGE OF NORMAL VISION        |
        |          | 20/10  20/13  20/16  20/20  20/25 |
        | (NEAR-)  |  2.0    1.6    1.25   1.0    0.8  |
        | NORMAL   |-----------------------------------|--------------
        | VISION   |                                   |
        |          |     NEAR-NORMAL VISION            |
        |          |        20/30  20/40  20/50  20/60 |
        |          |  0.7    0.6    0.5    0.4    0.3  |
        |----------|-----------------------------------|--------------
        |          |     MODERATE VISUAL IMPAIRMENT    |
        |          | 20/70  20/80  20/100 20/125 20/160| Moderate 
        | LOW      |         0.25   0.20   0.16   0.12 |    low vision
--------| VISION   |-----------------------------------|--------------
        |          |     SEVERE VISUAL IMPAIRMENT      | Severe
        |          | 20/200 20/250 20/320 20/400       |    low vision,
        |          |  0.10   0.08   0.06   0.05        | "Legal"
        |          | Visual field: 20 degrees or less  |    blindness
        |----------|-----------------------------------|--------------
LEGAL   |          |      PROFOUND VISUAL IMPAIRMENT   | Profound
BLIND-  |          | 20/500 20/630 20/800 20/1000      |    low vision,
NESS    |          |  0.04   0.03   0.025  0.02        | Moderate
(U.S.A.)|          |                                   |    blindness
        | BLINDNESS|  Count fingers at: less than 3m   |
        |          |                        (10 ft)    |
        |          |  Visual field: 10 degrees or less |   
        |          |-----------------------------------|--------------
        |          |    NEAR-TOTAL VISUAL IMPAIRMENT   | Severe
        |          | Visual acuity: less than 0.02     |    blindness,
        |          |                   (20/1000)       |
        |          |                                   |
both    |  (WHO)   | Count fingers: 1m (3 ft) or less  |
eyes    |          | Hand movements: 5m (15 ft) or less| Near-total
        |  one or  | Light projection, light perception|    blindness
        |  both    | Visual field: 5 degrees or less   |
        |  eyes    |-----------------------------------|--------------
        |          |    TOTAL VISUAL IMPAIRMENT        | Total
        |          | No light perception (NLP)         |    blindness
--------|----------|--------------------------------------------------  
Visual acuity refers to best achievable acuity with correction.

Non-listed Snellen fractions may be classified by converting to the nearest decimal equivalent, e.g. 10/200 = 0.05, 6/30 = 0.20.

CF (count fingers) without designation of distance, may be classified to profound impairment.

HM (hand motion) without designation of distance, may be classified to near-total impairment.

Visual field measurements refer to the largest field diameter for a 1/100 white test object.

370       Keratitis

370.0    Corneal ulcer

Excludes:          that due to vitamin A deficiency (264.3)

370.00  Corneal ulcer, unspecified

370.01  Marginal corneal ulcer

370.02  Ring corneal ulcer

370.03  Central corneal ulcer

370.04  Hypopyon ulcer

Serpiginous ulcer

370.05  Mycotic corneal ulcer

370.06  Perforated corneal ulcer

370.07  Mooren's ulcer

370.2    Superficial keratitis without conjunctivitis

Excludes:          dendritic [herpes simplex] keratitis (054.42)

370.20  Superficial keratitis, unspecified

370.21  Punctate keratitis

Thygeson's superficial punctate keratitis

370.22  Macular keratitis

Keratitis:

areolar

nummular

stellate

striate

370.23  Filamentary keratitis

370.24  Photokeratitis

Snow blindness

Welders' keratitis

370.3    Certain types of keratoconjunctivitis

370.31  Phlyctenular keratoconjunctivitis

Phlyctenulosis

Use additional code for any associated tuberculosis (017.3)

370.32  Limbar and corneal involvement in vernal conjunctivitis

Use additional code for vernal conjunctivitis (372.13)

370.33  Keratoconjunctivitis sicca, not specified as Sjögren's

Excludes:          Sjögren's syndrome (710.2)

370.34  Exposure keratoconjunctivitis

370.35  Neurotrophic keratoconjunctivitis

370.4    Other and unspecified keratoconjunctivitis

370.40  Keratoconjunctivitis, unspecified

Superficial keratitis with conjunctivitis NOS

370.44  Keratitis or keratoconjunctivitis in exanthema

Code first underlying condition (050.0-052.9)

Excludes:          herpes simplex (054.43)

herpes zoster (053.21)

measles (055.71)

370.49  Other

Excludes:          epidemic keratoconjunctivitis (077.1)

370.5    Interstitial and deep keratitis

370.50  Interstitial keratitis, unspecified

370.52  Diffuse interstitial keratitis

Cogan's syndrome

370.54  Sclerosing keratitis

370.55  Corneal abscess

370.59  Other

Excludes:          disciform herpes simplex keratitis (054.43)

syphilitic keratitis (090.3)

370.6    Corneal neovascularization

370.60  Corneal neovascularization, unspecified

370.61  Localized vascularization of cornea

370.62  Pannus (corneal)

370.63  Deep vascularization of cornea

370.64  Ghost vessels (corneal)

370.8    Other forms of keratitis

370.9    Unspecified keratitis

371       Corneal opacity and other disorders of cornea

371.0    Corneal scars and opacities

Excludes:          that due to vitamin A deficiency (264.6)

371.00  Corneal opacity, unspecified

Corneal scar NOS

371.01  Minor opacity of cornea

Corneal nebula

371.02  Peripheral opacity of cornea

Corneal macula not interfering with central vision

371.03  Central opacity of cornea

Corneal:

leucoma interfering with central vision

macula interfering with central vision

371.04  Adherent leucoma

371.05  Phthisical cornea

Code first underlying tuberculosis (017.3)

371.1    Corneal pigmentations and deposits

371.10  Corneal deposit, unspecified

371.11  Anterior pigmentations

Stähli's lines

371.12  Stromal pigmentations

Hematocornea

371.13  Posterior pigmentations

Krukenberg spindle

371.14  Kayser-Fleischer ring

371.15  Other deposits associated with metabolic disorders

371.16  Argentous deposits

371.2    Corneal edema

371.20  Corneal edema, unspecified

371.21  Idiopathic corneal edema

371.22  Secondary corneal edema

371.23  Bullous keratopathy

371.24  Corneal edema due to wearing of contact lenses

371.3    Changes of corneal membranes

371.30  Corneal membrane change, unspecified

371.31  Folds and rupture of Bowman's membrane

371.32  Folds in Descemet's membrane

371.33  Rupture in Descemet's membrane

371.4    Corneal degenerations

371.40  Corneal degeneration, unspecified

371.41  Senile corneal changes

Arcus senilis

Hassall-Henle bodies

371.42  Recurrent erosion of cornea

Excludes:          Mooren's ulcer (370.07)

371.43  Band-shaped keratopathy

371.44  Other calcerous degenerations of cornea

371.45  Keratomalacia NOS

Excludes:          that due to vitamin A deficiency (264.4)

371.46  Nodular degeneration of cornea

Salzmann's nodular dystrophy

371.48  Peripheral degenerations of cornea

Marginal degeneration of cornea [Terrien's]

371.49  Other

Discrete colliquative keratopathy

371.5    Hereditary corneal dystrophies

371.50  Corneal dystrophy, unspecified

371.51  Juvenile epithelial corneal dystrophy

371.52  Other anterior corneal dystrophies

Corneal dystrophy:

microscopic cystic

ring-like

371.53  Granular corneal dystrophy

371.54  Lattice corneal dystrophy

371.55  Macular corneal dystrophy

371.56  Other stromal corneal dystrophies

Crystalline corneal dystrophy

371.57  Endothelial corneal dystrophy

Combined corneal dystrophy

Cornea guttata

Fuchs' endothelial dystrophy

371.58  Other posterior corneal dystrophies

Polymorphous corneal dystrophy

371.6    Keratoconus

371.60  Keratoconus, unspecified

371.61  Keratoconus, stable condition

371.62  Keratoconus, acute hydrops

371.7    Other corneal deformities

371.70  Corneal deformity, unspecified

371.71  Corneal ectasia

371.72  Descemetocele

371.73  Corneal staphyloma

371.8    Other corneal disorders

371.81  Corneal anesthesia and hypoesthesia

371.82  Corneal disorder due to contact lens

Excludes:          corneal edema due to contact lens (371.24)

371.89  Other

371.9    Unspecified corneal disorder

372       Disorders of conjunctiva

Excludes:          keratoconjunctivitis (370.3-370.4)

372.0    Acute conjunctivitis

372.00  Acute conjunctivitis, unspecified

372.01  Serous conjunctivitis, except viral

Excludes:          viral conjunctivitis NOS (077.9)

372.02  Acute follicular conjunctivitis

Conjunctival folliculosis NOS

Excludes:          conjunctivitis:

adenoviral (acute follicular) (077.3)

epidemic hemorrhagic (077.4)

inclusion (077.0)

Newcastle (077.8)

epidemic keratoconjunctivitis (077.1)

pharyngoconjunctival fever (077.2)

372.03  Other mucopurulent conjunctivitis

Catarrhal conjunctivitis

Excludes:          blennorrhea neonatorum (gonococcal) (098.40)

neonatal conjunctivitis (771.6)

ophthalmia neonatorum NOS (771.6)

372.04  Pseudomembranous conjunctivitis

Membranous conjunctivitis

Excludes:          diphtheritic conjunctivitis (032.81)

372.05  Acute atopic conjunctivitis

372.1    Chronic conjunctivitis

372.10  Chronic conjunctivitis, unspecified

372.11  Simple chronic conjunctivitis

372.12  Chronic follicular conjunctivitis

372.13  Vernal conjunctivitis

372.14  Other chronic allergic conjunctivitis

372.15  Parasitic conjunctivitis

Code first underlying disease as:

filariasis (125.0-125.9)

mucocutaneous leishmaniasis (085.5)

372.2    Blepharoconjunctivitis

372.20  Blepharoconjunctivitis, unspecified

372.21  Angular blepharoconjunctivitis

372.22  Contact blepharoconjunctivitis

372.3    Other and unspecified conjunctivitis

372.30  Conjunctivitis, unspecified

372.31  Rosacea conjunctivitis

Code first underlying rosacea dermatitis (695.3)

372.33  Conjunctivitis in mucocutaneous disease

Code first underlying disease as:

erythema multiforme (695.1)

Reiter's disease (099.3)

Excludes:          ocular pemphigoid (694.61)

372.39  Other

372.4    Pterygium

Excludes:          pseudopterygium (372.52)

372.40  Pterygium, unspecified

372.41  Peripheral pterygium, stationary

372.42  Peripheral pterygium, progressive

372.43  Central pterygium

372.44  Double pterygium

372.45  Recurrent pterygium

372.5    Conjunctival degenerations and deposits

372.50  Conjunctival degeneration, unspecified

372.51  Pinguecula

372.52  Pseudopterygium

372.53  Conjunctival xerosis

Excludes:          conjunctival xerosis due to vitamin A deficiency (264.0, 264.1, 264.7)

372.54  Conjunctival concretions

372.55  Conjunctival pigmentations

Conjunctival argyrosis

372.56  Conjunctival deposits

372.6    Conjunctival scars

372.61  Granuloma of conjunctiva

372.62  Localized adhesions and strands of conjunctiva

372.63  Symblepharon

Extensive adhesions of conjunctiva

372.64  Scarring of conjunctiva

Contraction of eye socket (after enucleation)

372.7    Conjunctival vascular disorders and cysts

372.71  Hyperemia of conjunctiva

372.72  Conjunctival hemorrhage

Hyposphagma

Subconjunctival hemorrhage

372.73  Conjunctival edema

Chemosis of conjunctiva

Subconjunctival edema

372.74  Vascular abnormalities of conjunctiva

Aneurysm(ata) of conjunctiva

372.75  Conjunctival cysts

372.8    Other disorders of conjunctiva

372.81  Conjunctivochalasis

372.89  Other disorders of conjunctiva

372.9    Unspecified disorder of conjunctiva

373       Inflammation of eyelids

373.0    Blepharitis

Excludes:          blepharoconjunctivitis (372.20-372.22)

373.00  Blepharitis, unspecified

373.01  Ulcerative blepharitis

373.02  Squamous blepharitis

373.1    Hordeolum and other deep inflammation of eyelid

373.11  Hordeolum externum

Hordeolum NOS

Stye

373.12  Hordeolum internum

Infection of meibomian gland

373.13  Abscess of eyelid

Furuncle of eyelid

373.2    Chalazion

Meibomian (gland) cyst

Excludes:          infected meibomian gland (373.12)

373.3    Noninfectious dermatoses of eyelid

373.31  Eczematous dermatitis of eyelid

373.32  Contact and allergic dermatitis of eyelid

373.33  Xeroderma of eyelid

373.34  Discoid lupus erythematosus of eyelid

373.4    Infective dermatitis of eyelid of types resulting in deformity

Code first underlying disease, as:

leprosy (030.0-030.9)

lupus vulgaris (tuberculous) (017.0)

yaws (102.0-102.9)

373.5    Other infective dermatitis of eyelid

Code first underlying disease, as:

actinomycosis (039.3)

impetigo (684)

mycotic dermatitis (110.0-111.9)

vaccinia (051.0)

postvaccination (999.0)

Excludes:          herpes:

simplex (054.41)

zoster (053.20)

373.6    Parasitic infestation of eyelid

Code first underlying disease, as:

leishmaniasis (085.0-085.9)

loiasis (125.2)

onchocerciasis (125.3)

pediculosis (132.0)

373.8    Other inflammations of eyelids

373.9    Unspecified inflammation of eyelid

374       Other disorders of eyelids

374.0    Entropion and trichiasis of eyelid

374.00  Entropion, unspecified

374.01  Senile entropion

374.02  Mechanical entropion

374.03  Spastic entropion

374.04  Cicatricial entropion

374.05  Trichiasis without entropion

374.1    Ectropion

374.10  Ectropion, unspecified

374.11  Senile ectropion

374.12  Mechanical ectropion

374.13  Spastic ectropion

374.14  Cicatricial ectropion

374.2    Lagophthalmos

374.20  Lagophthalmos, unspecified

374.21  Paralytic lagophthalmos

374.22  Mechanical lagophthalmos

374.23  Cicatricial lagophthalmos

374.3    Ptosis of eyelid

374.30  Ptosis of eyelid, unspecified

374.31  Paralytic ptosis

374.32  Myogenic ptosis

374.33  Mechanical ptosis

374.34  Blepharochalasis

Pseudoptosis

374.4    Other disorders affecting eyelid function

Excludes:          blepharoclonus (333.81)

blepharospasm (333.81)

facial nerve palsy (351.0)

third nerve palsy or paralysis (378.51-378.52)

tic (psychogenic) (307.20-307.23)

organic (333.3)

374.41  Lid retraction or lag

374.43  Abnormal innervation syndrome

Jaw-blinking

Paradoxical facial movements

374.44  Sensory disorders

374.45  Other sensorimotor disorders

Deficient blink reflex

374.46  Blepharophimosis

Ankyloblepharon

374.5    Degenerative disorders of eyelid and periocular area

374.50  Degenerative disorder of eyelid, unspecified

374.51  Xanthelasma

Xanthoma (planum) (tuberosum) of eyelid

Code first underlying condition (272.0-272.9)

374.52  Hyperpigmentation of eyelid

Chloasma

Dyspigmentation

374.53  Hypopigmentation of eyelid

Vitiligo of eyelid

374.54  Hypertrichosis of eyelid

374.55  Hypotrichosis of eyelid

Madarosis of eyelid

374.56  Other degenerative disorders of skin affecting eyelid

374.8    Other disorders of eyelid

374.81  Hemorrhage of eyelid

Excludes:          black eye (921.0)

374.82  Edema of eyelid

Hyperemia of eyelid

374.83  Elephantiasis of eyelid

374.84  Cysts of eyelids

Sebaceous cyst of eyelid

374.85  Vascular anomalies of eyelid

374.86  Retained foreign body of eyelid

374.87  Dermatochalasis

374.89  Other disorders of eyelid

374.9    Unspecified disorder of eyelid

375       Disorders of lacrimal system

375.0    Dacryoadenitis

375.00  Dacryoadenitis, unspecified

375.01  Acute dacryoadenitis

375.02  Chronic dacryoadenitis

375.03  Chronic enlargement of lacrimal gland

375.1    Other disorders of lacrimal gland

375.11  Dacryops

375.12  Other lacrimal cysts and cystic degeneration

375.13  Primary lacrimal atrophy

375.14  Secondary lacrimal atrophy

375.15  Tear film insufficiency, unspecified

Dry eye syndrome

375.16  Dislocation of lacrimal gland

375.2    Epiphora

375.20  Epiphora, unspecified as to cause

375.21  Epiphora due to excess lacrimation

375.22  Epiphora due to insufficient drainage

375.3    Acute and unspecified inflammation of lacrimal passages

Excludes:          neonatal dacryocystitis (771.6)

375.30  Dacryocystitis, unspecified

375.31  Acute canaliculitis, lacrimal

375.32  Acute dacryocystitis

Acute peridacryocystitis

375.33  Phlegmonous dacryocystitis

375.4    Chronic inflammation of lacrimal passages

375.41  Chronic canaliculitis

375.42  Chronic dacryocystitis

375.43  Lacrimal mucocele

375.5    Stenosis and insufficiency of lacrimal passages

375.51  Eversion of lacrimal punctum

375.52  Stenosis of lacrimal punctum

375.53  Stenosis of lacrimal canaliculi

375.54  Stenosis of lacrimal sac

375.55  Obstruction of nasolacrimal duct, neonatal

Excludes:          congenital anomaly of nasolacrimal duct (743.65)

375.56  Stenosis of nasolacrimal duct, acquired

375.57  Dacryolith

375.6    Other changes of lacrimal passages

375.61  Lacrimal fistula

375.69  Other

375.8    Other disorders of lacrimal system

375.81  Granuloma of lacrimal passages

375.89  Other

375.9    Unspecified disorder of lacrimal system

376       Disorders of the orbit

376.0    Acute inflammation of orbit

376.00  Acute inflammation of orbit, unspecified

376.01  Orbital cellulitis

Abscess of orbit

376.02  Orbital periostitis

376.03  Orbital osteomyelitis

376.04  Tenonitis

376.1    Chronic inflammatory disorders of orbit

376.10  Chronic inflammation of orbit, unspecified

376.11  Orbital granuloma

Pseudotumor (inflammatory) of orbit

376.12  Orbital myositis

376.13  Parasitic infestation of orbit

Code first underlying disease, as:

hydatid infestation of orbit (122.3, 122.6, 122.9)

myiasis of orbit (134.0)

376.2    Endocrine exophthalmos

Code first underlying thyroid disorder (242.0-242.9)

376.21  Thyrotoxic exophthalmos

376.22  Exophthalmic ophthalmoplegia

376.3    Other exophthalmic conditions

376.30  Exophthalmos, unspecified

376.31  Constant exophthalmos

376.32  Orbital hemorrhage

376.33  Orbital edema or congestion

376.34  Intermittent exophthalmos

376.35  Pulsating exophthalmos

376.36  Lateral displacement of globe

376.4    Deformity of orbit

376.40  Deformity of orbit, unspecified

376.41  Hypertelorism of orbit

376.42  Exostosis of orbit

376.43  Local deformities due to bone disease

376.44  Orbital deformities associated with craniofacial deformities

376.45  Atrophy of orbit

376.46  Enlargement of orbit

376.47  Deformity due to trauma or surgery

376.5    Enophthalmos

376.50  Enophthalmos, unspecified as to cause

376.51  Enophthalmos due to atrophy of orbital tissue

376.52  Enophthalmos due to trauma or surgery

376.6    Retained (old) foreign body following penetrating wound of orbit

Retrobulbar foreign body

376.8    Other orbital disorders

376.81  Orbital cysts

Encephalocele of orbit

376.82  Myopathy of extraocular muscles

376.89  Other

376.9    Unspecified disorder of orbit

377       Disorders of optic nerve and visual pathways

377.0    Papilledema

377.00  Papilledema, unspecified

377.01  Papilledema associated with increased intracranial pressure

377.02  Papilledema associated with decreased ocular pressure

377.03  Papilledema associated with retinal disorder

377.04  Foster-Kennedy syndrome

377.1    Optic atrophy

377.10  Optic atrophy, unspecified

377.11  Primary optic atrophy

Excludes:          neurosyphilitic optic atrophy (094.84)

377.12  Postinflammatory optic atrophy

377.13  Optic atrophy associated with retinal dystrophies

377.14  Glaucomatous atrophy [cupping] of optic disc

377.15  Partial optic atrophy

Temporal pallor of optic disc

377.16  Hereditary optic atrophy

Optic atrophy:

dominant hereditary

Leber's

377.2    Other disorders of optic disc

377.21  Drusen of optic disc

377.22  Crater-like holes of optic disc

377.23  Coloboma of optic disc

377.24  Pseudopapilledema

377.3    Optic neuritis

Excludes:          meningococcal optic neuritis (036.81)

377.30  Optic neuritis, unspecified

377.31  Optic papillitis

377.32  Retrobulbar neuritis (acute)

Excludes:          syphilitic retrobulbar neuritis (094.85)

377.33  Nutritional optic neuropathy

377.34  Toxic optic neuropathy

Toxic amblyopia

377.39  Other

Excludes:          ischemic optic neuropathy (377.41)

377.4    Other disorders of optic nerve

377.41  Ischemic optic neuropathy

377.42  Hemorrhage in optic nerve sheaths

377.49  Other

Compression of optic nerve

377.5    Disorders of optic chiasm

377.51  Associated with pituitary neoplasms and disorders

377.52  Associated with other neoplasms

377.53  Associated with vascular disorders

377.54  Associated with inflammatory disorders

377.6    Disorders of other visual pathways

377.61  Associated with neoplasms

377.62  Associated with vascular disorders

377.63  Associated with inflammatory disorders

377.7    Disorders of visual cortex

Excludes:          visual:

agnosia (368.16)

hallucinations (368.16)

halos (368.15)

377.71  Associated with neoplasms

377.72  Associated with vascular disorders

377.73  Associated with inflammatory disorders

377.75  Cortical blindness

377.9    Unspecified disorder of optic nerve and visual pathways

378       Strabismus and other disorders of binocular eye movements

Excludes:          nystagmus and other irregular eye movements (379.50-379.59)

378.0    Esotropia

Convergent concomitant strabismus

Excludes:          intermittent esotropia (378.20-378.22)

378.00  Esotropia, unspecified

378.01  Monocular esotropia

378.02  Monocular esotropia with A pattern

378.03  Monocular esotropia with V pattern

378.04  Monocular esotropia with other noncomitancies

Monocular esotropia with X or Y pattern

378.05  Alternating esotropia

378.06  Alternating esotropia with A pattern

378.07  Alternating esotropia with V pattern

378.08  Alternating esotropia with other noncomitancies

Alternating esotropia with X or Y pattern

378.1    Exotropia

Divergent concomitant strabismus

Excludes:          intermittent exotropia (378.20, 378.23-378.24)

378.10  Exotropia, unspecified

378.11  Monocular exotropia

378.12  Monocular exotropia with A pattern

378.13  Monocular exotropia with V pattern

378.14  Monocular exotropia with other noncomitancies

Monocular exotropia with X or Y pattern

378.15  Alternating exotropia

378.16  Alternating exotropia with A pattern

378.17  Alternating exotropia with V pattern

378.18  Alternating exotropia with other noncomitancies

Alternating exotropia with X or Y pattern

378.2    Intermittent heterotropia

Excludes:          vertical heterotropia (intermittent) (378.31)

378.20  Intermittent heterotropia, unspecified

Intermittent:

esotropia NOS

exotropia NOS

378.21  Intermittent esotropia, monocular

378.22  Intermittent esotropia, alternating

378.23  Intermittent exotropia, monocular

378.24  Intermittent exotropia, alternating

378.3    Other and unspecified heterotropia

378.30  Heterotropia, unspecified

378.31  Hypertropia

Vertical heterotropia (constant) (intermittent)

378.32  Hypotropia

378.33  Cyclotropia

378.34  Monofixation syndrome

Microtropia

378.35  Accommodative component in esotropia

378.4    Heterophoria

378.40  Heterophoria, unspecified

378.41  Esophoria

378.42  Exophoria

378.43  Vertical heterophoria

378.44  Cyclophoria

378.45  Alternating hyperphoria

378.5    Paralytic strabismus

378.50  Paralytic strabismus, unspecified

378.51  Third or oculomotor nerve palsy, partial

378.52  Third or oculomotor nerve palsy, total

378.53  Fourth or trochlear nerve palsy

378.54  Sixth or abducens nerve palsy

378.55  External ophthalmoplegia

378.56  Total ophthalmoplegia

378.6    Mechanical strabismus

378.60  Mechanical strabismus, unspecified

378.61  Brown's (tendon) sheath syndrome

378.62  Mechanical strabismus from other musculofascial disorders

378.63  Limited duction associated with other conditions

378.7    Other specified strabismus

378.71  Duane's syndrome

378.72  Progressive external ophthalmoplegia

378.73  Strabismus in other neuromuscular disorders

378.8    Other disorders of binocular eye movements

Excludes:          nystagmus (379.50-379.56)

378.81  Palsy of conjugate gaze

378.82  Spasm of conjugate gaze

378.83  Convergence insufficiency or palsy

378.84  Convergence excess or spasm

378.85  Anomalies of divergence

378.86  Internuclear ophthalmoplegia

378.87  Other dissociated deviation of eye movements

Skew deviation

378.9    Unspecified disorder of eye movements

Ophthalmoplegia NOS

Strabismus NOS

379       Other disorders of eye

379.0    Scleritis and episcleritis

Excludes:          syphilitic episcleritis (095.0)

379.00  Scleritis, unspecified

Episcleritis NOS

379.01  Episcleritis periodica fugax

379.02  Nodular episcleritis

379.03  Anterior scleritis

379.04  Scleromalacia perforans

379.05  Scleritis with corneal involvement

Scleroperikeratitis

379.06  Brawny scleritis

379.07  Posterior scleritis

Sclerotenonitis

379.09  Other

Scleral abscess

379.1    Other disorders of sclera

Excludes:          blue sclera (743.47)

379.11  Scleral ectasia

Scleral staphyloma NOS

379.12  Staphyloma posticum

379.13  Equatorial staphyloma

379.14  Anterior staphyloma, localized

379.15  Ring staphyloma

379.16  Other degenerative disorders of sclera

379.19  Other

379.2    Disorders of vitreous body

379.21  Vitreous degeneration

Vitreous:

cavitation

detachment

liquefaction

379.22  Crystalline deposits in vitreous

Asteroid hyalitis

Synchysis scintillans

379.23  Vitreous hemorrhage

379.24  Other vitr